ICD-10-CM Code D81.9

Valid for Submission

D81.9 is a billable code used to specify a medical diagnosis of combined immunodeficiency, unspecified. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code D81.9 might also be used to specify conditions or terms like autosomal recessive scid, autosomal recessive severe combined immunodeficiency, benign combined immunodeficiency, combined immunodeficiency disease, combined immunodeficiency with faciooculoskeletal anomalies syndrome, congenital atrophy of optic nerve, etc

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code D81.9:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.

• Severe combined immunodeficiency disorder SCID NOS

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code D81.9 are found in the index:

• - Agammaglobulinemia (acquired (secondary)) (nonfamilial) - D80.1
  • - with
    • - lymphopenia - D81.9
  • - lymphopenic - D81.9

• - Deficiency, deficient
  • - immunity - D84.9
    • - combined - D81.9

• - Immunodeficiency - D84.9
  • - combined - D81.9
    • - severe (SCID) - D81.9
  • - severe combined (SCID) - D81.9

• - Syndrome - See Also: Disease;
  • - combined immunity deficiency - D81.9
  • - immunity deficiency, combined - D81.9
  • - immunodeficiency
    • - combined - D81.9

Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Autosomal recessive SCID
• Autosomal recessive severe combined immunodeficiency
• Benign combined immunodeficiency
• Combined immunodeficiency disease
• Combined immunodeficiency with faciooculoskeletal anomalies syndrome
• Congenital atrophy of optic nerve
• Hepatic veno-occlusive disease with immunodeficiency syndrome
• Obstruction of visceral vein
• Severe combined immunodeficiency disease
• Severe combined immunodeficiency with low T- and B-cell numbers
• Severe combined immunodeficiency with maternofetal engraftment
• Severe combined immunodeficiency, microcephaly, growth retardation, sensitivity to ionizing radiation syndrome
• Veno-occlusive disease of the liver

Clinical Information

• SEVERE COMBINED IMMUNODEFICIENCY-. group of rare congenital disorders characterized by impairment of both humoral and cell mediated immunity leukopenia and low or absent antibody levels. it is inherited as an x linked or autosomal recessive defect. mutations occurring in many different genes cause human severe combined immunodeficiency scid.
• X LINKED COMBINED IMMUNODEFICIENCY DISEASES-. forms of combined immunodeficiency caused by mutations in the gene for interleukin receptor common gamma subunit. both severe and non severe subtypes of the disease have been identified.

Diagnostic Related Groups

The ICD-10 code D81.9 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC). applicable from 10/01/2019 through 09/30/2020.

• 808 - MAJOR HEMATOLOGICAL AND IMMUNOLOGICAL DIAGNOSES EXCEPT SICKLE CELL CRISIS AND COAGULATION DISORDERS WITH MCC
• 809 - MAJOR HEMATOLOGICAL AND IMMUNOLOGICAL DIAGNOSES EXCEPT SICKLE CELL CRISIS AND COAGULATION DISORDERS WITH CC
• 810 - MAJOR HEMATOLOGICAL AND IMMUNOLOGICAL DIAGNOSES EXCEPT SICKLE CELL CRISIS AND COAGULATION DISORDERS WITHOUT CC/MCC

Convert D81.9 to ICD-9

• 279.2 - Combined immunity defic (Approximate Flag)

Code Classification

• Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50–D89)
  • Certain disorders involving the immune mechanism (D80-D89)
    • Combined immunodeficiencies (D81)

Code History

• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
  (First year ICD-10-CM implemented into the HIPAA code set)
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

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