2022 ICD-10-CM Code H55.01

Congenital nystagmus

Version 2021

Valid for Submission

ICD-10:H55.01
Short Description:Congenital nystagmus
Long Description:Congenital nystagmus

Code Classification

  • Diseases of the eye and adnexa (H00–H59)
    • Other disorders of eye and adnexa (H55-H57)
      • Nystagmus and other irregular eye movements (H55)

H55.01 is a billable diagnosis code used to specify a medical diagnosis of congenital nystagmus. The code H55.01 is valid during the fiscal year 2022 from October 01, 2021 through September 30, 2022 for the submission of HIPAA-covered transactions.

The ICD-10-CM code H55.01 might also be used to specify conditions or terms like 2q partial trisomy syndrome, acquired esotropia, acquired esotropia, autosomal recessive cerebellar ataxia, pyramidal signs, nystagmus, oculomotor apraxia syndrome, congenital nystagmus , congenital nystagmus, etc.

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code H55.01 are found in the index:

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

Clinical Information

Convert H55.01 to ICD-9 Code

Information for Patients


Eye Movement Disorders

When you look at an object, you're using several muscles to move both eyes to focus on it. If you have a problem with the muscles, the eyes don't work properly.

There are many kinds of eye movement disorders. Two common ones are

Some eye movement disorders are present at birth. Others develop over time and may be associated with other problems, such as injuries. Treatments include glasses, patches, eye muscle exercises, and surgery. There is no cure for some kinds of eye movement disorders, such as most kinds of nystagmus.


[Learn More in MedlinePlus]

X-linked infantile nystagmus

X-linked infantile nystagmus is a condition characterized by abnormal eye movements. Nystagmus is a term that refers to involuntary side-to-side movements of the eyes. In people with this condition, nystagmus is present at birth or develops within the first six months of life. The abnormal eye movements may worsen when an affected person is feeling anxious or tries to stare directly at an object. The severity of nystagmus varies, even among affected individuals within the same family. Sometimes, affected individuals will turn or tilt their head to compensate for the irregular eye movements.


[Learn More in MedlinePlus]

Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)