ICD-9 Diagnosis Code 746.89

Cong heart anomaly NEC

Diagnosis Code 746.89

ICD-9: 746.89
Short Description: Cong heart anomaly NEC
Long Description: Other specified congenital anomalies of heart
This is the 2014 version of the ICD-9-CM diagnosis code 746.89

Code Classification
  • Congenital anomalies (740–759)
    • Congenital anomalies (740-759)
      • 746 Other congenital anomalies of heart

Information for Medical Professionals

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Synonyms
  • Abnormal atrial arrangement
  • Abnormal atrioventricular connection
  • Abnormal atrioventricular connection - biventricular
  • Abnormal atrioventricular connection - univentricular
  • Abnormal attachment of tricuspid chordae tendinae
  • Abnormal number of leaflets
  • Abnormal position of cardiac valve
  • Abnormality of atrioventricular
  • Abnormality of common atrioventricular valve papillary muscle
  • Aborted systole
  • Absence of mitral chordae tendinae
  • Absence of primary mitral chordae tendinae
  • Absent atrioventricular connection with straddling valve
  • Absent left sided atrioventricular connection
  • Absent right atrioventricular valve leaflets
  • Accessory tissue on aortic valve cusp
  • Accessory tissue on common atrioventricular valve leaflet
  • Accessory tissue on left atrioventricular valve leaflet
  • Accessory tissue on mitral leaflet
  • Accessory tissue on right atrioventricular valve leaflet
  • Accessory tissue on tricuspid leaflet
  • Accessory tissue on truncal valve cusp
  • Acommissural unicuspid aortic valve
  • Anomalous coronary venous return
  • Anomalous muscle bands of left ventricle
  • Anomalous muscle bands of right ventricle
  • Anomalous valve of coronary sinus
  • Anterior leaflet of mitral valve attached to septum
  • Aortic orifice anterior left with respect to pulmonary orifice
  • Aortic orifice anterior right with respect to pulmonary orifice
  • Aortic orifice anterior with respect to pulmonary orifice
  • Aortic orifice left side by side with respect to pulmonary orifice
  • Aortic orifice posterior left with respect to pulmonary orifice
  • Aortic orifice posterior with respect to pulmonary orifice
  • Aortic orifice right side by side with respect to pulmonary orifice
  • Aortic valve dysplasia
  • Aortic valve ring hypoplasia
  • Aortico-left ventricular tunnel with aneurysm of intracardiac septal wall and aneurysm of extracardiac aortic wall
  • Aortico-left ventricular tunnel with extracardiac aneurysm of aortic wall
  • Arrhythmogenic right ventricular dysplasia
  • Atresia of common atrioventricular valve
  • Atrioventricular septal defect - ventricular component under inferior bridging leaflet
  • Atrioventricular septal defect - ventricular component under superior bridging leaflet
  • Atrioventricular septal defect with atrioventricular valve regurgitation through left inferior bridging leaflet lateral mural commissure
  • Atrioventricular septal defect with ventricular imbalance consisting of dominant left ventricle and hypoplastic right ventricle
  • Bifid apex of heart
  • Bilateral atria
  • Bilateral isomeric atria
  • Bipartite right ventricle
  • Brugada syndrome
  • Chiari's network
  • Cleft leaflet of tricuspid valve
  • Commissural fusion of aortic cusp
  • Commissural fusion of aortic valve
  • Commissural fusion of truncal valve
  • Common atrioventricular valve stenosis
  • Completely unroofed coronary sinus defect in left atrium
  • Congenital abnormality of anterior cardiac vein
  • Congenital abnormality of atrioventricular valves in atrioventricular septal defect
  • Congenital abnormality of cardiac vein
  • Congenital abnormality of great cardiac vein
  • Congenital abnormality of left atrioventricular valve chordae tendinae in double inlet ventricle
  • Congenital abnormality of left atrioventricular valve in double inlet ventricle
  • Congenital abnormality of left atrium
  • Congenital abnormality of middle cardiac vein
  • Congenital abnormality of mitral subvalvular apparatus
  • Congenital abnormality of posterior cardiac vein of left ventricle
  • Congenital abnormality of right atrioventricular valve chordae tendinae in double inlet ventricle
  • Congenital abnormality of right atrioventricular valve in double inlet ventricle
  • Congenital abnormality of right atrioventricular valve leaflet in double inlet ventricle
  • Congenital abnormality of right atrioventricular valve papillary muscle in double inlet ventricle
  • Congenital abnormality of tricuspid chordae tendinae
  • Congenital abnormality of tricuspid leaflet
  • Congenital abnormality of tricuspid papillary muscle
  • Congenital absence of aortic valve
  • Congenital absence of chordae tendineae
  • Congenital absence of coronary sinus
  • Congenital aneurysm of heart
  • Congenital aneurysm of subaortic left ventricle
