G23.2 - Striatonigral degeneration

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Infantile striatonigral degeneration
• Sporadic infantile bilateral striatal necrosis
• Striatonigral degeneration

Clinical Information

• Machado-Joseph Disease-. a dominantly-inherited ataxia first described in people of azorean and portuguese descent, and subsequently identified in brazil, japan, china, and australia. this disorder is classified as one of the spinocerebellar ataxias (type 3) and has been associated with a mutation of the mjd1 gene on chromosome 14. clinical features include progressive ataxia, dysarthria, postural instability, nystagmus, eyelid retraction, and facial fasciculations. dystonia is prominent in younger patients (referred to as type i machado-joseph disease). type ii features ataxia and ocular signs; type iii features muscular atrophy and a sensorimotor neuropathy; and type iv features extrapyramidal signs combined with a sensorimotor neuropathy. (from clin neurosci 1995;3(1):17-22; ann neurol 1998 mar;43(3):288-96)
• Striatonigral Degeneration-. a sporadic neurodegenerative disease with onset in middle-age characterized clinically by parkinsonian features (e.g., muscle rigidity; hypokinesia; stooped posture) and hypotension. this condition is considered a clinical variant of multiple system atrophy. pathologic features include a prominent loss of neurons in the zona compacta of the substantia nigra and putamen. (from adams et al., principles of neurology, 6th ed, p1075-6)
• Striatonigral Degeneration-. a progressive neurodegenerative disorder caused by a disruption in the connection between the striatum and the substantia nigra. it is a type of multiple system atrophy (msa). signs and symptoms include rigidity, instability, impaired speech, and slow movements.

Convert to ICD-9 Code

Patient Education

Degenerative Nerve Diseases

Degenerative nerve diseases affect many of your body's activities, such as balance, movement, talking, breathing, and heart function. Many of these diseases are genetic. Sometimes the cause is a medical condition such as alcoholism, a tumor, or a stroke. Other causes may include toxins, chemicals, and viruses. Sometimes the cause is unknown.

Degenerative nerve diseases include:

• Alzheimer's disease
• Amyotrophic lateral sclerosis
• Friedreich ataxia
• Huntington's disease
• Lewy body disease
• Parkinson's disease
• Spinal muscular atrophy

Degenerative nerve diseases can be serious or life-threatening. It depends on the type. Most of them have no cure. Treatments may help improve symptoms, relieve pain, and increase mobility.

Code History

• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)