ICD-10-CM Code G40.9

Epilepsy, unspecified

Version 2021 Non-Billable Code

Not Valid for Submission

G40.9 is a "header" nonspecific and non-billable code code, consider using a code with a higher level of specificity for a diagnosis of epilepsy, unspecified. The code is NOT valid for the year 2021 for the submission of HIPAA-covered transactions.

ICD-10:G40.9
Short Description:Epilepsy, unspecified
Long Description:Epilepsy, unspecified

Consider the following ICD-10 codes with a higher level of specificity:

  • G40.90 - ... not intractable
  • G40.901 - ... not intractable, with status epilepticus
  • G40.909 - ... not intractable, without status epilepticus
  • G40.91 - ... intractable
  • G40.911 - ... intractable, with status epilepticus
  • G40.919 - ... intractable, without status epilepticus

Clinical Information

  • DRUG RESISTANT EPILEPSY-. epileptic condition in which adequate trials of two tolerated and appropriately chosen and used antiepileptic drugs schedules to achieve sustained seizure freedom failed.
  • EPILEPTIC SYNDROMES-. epileptic seizures that are of similar type and age of onset and have other similar features e.g. clinical course eeg findings genetic association and neuropathology.
  • EPILEPSY-. a disorder characterized by recurrent episodes of paroxysmal brain dysfunction due to a sudden disorderly and excessive neuronal discharge. epilepsy classification systems are generally based upon: 1 clinical features of the seizure episodes e.g. motor seizure 2 etiology e.g. post traumatic 3 anatomic site of seizure origin e.g. frontal lobe seizure 4 tendency to spread to other structures in the brain and 5 temporal patterns e.g. nocturnal epilepsy. from adams et al. principles of neurology 6th ed p313
  • EPILEPSIES PARTIAL-. conditions characterized by recurrent paroxysmal neuronal discharges which arise from a focal region of the brain. partial seizures are divided into simple and complex depending on whether consciousness is unaltered simple partial seizure or disturbed complex partial seizure. both types may feature a wide variety of motor sensory and autonomic symptoms. partial seizures may be classified by associated clinical features or anatomic location of the seizure focus. a secondary generalized seizure refers to a partial seizure that spreads to involve the brain diffusely. from adams et al. principles of neurology 6th ed pp317
  • EPILEPSY GENERALIZED-. recurrent conditions characterized by epileptic seizures which arise diffusely and simultaneously from both hemispheres of the brain. classification is generally based upon motor manifestations of the seizure e.g. convulsive nonconvulsive akinetic atonic etc. or etiology e.g. idiopathic cryptogenic and symptomatic. from mayo clin proc 1996 apr;714:405 14
  • EPILEPSY TONIC CLONIC-. a generalized seizure disorder characterized by recurrent major motor seizures. the initial brief tonic phase is marked by trunk flexion followed by diffuse extension of the trunk and extremities. the clonic phase features rhythmic flexor contractions of the trunk and limbs pupillary dilation elevations of blood pressure and pulse urinary incontinence and tongue biting. this is followed by a profound state of depressed consciousness post ictal state which gradually improves over minutes to hours. the disorder may be cryptogenic familial or symptomatic caused by an identified disease process. from adams et al. principles of neurology 6th ed p329
  • EPILEPSIES MYOCLONIC-. a clinically diverse group of epilepsy syndromes characterized either by myoclonic seizures or by myoclonus in association with other seizure types. myoclonic epilepsy syndromes are divided into three subtypes based on etiology: familial cryptogenic and symptomatic.
  • EPILEPSY ABSENCE-. a seizure disorder usually occurring in childhood characterized by rhythmic electrical brain discharges of generalized onset. clinical features include a sudden cessation of ongoing activity usually without loss of postural tone. rhythmic blinking of the eyelids or lip smacking frequently accompanies the seizures. the usual duration is 5 10 seconds and multiple episodes may occur daily. juvenile absence epilepsy is characterized by the juvenile onset of absence seizures and an increased incidence of myoclonus and tonic clonic seizures. menkes textbook of child neurology 5th ed p736
  • EPILEPSY TEMPORAL LOBE-. a localization related focal form of epilepsy characterized by recurrent seizures that arise from foci within the temporal lobe most commonly from its mesial aspect. a wide variety of psychic phenomena may be associated including illusions hallucinations dyscognitive states and affective experiences. the majority of complex partial seizures see epilepsy complex partial originate from the temporal lobes. temporal lobe seizures may be classified by etiology as cryptogenic familial or symptomatic. from adams et al. principles of neurology 6th ed p321.
  • EPILEPSY POST TRAUMATIC-. recurrent seizures causally related to craniocerebral trauma. seizure onset may be immediate but is typically delayed for several days after the injury and may not occur for up to two years. the majority of seizures have a focal onset that correlates clinically with the site of brain injury. cerebral cortex injuries caused by a penetrating foreign object craniocerebral trauma penetrating are more likely than closed head injuries head injuries closed to be associated with epilepsy. concussive convulsions are nonepileptic phenomena that occur immediately after head injury and are characterized by tonic and clonic movements. from rev neurol 1998 feb;26150:256 261; sports med 1998 feb;252:131 6
  • EPILEPSY COMPLEX PARTIAL-. a disorder characterized by recurrent partial seizures marked by impairment of cognition. during the seizure the individual may experience a wide variety of psychic phenomenon including formed hallucinations illusions deja vu intense emotional feelings confusion and spatial disorientation. focal motor activity sensory alterations and automatism may also occur. complex partial seizures often originate from foci in one or both temporal lobes. the etiology may be idiopathic cryptogenic partial complex epilepsy or occur as a secondary manifestation of a focal cortical lesion symptomatic partial complex epilepsy. from adams et al. principles of neurology 6th ed pp317 8
