ICD-9 Code 746.89

Other specified congenital anomalies of heart

Not Valid for Submission

746.89 is a legacy non-billable code used to specify a medical diagnosis of other specified congenital anomalies of heart. This code was replaced on September 30, 2015 by its ICD-10 equivalent.

ICD-9:	746.89
Short Description:	Cong heart anomaly NEC
Long Description:	Other specified congenital anomalies of heart

Convert 746.89 to ICD-10

The following crosswalk between ICD-9 to ICD-10 is based based on the General Equivalence Mappings (GEMS) information:

Q23.8 - Other congenital malformations of aortic and mitral valves
Q24.8 - Other specified congenital malformations of heart

Code Classification

Congenital anomalies (740–759)
- Congenital anomalies (740-759)
  - 746 Other congenital anomalies of heart

Information for Medical Professionals

Synonyms

Abnormal atrial arrangement
Abnormal atrioventricular connection
Abnormal atrioventricular connection - biventricular
Abnormal atrioventricular connection - univentricular
Abnormal attachment of tricuspid chordae tendinae
Abnormal number of leaflets
Abnormal position of cardiac valve
Abnormality of atrioventricular
Abnormality of common atrioventricular valve papillary muscle
Aborted systole
Absence of mitral chordae tendinae
Absence of primary mitral chordae tendinae
Absent atrioventricular connection with straddling valve
Absent left sided atrioventricular connection
Absent right atrioventricular valve leaflets
Accessory tissue on aortic valve cusp
Accessory tissue on common atrioventricular valve leaflet
Accessory tissue on left atrioventricular valve leaflet
Accessory tissue on mitral leaflet
Accessory tissue on right atrioventricular valve leaflet
Accessory tissue on tricuspid leaflet
Accessory tissue on truncal valve cusp
Acommissural unicuspid aortic valve
Anomalous coronary venous return
Anomalous muscle bands of left ventricle
Anomalous muscle bands of right ventricle
Anomalous valve of coronary sinus
Anterior leaflet of mitral valve attached to septum
Aortic orifice anterior left with respect to pulmonary orifice
Aortic orifice anterior right with respect to pulmonary orifice
Aortic orifice anterior with respect to pulmonary orifice
Aortic orifice left side by side with respect to pulmonary orifice
Aortic orifice posterior left with respect to pulmonary orifice
Aortic orifice posterior with respect to pulmonary orifice
Aortic orifice right side by side with respect to pulmonary orifice
Aortic valve dysplasia
Aortic valve ring hypoplasia
Aortico-left ventricular tunnel with aneurysm of intracardiac septal wall and aneurysm of extracardiac aortic wall
Aortico-left ventricular tunnel with extracardiac aneurysm of aortic wall
Arrhythmogenic right ventricular dysplasia
Atresia of common atrioventricular valve
Atrioventricular septal defect - ventricular component under inferior bridging leaflet
Atrioventricular septal defect - ventricular component under superior bridging leaflet
Atrioventricular septal defect with atrioventricular valve regurgitation through left inferior bridging leaflet lateral mural commissure
Atrioventricular septal defect with ventricular imbalance consisting of dominant left ventricle and hypoplastic right ventricle
Bifid apex of heart
Bilateral atria
Bilateral isomeric atria
Bipartite right ventricle
Brugada syndrome
Chiari's network
Cleft leaflet of tricuspid valve
Commissural fusion of aortic cusp
Commissural fusion of aortic valve
Commissural fusion of truncal valve
Common atrioventricular valve stenosis
Completely unroofed coronary sinus defect in left atrium
Congenital abnormality of anterior cardiac vein
Congenital abnormality of atrioventricular valves in atrioventricular septal defect
Congenital abnormality of cardiac vein
Congenital abnormality of great cardiac vein
Congenital abnormality of left atrioventricular valve chordae tendinae in double inlet ventricle
Congenital abnormality of left atrioventricular valve in double inlet ventricle
Congenital abnormality of left atrium
Congenital abnormality of middle cardiac vein
Congenital abnormality of mitral subvalvular apparatus
Congenital abnormality of posterior cardiac vein of left ventricle
Congenital abnormality of right atrioventricular valve chordae tendinae in double inlet ventricle
Congenital abnormality of right atrioventricular valve in double inlet ventricle
Congenital abnormality of right atrioventricular valve leaflet in double inlet ventricle
Congenital abnormality of right atrioventricular valve papillary muscle in double inlet ventricle
Congenital abnormality of tricuspid chordae tendinae
