2024 ICD-10-CM Diagnosis Code Q82.0

Hereditary lymphedema

ICD-10-CM Code:
Q82.0
ICD-10 Code for:
Hereditary lymphedema
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Other congenital malformations
      (Q80-Q89)
      • Other congenital malformations of skin
        (Q82)

Q82.0 is a billable diagnosis code used to specify a medical diagnosis of hereditary lymphedema. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Accessory eyelid
  • Anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphedema syndrome
  • CELSR1-related late-onset primary lymphedema
  • Cerebral arteriovenous malformation
  • Choanal atresia
  • Congenital atresia of nares
  • Congenital atresia of nasopharynx
  • Congenital atresia of pharynx
  • Congenital cutaneous lymphangiectasia
  • Congenital distichiasis
  • Congenital elephantiasis
  • Congenital lymphangiectasia
  • Congenital lymphangiectasia with chylous reflux
  • Congenital malformation of lymphatic vessel of skin
  • Congenital primary lymphedema of Gordon
  • Constricting band of extremity
  • Constricting band of extremity
  • Constriction ring of lower limb with lymphedema
  • Constriction ring of upper limb with lymphedema
  • Constriction ring syndrome
  • Constriction ring syndrome
  • Constriction ring syndrome of lower limb
  • Constriction ring syndrome of upper limb
  • Distichiasis
  • Distichiasis-lymphedema syndrome
  • Ectopic cilia of eyelid
  • Edema of foot
  • EPHB4-related lymphatic-related hydrops fetalis
  • GJC2-related late-onset primary lymphedema
  • Hereditary disorder of lymphatic system
  • Hereditary lymphedema
  • Hereditary lymphedema and yellow nails
  • Hereditary lymphedema type I
  • Hereditary lymphedema type II
  • Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
  • Lymphedema and cerebral arteriovenous anomaly syndrome
  • Lymphedema of lower extremity
  • Lymphedema of lower extremity
  • Lymphedema of lower extremity
  • Lymphedema of upper limb
  • Lymphedema, posterior choanal atresia syndrome
  • Macrothrombocytopenia, lymphedema, developmental delay, facial dysmorphism, camptodactyly syndrome
  • Megakaryocytic thrombocytopenia
  • Microcephalus, lymphedema, chorioretinopathy syndrome
  • PIEZO1-related generalized lymphatic dysplasia with non-immune hydrops fetalis
  • Primary lymphedema tardum
  • Progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like syndrome
  • Warts, immunodeficiency, lymphedema, anogenital dysplasia syndrome
  • Yellow nails

Clinical Classification

Clinical Information

  • Choanal Atresia

    a congenital abnormality that is characterized by a blocked choanae, the opening between the nose and the nasopharynx. blockage can be unilateral or bilateral; bony or membranous.

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Present on Admission (POA)

Q82.0 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA IndicatorReason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q82.0 to ICD-9-CM

  • ICD-9-CM Code: 757.0 - Hereditary edema of legs

Patient Education


Skin Conditions

What does your skin do?

Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:

  • Holds body fluids in, which helps prevent you from getting dehydrated
  • Keeps out harmful germs, which helps prevent infections
  • Helps you feel things like heat, cold, and pain
  • Helps control your body temperature
  • Makes vitamin D when the sun shines on it
  • Shields your body against heat and light

What problems and conditions can affect your skin?

There are many different problems and conditions which can affect your skin. Some of them can cause uncomfortable symptoms, such as itching, burning, redness, and rashes. They might also affect your appearance. Some of the more common skin conditions include:

  • Acne, which causes pimples when hair follicles under your skin get clogged up
  • Burns
  • Cuts and scrapes
  • Dandruff, flaking of the skin on your scalp (the top of your head)
  • Eczema (atopic dermatitis), which causes inflammation, redness, and irritation of the skin
  • Hives, which are red and sometimes itchy bumps on your skin
  • Insect bites
  • Psoriasis, which causes itchy, scaly red patches
  • Skin cancer
  • Skin infections

How can I keep my skin healthy?

Since your skin protects your body in many ways, it's important to try to keep your skin healthy. For example, you can:

  • Wear the right protective equipment, like gloves, long sleeves, knee and elbow pads, or helmets to protect against cuts, bumps and scrapes.
  • If you do get a cut or scrape, clean it right away with soap and warm water. Put on a bandage to protect it while it heals.
  • When you are spending time outdoors, wear long sleeves and pants and use insect repellant to prevent insect bites.
  • Prevent sunburn by covering up and using sunscreen when outdoors.
  • Wash your hands often with soap and water.
  • When you take a shower or bath, use warm (not hot) water. Use mild cleansers and wash gently (don't scrub).
  • Use moisturizers, like lotions, creams, or ointments, to prevent dry skin.

NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases


[Learn More in MedlinePlus]

Meige disease

Meige disease is a condition that affects the normal function of the lymphatic system. The lymphatic system consists of a network of vessels that transport lymphatic fluid and immune cells throughout the body. Meige disease is characterized by the abnormal transport of lymphatic fluid. When this fluid builds up abnormally, it causes swelling (lymphedema) in the lower limbs.

Meige disease is classified as a primary lymphedema, which means it is a form of lymphedema that is not caused by other health conditions. In Meige disease, the lymphatic system abnormalities are present from birth (congenital), although the swelling is not usually apparent until puberty. The swelling often begins in the feet and ankles and progresses up the legs to the knees. Some affected individuals develop non-contagious skin infections called cellulitis or erysipelas in the legs, which can further damage the vessels that carry lymphatic fluid.


[Learn More in MedlinePlus]

Milroy disease

Milroy disease is a condition that affects the normal function of the lymphatic system. The lymphatic system produces and transports fluids and immune cells throughout the body. Impaired transport with accumulation of lymph fluid can cause swelling (lymphedema). Individuals with Milroy disease typically have lymphedema in their lower legs and feet at birth or develop it in infancy. The lymphedema typically occurs on both sides of the body and may worsen over time.

Milroy disease is associated with other features in addition to lymphedema. Males with Milroy disease are sometimes born with an accumulation of fluid in the scrotum (hydrocele). Males and females may have upslanting toenails, deep creases in the toes, wart-like growths (papillomas), and prominent leg veins. Some individuals develop non-contagious skin infections called cellulitis that can damage the thin tubes that carry lymph fluid (lymphatic vessels). Episodes of cellulitis can cause further swelling in the lower limbs.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.