  • EPILEPSY FRONTAL LOBE-. a localization related focal form of epilepsy characterized by seizures which arise in the frontal lobe.
  • EPILEPSIA PARTIALIS CONTINUA-. a variant of epilepsy characterized by continuous focal jerking of a body part over a period of hours days or even years without spreading to other body regions. contractions may be aggravated by movement and are reduced but not abolished during sleep. electroencephalography demonstrates epileptiform spike and wave discharges over the hemisphere opposite to the affected limb in most instances. the repetitive movements may originate from the cerebral cortex or from subcortical structures e.g. brain stem; basal ganglia. this condition is associated with russian spring and summer encephalitis see encephalitis tick borne; rasmussen syndrome see encephalitis; multiple sclerosis; diabetes mellitus; brain neoplasms; and cerebrovascular disorders. from brain 1996 april;119pt2:393 407; epilepsia 1993;34;suppl 1:s29 s36; and adams et al. principles of neurology 6th ed p319
  • EPILEPSY ROLANDIC-. an autosomal dominant inherited partial epilepsy syndrome with onset between age 3 and 13 years. seizures are characterized by paresthesia and tonic or clonic activity of the lower face associated with drooling and dysarthria. in most cases affected children are neurologically and developmentally normal. from epilepsia 1998 39;suppl 4:s32 s41
  • MYOCLONIC EPILEPSY JUVENILE-. a disorder characterized by the onset of myoclonus in adolescence a marked increase in the incidence of absence seizures see epilepsy absence and generalized major motor seizures see epilepsy tonic clonic. the myoclonic episodes tend to occur shortly after awakening. seizures tend to be aggravated by sleep deprivation and alcohol consumption. hereditary and sporadic forms have been identified. from adams et al. principles of neurology 6th ed p323
  • MYOCLONIC EPILEPSIES PROGRESSIVE-. a heterogeneous group of primarily familial epilepsy disorders characterized by myoclonic seizures tonic clonic seizures ataxia progressive intellectual deterioration and neuronal degeneration. these include lafora disease; merrf syndrome; neuronal ceroid lipofuscinosis; sialidosis see mucolipidoses and unverricht lundborg syndrome.
  • LAFORA DISEASE-. a form of stimulus sensitive myoclonic epilepsy inherited as an autosomal recessive condition. the most common presenting feature is a single seizure in the second decade of life. this is followed by progressive myoclonus myoclonic seizures tonic clonic seizures focal occipital seizures intellectual decline and severe motor and coordination impairments. most affected individuals do not live past the age of 25 years. concentric amyloid lafora bodies are found in neurons liver skin bone and muscle from menkes textbook of childhood neurology 5th ed pp111 110.
  • UNVERRICHT LUNDBORG SYNDROME-. an autosomal recessive condition characterized by recurrent myoclonic and generalized seizures ataxia slowly progressive intellectual deterioration dysarthria and intention tremor. myoclonic seizures are severe and continuous and tend to be triggered by movement stress and sensory stimuli. the age of onset is between 8 and 13 years and the condition is relatively frequent in the baltic region especially finland. from menkes textbook of child neurology 5th ed pp109 110
  • EPILEPSY REFLEX-. a subtype of epilepsy characterized by seizures that are consistently provoked by a certain specific stimulus. auditory visual and somatosensory stimuli as well as the acts of writing reading eating and decision making are examples of events or activities that may induce seizure activity in affected individuals. from neurol clin 1994 feb;121:57 8
  • EPILEPSY BENIGN NEONATAL-. a condition marked by recurrent seizures that occur during the first 4 6 weeks of life despite an otherwise benign neonatal course. autosomal dominant familial and sporadic forms have been identified. seizures generally consist of brief episodes of tonic posturing and other movements apnea eye deviations and blood pressure fluctuations. these tend to remit after the 6th week of life. the risk of developing epilepsy at an older age is moderately increased in the familial form of this disorder. neurologia 1996 feb;112:51 5
  • EPILEPSY PARTIAL SENSORY-. a disorder characterized by recurrent focal onset seizures which have sensory i.e. olfactory visual tactile gustatory or auditory manifestations. partial seizures that feature alterations of consciousness are referred to as complex partial seizures epilepsy complex partial.
  • EPILEPSY PARTIAL MOTOR-. a disorder characterized by recurrent localized paroxysmal discharges of cerebral neurons that give rise to seizures that have motor manifestations. the majority of partial motor seizures originate in the frontal lobe see also epilepsy frontal lobe. motor seizures may manifest as tonic or clonic movements involving the face one limb or one side of the body. a variety of more complex patterns of movement including abnormal posturing of extremities may also occur.

Code Classification

  • Diseases of the nervous system (G00–G99)
    • Episodic and paroxysmal disorders (G40-G47)
      • Epilepsy and recurrent seizures (G40)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021

Information for Patients


Epilepsy

Epilepsy is a brain disorder that causes people to have recurring seizures. The seizures happen when clusters of nerve cells, or neurons, in the brain send out the wrong signals. People may have strange sensations and emotions or behave strangely. They may have violent muscle spasms or lose consciousness.

Epilepsy has many possible causes, including illness, brain injury, and abnormal brain development. In many cases, the cause is unknown.

Doctors use brain scans and other tests to diagnose epilepsy. It is important to start treatment right away. There is no cure for epilepsy, but medicines can control seizures for most people. When medicines are not working well, surgery or implanted devices such as vagus nerve stimulators may help. Special diets can help some children with epilepsy.

NIH: National Institute of Neurological Disorders and Stroke

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