Congenital abnormality of tricuspid leaflet
Congenital abnormality of tricuspid papillary muscle
Congenital absence of aortic valve
Congenital absence of chordae tendineae
Congenital absence of coronary sinus
Congenital aneurysm of heart
Congenital aneurysm of subaortic left ventricle
Congenital anomaly of aortic valve
Congenital anomaly of heart valve
Congenital anomaly of pericardium
Congenital atresia of cardiac valve
Congenital atresia of cardiac vein
Congenital billowing of mitral valve leaflet
Congenital cardiomegaly
Congenital cleft of cardiac valve
Congenital conduction defect
Congenital deformity of mitral valve annulus
Congenital dilatation of atrium
Congenital dilatation of cardiac ventricle
Congenital disease and abnormality of heart, thoracic aorta and pericardium
Congenital diverticulum of left ventricle
Congenital enlargement of coronary sinus
Congenital epicardial cyst
Congenital extrapericardial cyst
Congenital His bundle tachycardia
Congenital hypertrophy of cardiac ventricle
Congenital hypoplasia of aortic valve
Congenital hypoplasia of cardiac vein
Congenital hypoplasia of cardiac ventricle
Congenital hypoplasia of heart
Congenital hypoplasia of mitral valve
Congenital insufficiency of tricuspid valve
Congenital intrapericardial cyst
Congenital left ventricular aneurysm
Congenital left ventricular submitral valve aneurysm
Congenital mass of mitral leaflet
Congenital pericardial cyst
Congenital pericardial defect
Congenital right ventricular aneurysm
Congenital right ventricular diverticulum
Congenital stenosis of cardiac valve
Congenital stenosis of mitral subvalvular apparatus
Congenital subaortic diverticulum
Congenital valvular insufficiency
Continuity between mitral valve and pulmonary valve
Coronary sinus abnormality
Coronary sinus defect in left atrium
Coronary sinus drainage cephalad to left superior vena cava
Coronary sinus drainage cephalad to right superior vena cava
Criss-cross heart
Criss-cross heart with leftward rotation
Criss-cross heart with rightward rotation
Diffuse hypoplasia of left ventricle
Dilatation of common atrioventricular valve annulus
Dilatation of left atrioventricular valve annulus
Dilatation of mitral annulus
Dilatation of right atrioventricular valve annulus
Dilatation of tricuspid annulus
Discontinuity between mitral valve and aortic valve
Discontinuity between mitral valve and pulmonary valve
Discordant atrioventricular connection
Discordant ventriculoarterial connection
Diverticulum of coronary sinus
Divided left atrium
Divided left atrium with all pulmonary veins to proximal chamber without communication to left atrium with extracardiac pulmonary venous chamber communication
Divided right atrium
Double aortic valve
Double inlet left ventricle
Double inlet right ventricle
Double inlet to ventricle of indeterminate morphology
Double inlet ventricle
Double mitral valve
Double orifice of common atrioventricular valve
Double orifice of left atrioventricular valve
Double orifice of mitral valve
Double orifice of right atrioventricular valve
Double orifice of right atrioventricular valve in double inlet ventricle
Double orifice of tricuspid valve
Double outlet from ventricle of indeterminate morphology
Ebstein-like downward displacement of mitral valve
Ebstein-like malformation of the mitral valve
Eccentric opening of aortic valve
Failure of growth of fetal left cardiac ventricle
Failure of growth of fetal right cardiac ventricle
Fetal cardiomegaly
Fetal heart failure with myocardial hypertrophy
Fetal myocarditis
Functionally univentricular heart
Hemicardia
Hepatic vein to left atrium and right atrium
Hepatic vein to right sided atrium
Hypoplasia of aortic valve cusp
Hypoplasia of cardiac vein
Hypoplasia of infundibular septum
Hypoplasia of left atrioventricular valve annulus in double inlet ventricle
Hypoplasia of left ventricular outflow tract
Hypoplasia of left ventricular outflow tract and trabecular area
Hypoplasia of mitral valve annulus
Hypoplasia of right atrioventricular valve annulus in double inlet ventricle
Hypoplasia of right heart
Hypoplasia of trabecular portion of left ventricle
Hypoplasia of trabecular portion of right ventricle
Hypoplastic common atrioventricular valve papillary muscle
Hypoplastic mitral papillary muscle
Hypoplastic right atrioventricular valve papillary muscle
Hypoplastic tricuspid papillary muscle
Imperforate common atrioventricular valve
Imperforate left atrioventricular valve
Imperforate left ventriculoarterial valve
Imperforate right atrioventricular valve
Imperforate right ventriculoarterial valve
