ICD-9 Code 277.5
Mucopolysaccharidosis
Not Valid for Submission
277.5 is a legacy non-billable code used to specify a medical diagnosis of mucopolysaccharidosis. This code was replaced on September 30, 2015 by its ICD-10 equivalent.
ICD-9: | 277.5 |
Short Description: | Mucopolysaccharidosis |
Long Description: | Mucopolysaccharidosis |
Convert 277.5 to ICD-10
The following crosswalk between ICD-9 to ICD-10 is based based on the General Equivalence Mappings (GEMS) information:
Code Classification
-
Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
-
Other metabolic disorders and immunity disorders (270-279)
- 277 Other and unspecified disorders of metabolism
-
Other metabolic disorders and immunity disorders (270-279)
Information for Medical Professionals
Index to Diseases and Injuries
References found for the code 277.5 in the Index of Diseases and Injuries:
- Brailsford Morquio disease or syndrome mucopolysaccharidosis IV 277.5
- Cardiomyopathy congestive constrictive familial infiltrative obstructive restrictive sporadic 425.4
- due to
- mucopolysaccharidosis 277.5 425.7
- due to
- Cardiopathy SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Disease heart 429.9- mucopolysaccharidosis 277.5 425.7
- Chondrodystrophia fetalis 756.4
- tarda 277.5
- Chondro osteodysplasia Morquio Brailsford type 277.5
- Chondro osteodystrophy 277.5
- Curvature
- spine acquired angular idiopathic incorrect postural 737.9
- due to or associated with
- mucopolysaccharidosis 277.5 737.40
- due to or associated with
- spine acquired angular idiopathic incorrect postural 737.9
- Degeneration degenerative
- brain cortical progressive 331.9
- in
- Hunter s disease or syndrome 277.5 330.3
- mucopolysaccharidosis 277.5 330.3
- in
- brain cortical progressive 331.9
- Deposit
- cornea corneal NEC NEC "Not elsewhere classifiable"
This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 371.10- in
- mucopolysaccharidosis 277.5 371.15
- in
- cornea corneal NEC NEC "Not elsewhere classifiable"
- Disease diseased SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Syndrome- Brailsford Morquio mucopolysaccharidosis IV 277.5
- heart organic 429.9
- due to
- mucopolysaccharidosis 277.5 425.7
- due to
- Hurler s mucopolysaccharidosis I 277.5
- Morquio Brailsford Ullrich mucopolysaccharidosis IV 277.5
- storage
- mucopolysaccharide 277.5
- Disorder SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Disease- metabolism NEC NEC "Not elsewhere classifiable"
This abbreviation in the index represents “other specified” when a specific code is not available for a condition the index directs the coder to the “other specified” code in the tabular. 277.9- mucopolysaccharide 277.5
- mucopolysaccharide 277.5
- metabolism NEC NEC "Not elsewhere classifiable"
- Dwarf dwarfism 259.4
- polydystrophic 277.5
- Dysostosis
- multiplex 277.5
- Dystrophy dystrophia 783.9
- familial
- osseous 277.5
- familial
- Eccentro osteochondrodysplasia 277.5
- Gargoylism 277.5
- Heparitinuria 277.5
- Hunter Hurler syndrome mucopolysaccharidosis II 277.5
- Hurler Hunter disease or syndrome mucopolysaccharidosis II 277.5
- Kyphosis kyphotic acquired postural 737.10
- due to or associated with
- mucopolysaccharidosis 277.5 737.41
- Morquio Brailsford type spinal 277.5 737.41
- due to or associated with
- Lipochondrodystrophy 277.5
- Lordosis acquired postural 737.20
- due to or associated with
- mucopolysaccharidosis 277.5 737.42
- due to or associated with
- Maroteaux Lamy syndrome mucopolysaccharidosis VI 277.5
- Morquio Brailsford Ullrich disease or syndrome mucopolysaccharidosis IV 277.5
- kyphosis 277.5
- Mucopolysaccharidosis types 1 6 277.5
- cardiopathy 277.5 425.7
- Myocardiopathy congestive constrictive familial idiopathic infiltrative obstructive primary restrictive sporadic 425.4
- due to
- mucopolysaccharidosis 277.5 425.7
- due to
- Osteochondrodystrophy 277.5
- deformans 277.5
- familial 277.5
- fetalis 756.4
- Polydystrophic oligophrenia 277.5
- Sanfilippo s syndrome mucopolysaccharidosis III 277.5
- Scheie s syndrome mucopolysaccharidosis IS 277.5
- Scoliosis acquired postural 737.30
- due to or associated with
- mucopolysaccharidosis 277.5 737.43
- due to or associated with
- Syndrome SEE ALSO See Also