  • Congenital anomaly of aortic valve
  • Congenital anomaly of heart valve
  • Congenital anomaly of pericardium
  • Congenital atresia of cardiac valve
  • Congenital atresia of cardiac vein
  • Congenital billowing of mitral valve leaflet
  • Congenital cardiomegaly
  • Congenital cleft of cardiac valve
  • Congenital conduction defect
  • Congenital deformity of mitral valve annulus
  • Congenital dilatation of atrium
  • Congenital dilatation of cardiac ventricle
  • Congenital disease and abnormality of heart, thoracic aorta and pericardium
  • Congenital diverticulum of left ventricle
  • Congenital enlargement of coronary sinus
  • Congenital epicardial cyst
  • Congenital extrapericardial cyst
  • Congenital His bundle tachycardia
  • Congenital hypertrophy of cardiac ventricle
  • Congenital hypoplasia of aortic valve
  • Congenital hypoplasia of cardiac vein
  • Congenital hypoplasia of cardiac ventricle
  • Congenital hypoplasia of heart
  • Congenital hypoplasia of mitral valve
  • Congenital insufficiency of tricuspid valve
  • Congenital intrapericardial cyst
  • Congenital left ventricular aneurysm
  • Congenital left ventricular submitral valve aneurysm
  • Congenital mass of mitral leaflet
  • Congenital pericardial cyst
  • Congenital pericardial defect
  • Congenital right ventricular aneurysm
  • Congenital right ventricular diverticulum
  • Congenital stenosis of cardiac valve
  • Congenital stenosis of mitral subvalvular apparatus
  • Congenital subaortic diverticulum
  • Congenital valvular insufficiency
  • Continuity between mitral valve and pulmonary valve
  • Coronary sinus abnormality
  • Coronary sinus defect in left atrium
  • Coronary sinus drainage cephalad to left superior vena cava
  • Coronary sinus drainage cephalad to right superior vena cava
  • Criss-cross heart
  • Criss-cross heart with leftward rotation
  • Criss-cross heart with rightward rotation
  • Diffuse hypoplasia of left ventricle
  • Dilatation of common atrioventricular valve annulus
  • Dilatation of left atrioventricular valve annulus
  • Dilatation of mitral annulus
  • Dilatation of right atrioventricular valve annulus
  • Dilatation of tricuspid annulus
  • Discontinuity between mitral valve and aortic valve
  • Discontinuity between mitral valve and pulmonary valve
  • Discordant atrioventricular connection
  • Discordant ventriculoarterial connection
  • Diverticulum of coronary sinus
  • Divided left atrium
  • Divided left atrium with all pulmonary veins to proximal chamber without communication to left atrium with extracardiac pulmonary venous chamber communication
  • Divided right atrium
  • Double aortic valve
  • Double inlet left ventricle
  • Double inlet right ventricle
  • Double inlet to ventricle of indeterminate morphology
  • Double inlet ventricle
  • Double mitral valve
  • Double orifice of common atrioventricular valve
  • Double orifice of left atrioventricular valve
  • Double orifice of mitral valve
  • Double orifice of right atrioventricular valve
  • Double orifice of right atrioventricular valve in double inlet ventricle
  • Double orifice of tricuspid valve
  • Double outlet from ventricle of indeterminate morphology
  • Ebstein-like downward displacement of mitral valve
  • Ebstein-like malformation of the mitral valve
  • Eccentric opening of aortic valve
  • Failure of growth of fetal left cardiac ventricle
  • Failure of growth of fetal right cardiac ventricle
  • Fetal cardiomegaly
  • Fetal heart failure with myocardial hypertrophy
  • Fetal myocarditis
  • Functionally univentricular heart
  • Hemicardia
  • Hepatic vein to left atrium and right atrium
  • Hepatic vein to right sided atrium
  • Hypoplasia of aortic valve cusp
  • Hypoplasia of cardiac vein
  • Hypoplasia of infundibular septum
  • Hypoplasia of left atrioventricular valve annulus in double inlet ventricle
  • Hypoplasia of left ventricular outflow tract
  • Hypoplasia of left ventricular outflow tract and trabecular area
  • Hypoplasia of mitral valve annulus
  • Hypoplasia of right atrioventricular valve annulus in double inlet ventricle
  • Hypoplasia of right heart
  • Hypoplasia of trabecular portion of left ventricle
  • Hypoplasia of trabecular portion of right ventricle
  • Hypoplastic common atrioventricular valve papillary muscle
  • Hypoplastic mitral papillary muscle
  • Hypoplastic right atrioventricular valve papillary muscle
  • Hypoplastic tricuspid papillary muscle
  • Imperforate common atrioventricular valve
  • Imperforate left atrioventricular valve
  • Imperforate left ventriculoarterial valve
  • Imperforate right atrioventricular valve
  • Imperforate right ventriculoarterial valve
  • Imperforate ventriculoarterial valve
  • Indeterminate atrial arrangement
  • Leakage of conduit from right atrium to pulmonary artery