Imperforate ventriculoarterial valve
Indeterminate atrial arrangement
Leakage of conduit from right atrium to pulmonary artery
Left atrial appendage - right - juxtaposition
Left atrial appendage aneurysm
Left atrial dilatation
Left atrial hypoplasia
Left atrioventricular valve atresia
Left atrioventricular valve dysplasia
Left atrioventricular valve hypoplasia
Left atrioventricular valve leaflet abnormality
Left atrioventricular valve leaflet dysplasia
Left atrioventricular valve prolapse
Left atrioventricular valve stenosis
Left atrioventricular valve stenosis in double inlet ventricle
Left ventricular diverticulum
Left ventricular hypoplasia
Left ventricular outflow tract abnormality
Left ventricular outflow tract atresia
Left ventricular outflow tract obstruction
Left ventricular outflow tract obstruction due to prolapse of Eustachian valve
Left ventricular outflow tract obstruction due to prolapsed arterial valve
Levoatrial cardinal vein
Malattachment of atrial septum
Malattachment of atrial septum with posterior aspect of septum primum to left
Malattachment of atrial septum with superior aspect of septum primum to left and posterior
Mitral valve dysplasia
Monocuspid cardiac valve
Multiple mitral papillary muscles with hammock valve
Myxomatosis of cardiac valve
Obstruction of right ventricular outflow tract due to aortico-left ventricular tunnel
Overriding left atrioventricular valve
Overriding left ventriculoarterial valve
Overriding mitral valve
Overriding right atrioventricular valve
Overriding right ventriculoarterial valve
Overriding tricuspid valve
Overriding ventriculoarterial valve
Partial agenesis of pericardium
Pericardial anomaly
Pericardial cyst
Pericardial defect
Pericardial diverticulum
Pleuropericardial cyst
Progression of fetal left ventricular outflow tract obstruction
Progression of fetal right ventricular outflow tract obstruction
Prolapse of Eustachian valve
Prolapse of Eustachian valve through atrial septum
Prolapse of Eustachian valve through tricuspid valve
Quadricuspid aortic valve
Quadricuspid cardiac valve
Quadricuspid pulmonary valve
Quadricuspid truncal valve
Regurgitation of common atrioventricular valve
Regurgitation of fetal tricuspid valve
Regurgitation of fetal truncal valve
Right atrial appendage aneurysm
Right atrial endocardial fibroelastosis
Right atrioventricular valve atresia
Right atrioventricular valve chordae too long
Right atrioventricular valve chordae too short
Right atrioventricular valve leaflets absent in double inlet ventricle
Right hypoplastic heart syndrome
Right to left cardiac shunt
Right ventricle anterior to left ventricle
Right ventricle inferior to left ventricle
Right ventricle posterior to left ventricle
Right ventricle to left of left ventricle
Right ventricular diverticulum
Right ventricular outflow obstruction - localized
Right ventricular outflow tract obstruction due to aneurysm of membranous septum
Right ventricular outflow tract obstruction due to atrioventricular valve
Right ventricular outflow tract obstruction due to common atrioventricular valve
Right ventricular outflow tract obstruction due to fibromuscular shelf
Right ventricular outflow tract obstruction due to malaligned outlet septum
Right ventricular outflow tract obstruction due to prolapse of Eustachian valve
Right ventricular outflow tract obstruction due to prolapsed arterial valve
Right ventricular outflow tract obstruction due to septal hypertrophy
Right ventricular outflow tract obstruction due to septoparietal trabeculation
Rudimentary left ventricle
Septoparietal trabeculations
Solitary aortic trunk with pulmonary atresia
Solitary pulmonary trunk with aortic atresia
Stenosis of fetal truncal valve
Straddling left atrioventricular valve
Straddling mitral valve
Straddling right atrioventricular valve
Straddling tricuspid valve
Superior to inferior ventricular relationship
Totally absent pericardium
Tricuspid annulus hypoplasia
Tricuspid truncal valve
Tripartite right ventricle
Truncal valve overriding ventricular septum
Two atrioventricular valves in double inlet ventricle
Uniatrial biventricular connection with absent left sided atrioventricular connection with straddling valve
Uniatrial biventricular connection with absent right sided atrioventricular connection with straddling valve
Unicommissural unicuspid aortic valve
Unicuspid aortic valve
Unipartite right ventricle
Univentricular atrioventricular connection with absent left sided atrioventricular connection
Univentricular atrioventricular connection with absent right sided atrioventricular connection
Ventricular imbalance

