Pemphigus (L10)
Clinical Information
Desmoglein 1 - A desmosomal cadherin that is an autoantigen in the acquired skin disorder PEMPHIGUS FOLIACEUS.
Pemphigus - Group of chronic blistering diseases characterized histologically by ACANTHOLYSIS and blister formation within the EPIDERMIS.
Pemphigus, Benign Familial - An autosomal dominantly inherited skin disorder characterized by recurrent eruptions of vesicles and BULLAE mainly on the neck, axillae, and groin. Mutations in the ATP2C1 gene (encoding the secretory pathway Ca2++/Mn2++ ATPase 1 (SPCA1)) cause this disease. It is clinically and histologically similar to DARIER DISEASE - both have abnormal, unstable DESMOSOMES between KERATINOCYTES and defective CALCIUM-TRANSPORTING ATPASES. It is unrelated to PEMPHIGUS VULGARIS though it closely resembles that disease.
Instructional Notations
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- pemphigus neonatorum L01.03
Diseases of the skin and subcutaneous tissue (L00–L99)
Bullous disorders (L10-L14)
L10 Pemphigus
- L10.0 Pemphigus vulgaris
- L10.1 Pemphigus vegetans
- L10.2 Pemphigus foliaceous
- L10.3 Brazilian pemphigus [fogo selvagem]
- L10.4 Pemphigus erythematosus
- L10.5 Drug-induced pemphigus
L10.8 Other pemphigus
- L10.81 Paraneoplastic pemphigus
- L10.89 Other pemphigus
- L10.9 Pemphigus, unspecified
Pemphigus (L10)