  • Left atrial appendage - right - juxtaposition
  • Left atrial appendage aneurysm
  • Left atrial dilatation
  • Left atrial hypoplasia
  • Left atrioventricular valve atresia
  • Left atrioventricular valve dysplasia
  • Left atrioventricular valve hypoplasia
  • Left atrioventricular valve leaflet abnormality
  • Left atrioventricular valve leaflet dysplasia
  • Left atrioventricular valve prolapse
  • Left atrioventricular valve stenosis
  • Left atrioventricular valve stenosis in double inlet ventricle
  • Left ventricular diverticulum
  • Left ventricular hypoplasia
  • Left ventricular outflow tract abnormality
  • Left ventricular outflow tract atresia
  • Left ventricular outflow tract obstruction
  • Left ventricular outflow tract obstruction due to prolapse of Eustachian valve
  • Left ventricular outflow tract obstruction due to prolapsed arterial valve
  • Levoatrial cardinal vein
  • Malattachment of atrial septum
  • Malattachment of atrial septum with posterior aspect of septum primum to left
  • Malattachment of atrial septum with superior aspect of septum primum to left and posterior
  • Mitral valve dysplasia
  • Monocuspid cardiac valve
  • Multiple mitral papillary muscles with hammock valve
  • Myxomatosis of cardiac valve
  • Obstruction of right ventricular outflow tract due to aortico-left ventricular tunnel
  • Overriding left atrioventricular valve
  • Overriding left ventriculoarterial valve
  • Overriding mitral valve
  • Overriding right atrioventricular valve
  • Overriding right ventriculoarterial valve
  • Overriding tricuspid valve
  • Overriding ventriculoarterial valve
  • Partial agenesis of pericardium
  • Pericardial anomaly
  • Pericardial cyst
  • Pericardial defect
  • Pericardial diverticulum
  • Pleuropericardial cyst
  • Progression of fetal left ventricular outflow tract obstruction
  • Progression of fetal right ventricular outflow tract obstruction
  • Prolapse of Eustachian valve
  • Prolapse of Eustachian valve through atrial septum
  • Prolapse of Eustachian valve through tricuspid valve
  • Quadricuspid aortic valve
  • Quadricuspid cardiac valve
  • Quadricuspid pulmonary valve
  • Quadricuspid truncal valve
  • Regurgitation of common atrioventricular valve
  • Regurgitation of fetal tricuspid valve
  • Regurgitation of fetal truncal valve
  • Right atrial appendage aneurysm
  • Right atrial endocardial fibroelastosis
  • Right atrioventricular valve atresia
  • Right atrioventricular valve chordae too long
  • Right atrioventricular valve chordae too short
  • Right atrioventricular valve leaflets absent in double inlet ventricle
  • Right hypoplastic heart syndrome
  • Right to left cardiac shunt
  • Right ventricle anterior to left ventricle
  • Right ventricle inferior to left ventricle
  • Right ventricle posterior to left ventricle
  • Right ventricle to left of left ventricle
  • Right ventricular diverticulum
  • Right ventricular outflow obstruction - localized
  • Right ventricular outflow tract obstruction due to aneurysm of membranous septum
  • Right ventricular outflow tract obstruction due to atrioventricular valve
  • Right ventricular outflow tract obstruction due to common atrioventricular valve
  • Right ventricular outflow tract obstruction due to fibromuscular shelf
  • Right ventricular outflow tract obstruction due to malaligned outlet septum
  • Right ventricular outflow tract obstruction due to prolapse of Eustachian valve
  • Right ventricular outflow tract obstruction due to prolapsed arterial valve
  • Right ventricular outflow tract obstruction due to septal hypertrophy
  • Right ventricular outflow tract obstruction due to septoparietal trabeculation
  • Rudimentary left ventricle
  • Septoparietal trabeculations
  • Solitary aortic trunk with pulmonary atresia
  • Solitary pulmonary trunk with aortic atresia
  • Stenosis of fetal truncal valve
  • Straddling left atrioventricular valve
  • Straddling mitral valve
  • Straddling right atrioventricular valve
  • Straddling tricuspid valve
  • Superior to inferior ventricular relationship
  • Totally absent pericardium
  • Tricuspid annulus hypoplasia
  • Tricuspid truncal valve
  • Tripartite right ventricle
  • Truncal valve overriding ventricular septum
  • Two atrioventricular valves in double inlet ventricle
  • Uniatrial biventricular connection with absent left sided atrioventricular connection with straddling valve
  • Uniatrial biventricular connection with absent right sided atrioventricular connection with straddling valve
  • Unicommissural unicuspid aortic valve
  • Unicuspid aortic valve
  • Unipartite right ventricle
  • Univentricular atrioventricular connection with absent left sided atrioventricular connection
  • Univentricular atrioventricular connection with absent right sided atrioventricular connection
  • Ventricular imbalance