Index to Diseases and Injuries

References found for the code 746.89 in the Index of Diseases and Injuries:

Absence organ or part complete or partial
- aortic valve congenital 746.89
- pericardium congenital 746.89

Accessory congenital
- cusp s heart valve NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
  - pulmonary 746.09
- heart 746.89
  - valve NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - pulmonary 746.09
- leaflet heart valve NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
  - pulmonary 746.09
- valve heart NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
  - pulmonary 746.09

Agenesis SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Absence by site congenital
- heart 746.89
  - valve NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - aortic 746.89
    - mitral 746.89
    - pulmonary 746.01
- pericardium 746.89

Aneurysm anastomotic artery cirsoid diffuse false fusiform multiple ruptured saccular varicose 442.9
- heart chronic or with a stated duration of over 8 weeks infectional wall 414.10
  - congenital 746.89

Anomaly anomalous congenital unspecified type 759.9
- cardiac 746.9
  - valve NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.9
    - specified type NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- coronary
  - vein 746.89
- heart 746.9
  - specified type NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
  - valve NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.9
    - aortic 746.9
      - atresia 746.89
      - specified type NEC NEC "Not elsewhere classifiable"
        This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - mitral 746.9
      - atresia 746.89
      - specified type NEC NEC "Not elsewhere classifiable"
        This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- mitral leaflets valve 746.9
  - atresia 746.89
  - specified type NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- pericardium 746.89
- specified type NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular.
  - heart 746.89
    - valve NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
      - pulmonary 746.09
  - pericardium 746.89
- tricuspid leaflet valve 746.9
  - specified type NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- valve heart NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.9
  - specified type NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- vein s peripheral NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Anomaly peripheral vascular system 747.60
  - coronary 746.89

Aplasia SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Agenesis
- aortic valve congenital 746.89

Atresia atretic congenital 759.89
- aortic orifice valve 746.89
  - arch 747.11
- cardiac
  - valve 746.89
    - aortic 746.89
    - mitral 746.89
    - pulmonary 746.01
    - tricuspid 746.1
- heart
  - valve NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - aortic 746.89
    - mitral 746.89
    - pulmonary 746.01
    - tricuspid 746.1
- mitral valve 746.89
  - with atresia or hypoplasia of aortic orifice or valve with hypoplasia of ascending aorta and defective development of left ventricle 746.7
- vein NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Atresia blood vessel 747.60
  - cardiac 746.89

Bifid congenital SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Imperfect closure
- apex heart 746.89

Brugada syndrome 746.89

Cardiomegaly SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Hypertrophy cardiac 429.3
- congenital 746.89

Chiari s
- network 746.89

Cyst mucus retention serous simple
- celomic pericardium 746.89
- pericardial congenital 746.89
  - acquired secondary 423.8
- spring water pericardium 746.89

Defect defective 759.9
- pericardium 746.89

Deformity 738.9
- heart congenital 746.9
  - valve congenital NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.9
    - specified type NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- mitral leaflets valve congenital 746.9
  - Ebstein s 746.89
  - specified type NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- tricuspid leaflets valve congenital 746.9
  - specified type NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- valve valvular heart congenital 746.9
  - specified type NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89

Degeneration degenerative
- myocardium myocardial brown calcareous fatty fibrous hyaline mural muscular pigmentary senile with arteriosclerosis 429.1
  - congenital 746.89