A “see also” instruction following a main term in the index instructs that there is another main term that may also be referenced that may provide additional index entries that may be useful. It is not necessary to follow the “see also” note when the original main term provides the necessary code. Disease- Brailsford Morquio dystrophy mucopolysaccharidosis IV 277.5
- Hunter Hurler mucopolysaccharidosis II 277.5
- Hurler Hunter mucopolysaccharidosis II 277.5
- Maroteaux Lamy mucopolysaccharidosis VI 277.5
- Morquio Brailsford Ullrich mucopolysaccharidosis IV 277.5
- Sanfilippo s mucopolysaccharidosis III 277.5
- Scheie s mucopolysaccharidosis IS 277.5
Information for Patients
Carbohydrate Metabolism Disorders
Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder, something goes wrong with this process.
Carbohydrate metabolism disorders are a group of metabolic disorders. Normally your enzymes break carbohydrates down into glucose (a type of sugar). If you have one of these disorders, you may not have enough enzymes to break down the carbohydrates. Or the enzymes may not work properly. This causes a harmful amount of sugar to build up in your body. That can lead to health problems, some of which can be serious. Some of the disorders are fatal.
These disorders are inherited. Newborn babies get screened for many of them, using blood tests. If there is a family history of one of these disorders, parents can get genetic testing to see whether they carry the gene. Other genetic tests can tell whether the fetus has the disorder or carries the gene for the disorder.
Treatments may include special diets, supplements, and medicines. Some babies may also need additional treatments, if there are complications. For some disorders, there is no cure, but treatments may help with symptoms.
[Read More]
ICD-9 Footnotes
General Equivalence Map Definitions
The ICD-9 and ICD-10 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.
- Approximate Flag - The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.
- No Map Flag - The no map flag indicates that a code in the source system is not linked to any code in the target system.
- Combination Flag - The combination flag indicates that more than one code in the target system is required to satisfy the full equivalent meaning of a code in the source system.
Index of Diseases and Injuries Definitions
- And - The word "and" should be interpreted to mean either "and" or "or" when it appears in a title.
- Code also note - A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
- Code first - Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
- Type 1 Excludes Notes - A type 1 Excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- Type 2 Excludes Notes - A type 2 Excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
- Includes Notes - This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
- Inclusion terms - List of terms is included under some codes. These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
- NEC "Not elsewhere classifiable" - This abbreviation in the Alphabetic Index represents "other specified". When a specific code is not available for a condition, the Alphabetic Index directs the coder to the "other specified” code in the Tabular List.
- NOS "Not otherwise specified" - This abbreviation is the equivalent of unspecified.
- See - The "see" instruction following a main term in the Alphabetic Index indicates that another term should be referenced. It is necessary to go to the main term referenced with the "see" note to locate the correct code.
- See Also - A "see also" instruction following a main term in the Alphabetic Index instructs that there is another main term that may also be referenced that may provide additional Alphabetic Index entries that may be useful. It is not necessary to follow the "see also" note when the original main term provides the necessary code.
- 7th Characters - Certain ICD-10-CM categories have applicable 7th characters. The applicable 7th character is required for all codes within the category, or as the notes in the Tabular List instruct. The 7th character must always be the 7th character in the data field. If a code that requires a 7th character is not 6 characters, a placeholder X must be used to fill in the empty characters.
- With - The word "with" should be interpreted to mean "associated with" or "due to" when it appears in a code title, the Alphabetic Index, or an instructional note in the Tabular List. The word "with" in the Alphabetic Index is sequenced immediately following the main term, not in alphabetical order.