Index of Diseases and Injuries
References found for the code 746.89 in the Index of Diseases and Injuries:


Information for Patients


Congenital Heart Defects

A congenital heart defect is a problem with the structure of the heart. It is present at birth. Congenital heart defects are the most common type of birth defect. The defects can involve the walls of the heart, the valves of the heart, and the arteries and veins near the heart. They can disrupt the normal flow of blood through the heart. The blood flow can slow down, go in the wrong direction or to the wrong place, or be blocked completely.

Doctors use a physical exam and special heart tests to diagnose congenital heart defects. They often find severe defects during pregnancy or soon after birth. Signs and symptoms of severe defects in newborns include

  • Rapid breathing
  • Cyanosis - a bluish tint to the skin, lips, and fingernails
  • Fatigue
  • Poor blood circulation

Many congenital heart defects cause few or no signs and symptoms. They are often not diagnosed until children are older.

Many children with congenital heart defects don't need treatment, but others do. Treatment can include medicines, catheter procedures, surgery, and heart transplants. The treatment depends on the type of the defect, how severe it is, and a child's age, size, and general health.

NIH: National Heart, Lung, and Blood Institute

  • Absent pulmonary valve
  • Anomalous left coronary artery from the pulmonary artery
  • Aortic angiography
  • Aortopulmonary window
  • Atrial septal defect
  • Bicuspid aortic valve
  • Cardiac catheterization
  • Cardiac catheterization - discharge
  • Coarctation of the aorta
  • Congenital heart defect corrective surgeries
  • Congenital heart disease
  • Coronary artery fistula
  • Cyanotic heart disease
  • Dextrocardia
  • Double aortic arch
  • Double inlet left ventricle
  • Ebstein's anomaly
  • Eisenmenger syndrome
  • Electrocardiogram
  • Endocardial cushion defect
  • Heart murmurs and other sounds
  • Hypoplastic left heart syndrome
  • Left heart catheterization
  • Patent ductus arteriosus
  • Patent foramen ovale
  • Pediatric heart surgery - discharge
  • Pulmonary atresia
  • Pulmonary valve stenosis
  • Tetralogy of Fallot
  • Total anomalous pulmonary venous return
  • Transposition of the great vessels
  • Tricuspid atresia
  • Truncus arteriosus
  • Vascular ring
  • Ventricular septal defect


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