Dilatation
- cardiac acute chronic SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Hypertrophy cardiac 429.3
  - congenital 746.89
    - valve NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
      - pulmonary 746.09
- heart acute chronic SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Hypertrophy cardiac 429.3
  - congenital 746.89
  - valve SEE ALSO See Also
    A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis
    - congenital 746.89

Disease diseased SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Syndrome
- heart organic 429.9
  - congenital NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.9
    - specified type NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
  - fetal 746.9
    - inflammatory 746.89
  - valve valvular obstructive regurgitant SEE ALSO See Also
    A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis
    - congenital NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. SEE ALSO See Also
      A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Anomaly heart valve 746.9
      - specified type NEC NEC "Not elsewhere classifiable"
        This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- valve valvular SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis
  - congenital NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. SEE ALSO See Also
    A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Anomaly heart valve 746.9
    - specified type NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89

Displacement displaced
- ventricular septum 746.89
  - with rudimentary ventricle 746.89

Distortion congenital
- heart auricle ventricle 746.89
  - valve cusp 746.89

Diverticula diverticulosis diverticulum acute multiple perforated ruptured 562.10
- heart congenital 746.89
- pericardium congenital cyst 746.89
  - acquired true 423.8
- ventricle left congenital 746.89

Double
- orifice
  - heart valve NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - pulmonary 746.09

Endocarditis chronic indeterminate interstitial marantic nonbacterial thrombotic residual sclerotic sclerous senile valvular 424.90
- aortic heart nonrheumatic valve 424.1
  - congenital 746.89
- mitral chronic double fibroid heart inactive valve with chorea 394.9
  - congenital 746.89
- tricuspid chronic heart inactive rheumatic valve with chorea 397.0
  - congenital 746.89

Fenestration fenestrated SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Imperfect closure
- cusps heart valve NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
  - pulmonary 746.09

Folds anomalous SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Anomaly specified type NEC NEC "Not elsewhere classifiable"
This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular.
- heart 746.89

Fusion fused congenital
- cusps heart valve NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
  - mitral 746.5
  - tricuspid 746.89

Hemicardia 746.89

Hyperalimentation 783.6

Hypertrophy hypertrophic
- cardiac chronic idiopathic 429.3
  - congenital NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
  - valve SEE ALSO See Also
    A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis 424.90
    - congenital NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- heart idiopathic SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Hypertrophy cardiac
  - valve SEE ALSO See Also
    A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis
    - congenital NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- ventricle ventricular heart left right SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Hypertrophy cardiac
  - congenital 746.89

Hypoplasia hypoplasis 759.89
- cardiac 746.89
  - valve see Hypoplasia heart valve
  - vein 746.89
- heart 746.89
  - left complex syndrome 746.7
  - valve NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - pulmonary 746.01
- vein s peripheral NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Hypoplasia peripheral vascular system 747.60
  - cardiac 746.89

Imperfect
- closure congenital
  - cusps heart valve NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - pulmonary 746.09
  - Eustachian valve 746.89
  - heart valve cusps NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89

Incompetency incompetence incompetent
- heart valve congenital 746.89

Insufficiency insufficient
- heart SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Insufficiency myocardial
  - valve SEE ALSO See Also
    A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis 424.90
    - congenital NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
- myocardial myocardium with arteriosclerosis 428.0
  - congenital 746.89
- tricuspid SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis tricuspid 397.0
  - congenital 746.89

Malformation congenital SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Anomaly
- heart NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.9
  - specified type NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89

Morbus
- caeruleus 746.89

Myocarditis fibroid interstitial old progressive senile with arteriosclerosis 429.0
- congenital 746.89

Nonclosure SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Imperfect closure
- Eustachian valve 746.89

Nondevelopment
- heart 746.89

Paratyphoid fever see Fever paratyphoid

Patent SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Imperfect closure
- Eustachian
  - valve 746.89

Pseudoglioma 360.44

Quadricuspid aortic valve 746.89

Stenosis cicatricial SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Stricture
- heart valve acquired SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis
  - congenital NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - aortic 746.3
    - mitral 746.5
    - pulmonary 746.02
    - tricuspid 746.1
- valve cardiac heart SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis 424.90
  - congenital NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - aortic 746.3
    - mitral 746.5
    - pulmonary 746.02
    - tricuspid 746.1
    - urethra 753.6
- valvular SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis 424.90
  - congenital NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - urethra 753.6

