ICD-10-CM Code A81.00

Creutzfeldt-Jakob disease, unspecified

Version 2020 Billable Code

Valid for Submission

A81.00 is a billable code used to specify a medical diagnosis of creutzfeldt-jakob disease, unspecified. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code A81.00 might also be used to specify conditions or terms like cerebral degeneration due to creutzfeldt-jakob disease or creutzfeldt-jakob disease or dementia due to creutzfeldt jakob disease or dementia due to infectious disease.

ICD-10:A81.00
Short Description:Creutzfeldt-Jakob disease, unspecified
Long Description:Creutzfeldt-Jakob disease, unspecified

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code A81.00:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Jakob-Creutzfeldt disease, unspecified

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code A81.00 are found in the index:


Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Cerebral degeneration due to Creutzfeldt-Jakob disease
  • Creutzfeldt-Jakob disease
  • Dementia due to Creutzfeldt Jakob disease
  • Dementia due to infectious disease

Clinical Information

  • PRION PROTEINS-. membrane glycosylphosphatidylinositol anchored glycoproteins that may aggregate into rod like structures. the prion protein prnp gene is characterized by five tandem repeat sequences that encode a highly unstable protein region of five octapeptide repeats. mutations in the repeat region and elsewhere in this gene are associated with creutzfeldt jakob disease; fatal familial insomnia; gerstmann straussler disease; huntington disease like 1 and kuru.
  • CREUTZFELDT JAKOB SYNDROME-. a rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. affected individuals may present with sleep disturbances personality changes ataxia; aphasia visual loss weakness muscle atrophy myoclonus progressive dementia and death within one year of disease onset. a familial form exhibiting autosomal dominant inheritance and a new variant cjd potentially associated with encephalopathy bovine spongiform have been described. pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of prions. from n engl j med 1998 dec 31;33927

Convert A81.00 to ICD-9

  • 046.19 - Creutzfldt-Jakob NEC/NOS (Approximate Flag)

Code Classification

  • Certain infectious and parasitic diseases (A00–B99)
    • Viral and prion infections of the central nervous system (A80-A89)
      • Atypical virus infections of central nervous system (A81)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients


Creutzfeldt-Jakob Disease

Creutzfeldt-Jakob disease (CJD) is a rare, degenerative brain disorder. Symptoms usually start around age 60. Memory problems, behavior changes, vision problems, and poor muscle coordination progress quickly to dementia, coma, and death. Most patients die within a year.

The three main categories of CJD are

  • Sporadic CJD, which occurs for no known reason
  • Hereditary CJD, which runs in families
  • Acquired CJD, which occurs from contact with infected tissue, usually during a medical procedure

Cattle can get a disease related to CJD called bovine spongiform encephalopathy (BSE) or "mad cow disease." There is concern that people can get a variant of CJD from eating beef from an infected animal, but there is no direct proof to support this.

NIH: National Institute of Neurological Disorders and Stroke


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Prion disease Prion disease represents a group of conditions that affect the nervous system in humans and animals. In people, these conditions impair brain function, causing changes in memory, personality, and behavior; a decline in intellectual function (dementia); and abnormal movements, particularly difficulty with coordinating movements (ataxia). The signs and symptoms of prion disease typically begin in adulthood and worsen with time, leading to death within a few months to several years.
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