2024 ICD-10-CM Diagnosis Code Q89.3

Situs inversus

ICD-10-CM Code:
Q89.3
ICD-10 Code for:
Situs inversus
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Other congenital malformations
      (Q80-Q89)
      • Other congenital malformations, not elsewhere classified
        (Q89)

Q89.3 is a billable diagnosis code used to specify a medical diagnosis of situs inversus. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Agnathia, holoprosencephaly, situs inversus syndrome
  • Atrial situs inversus
  • Complete situs inversus with dextrocardia
  • Congenital malposition of heart
  • Congenital malposition of heart
  • Dextrocardia
  • Dextrocardia
  • Dextrocardia/situs inversus finding
  • Immotile cilia syndrome
  • Kartagener syndrome
  • Laterality sequence
  • Situs inversus abdominalis
  • Situs inversus thoracis
  • Situs inversus viscerum
  • Situs inversus with levocardia

Clinical Classification

Clinical Information

  • Levocardia

    congenital abnormalities in which the heart is in the normal position (levocardia) in the left side of the chest but some or all of the thorax or abdomen viscera are transposed laterally (situs inversus). it is also known as situs inversus with levocardia, or isolated levocardia. this condition is often associated with severe heart defects and splenic abnormalities such as asplenia or polysplenia.
  • Situs Inversus

    a congenital abnormality in which organs in the thorax and the abdomen are opposite to their normal positions (situs solitus) due to lateral transposition. normally the stomach and spleen are on the left, liver on the right, the three-lobed right lung is on the right, and the two-lobed left lung on the left. situs inversus has a familial pattern and has been associated with a number of genes related to microtubule-associated proteins.
  • Dextrocardia

    a congenital defect in which the heart is located on the right side of the thorax instead of on the left side (levocardia, the normal position). when dextrocardia is accompanied with inverted heart atria, a right-sided stomach, and a left-sided liver, the combination is called dextrocardia with situs inversus. dextrocardia may adversely affect other thoracic organs.
  • Kartagener Syndrome

    an autosomal recessive disorder characterized by a triad of dextrocardia; infertility; and sinusitis. the syndrome is caused by mutations of dynein genes encoding motility proteins which are components of sperm tails, and cilia in the respiratory and the reproductive tracts.
  • Kartagener Syndrome

    a rare autosomal recessive inherited syndrome characterized by situs inversus, bronchiectasis, and chronic sinusitis. there is a defect in the function of the cilia that line the respiratory tract.
  • Situs Inversus Thoracis

    a congenital condition in which there is complete right-to-left reversal of the position of the thoracic organs.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Dextrocardia with situs inversus
  • Mirror-image atrial arrangement with situs inversus
  • Situs inversus or transversus abdominalis
  • Situs inversus or transversus thoracis
  • Transposition of abdominal viscera
  • Transposition of thoracic viscera

Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Present on Admission (POA)

Q89.3 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA IndicatorReason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q89.3 to ICD-9-CM

  • ICD-9-CM Code: 759.3 - Situs inversus

Patient Education


Heterotaxy syndrome

Heterotaxy syndrome is a condition in which the internal organs are abnormally arranged in the chest and abdomen. The term "heterotaxy" is from the Greek words "heteros," meaning "other than," and "taxis," meaning "arrangement." Individuals with this condition have complex birth defects affecting the heart, lungs, liver, spleen, intestines, and other organs.

In the normal body, most of the organs in the chest and abdomen have a particular location on the right or left side. For example, the heart, spleen, and pancreas are on the left side of the body, and most of the liver is on the right. This normal arrangement of the organs is known as "situs solitus." Rarely, the orientation of the internal organs is completely flipped from right to left, a situation known as "situs inversus." This mirror-image orientation usually does not cause any health problems, unless it occurs as part of a syndrome affecting other parts of the body. Heterotaxy syndrome is an arrangement of internal organs somewhere between situs solitus and situs inversus; this condition is also known as "situs ambiguus." Unlike situs inversus, the abnormal arrangement of organs in heterotaxy syndrome often causes serious health problems.

Heterotaxy syndrome can alter the structure of the heart, including the attachment of the large blood vessels that carry blood to and from the rest of the body. It can also affect the structure of the lungs, such as the number of lobes in each lung and the length of the tubes (called bronchi) that lead from the windpipe to the lungs. In the abdomen, the condition can cause a person to have no spleen (asplenia) or multiple small, poorly functioning spleens (polysplenia). The liver may lie across the middle of the body instead of being in its normal position to the right of the stomach. Some affected individuals also have intestinal malrotation, which is an abnormal twisting of the intestines that occurs in the early stages of development before birth.

Depending on the organs involved, signs and symptoms of heterotaxy syndrome can include a bluish appearance of the skin or lips (cyanosis, which is due to a shortage of oxygen), breathing difficulties, an increased risk of infections, and problems with digesting food. The most serious complications are generally caused by critical congenital heart disease, a group of complex heart defects that are present from birth. Biliary atresia, a problem with the bile ducts in the liver, can also cause severe health problems in infancy.

The severity of heterotaxy syndrome varies depending on the specific abnormalities involved. Some affected individuals have only mild health problems related to the condition. At the other end of the spectrum, heterotaxy syndrome can be life-threatening in infancy or childhood, even with treatment.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.