Stricture SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Stenosis 799.89
- heart SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Disease heart
  - congenital NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
  - valve SEE ALSO See Also
    A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis
    - congenital NEC NEC "Not elsewhere classifiable"
      This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
      - aortic 746.3
      - mitral 746.5
      - pulmonary 746.02
      - tricuspid 746.1
- valve cardiac heart SEE ALSO See Also
  A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Endocarditis 424.90
  - congenital cardiac heart NEC NEC "Not elsewhere classifiable"
    This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
    - aortic 746.3
    - mitral 746.5
    - pulmonary 746.02
    - tricuspid 746.1
    - urethra 753.6

Supernumerary congenital
- aortic cusps 746.89
- cusps heart valve NEC NEC "Not elsewhere classifiable"
  This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 746.89
  - mitral 746.5
  - pulmonary 746.09

Syndrome SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Disease
- Brugada 746.89
- retroviral seroconversion acute V08

Undeveloped undevelopment SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Hypoplasia
- heart 746.89

Information for Patients

Congenital Heart Defects

A congenital heart defect is a problem with the structure of the heart. It is present at birth. Congenital heart defects are the most common type of birth defect. The defects can involve the walls of the heart, the valves of the heart, and the arteries and veins near the heart. They can disrupt the normal flow of blood through the heart. The blood flow can slow down, go in the wrong direction or to the wrong place, or be blocked completely.

Doctors use a physical exam and special heart tests to diagnose congenital heart defects. They often find severe defects during pregnancy or soon after birth. Signs and symptoms of severe defects in newborns include:

Rapid breathing
Cyanosis - a bluish tint to the skin, lips, and fingernails
Fatigue
Poor blood circulation

Many congenital heart defects cause few or no signs and symptoms. They are often not diagnosed until children are older.

Many children with congenital heart defects don't need treatment, but others do. Treatment can include medicines, catheter procedures, surgery, and heart transplants. The treatment depends on the type of the defect, how severe it is, and a child's age, size, and general health.

NIH: National Heart, Lung, and Blood Institute

[Read More]

ICD-9 Footnotes

General Equivalence Map Definitions
The ICD-9 and ICD-10 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Approximate Flag - The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.
No Map Flag - The no map flag indicates that a code in the source system is not linked to any code in the target system.
Combination Flag - The combination flag indicates that more than one code in the target system is required to satisfy the full equivalent meaning of a code in the source system.

Index of Diseases and Injuries Definitions

And - The word "and" should be interpreted to mean either "and" or "or" when it appears in a title.
Code also note - A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
Code first - Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
Type 1 Excludes Notes - A type 1 Excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Type 2 Excludes Notes - A type 2 Excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Includes Notes - This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
Inclusion terms - List of terms is included under some codes. These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
NEC "Not elsewhere classifiable" - This abbreviation in the Alphabetic Index represents "other specified". When a specific code is not available for a condition, the Alphabetic Index directs the coder to the "other specified” code in the Tabular List.
NOS "Not otherwise specified" - This abbreviation is the equivalent of unspecified.
See - The "see" instruction following a main term in the Alphabetic Index indicates that another term should be referenced. It is necessary to go to the main term referenced with the "see" note to locate the correct code.
See Also - A "see also" instruction following a main term in the Alphabetic Index instructs that there is another main term that may also be referenced that may provide additional Alphabetic Index entries that may be useful. It is not necessary to follow the "see also" note when the original main term provides the necessary code.
7th Characters - Certain ICD-10-CM categories have applicable 7th characters. The applicable 7th character is required for all codes within the category, or as the notes in the Tabular List instruct. The 7th character must always be the 7th character in the data field. If a code that requires a 7th character is not 6 characters, a placeholder X must be used to fill in the empty characters.
With - The word "with" should be interpreted to mean "associated with" or "due to" when it appears in a code title, the Alphabetic Index, or an instructional note in the Tabular List. The word "with" in the Alphabetic Index is sequenced immediately following the main term, not in alphabetical order.

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