ICD-10 Diagnosis Code Q80.3

Congenital bullous ichthyosiform erythroderma

Diagnosis Code Q80.3

ICD-10: Q80.3
Short Description: Congenital bullous ichthyosiform erythroderma
Long Description: Congenital bullous ichthyosiform erythroderma
This is the 2017 version of the ICD-10-CM diagnosis code Q80.3

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities
    • Other congenital malformations (Q80-Q89)
      • Congenital ichthyosis (Q80)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code Q80.3 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Present on Admission (POA) Additional informationCallout TooltipPresent on Admission
The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement.

The code Q80.3 is exempt from POA reporting.

  • Bullous ichthyosiform erythroderma
  • Bullous ichthyosis
  • Bullous ichthyosis
  • Bullous ichthyosis
  • Congenital ichthyosiform erythroderma
  • Congenital non bullous ichthyosiform erythroderma
  • Congenital reticular ichthyosiform erythroderma
  • Ichthyosiform erythroderma
  • Ichthyosis bullosa of Siemens
  • Localized bullous ichthyosiform erythroderma
  • Rud's syndrome

Information for Patients

Skin Conditions

Also called: Cutaneous disorders, Dermatologic disorders

Your skin is your body's largest organ. It covers and protects your body. Your skin

  • Holds body fluids in, preventing dehydration
  • Keeps harmful microbes out, preventing infections
  • Helps you feel things like heat, cold, and pain
  • Keeps your body temperature even
  • Makes vitamin D when the sun shines on it

Anything that irritates, clogs, or inflames your skin can cause symptoms such as redness, swelling, burning, and itching. Allergies, irritants, your genetic makeup, and certain diseases and immune system problems can cause rashes, hives, and other skin conditions. Many skin problems, such as acne, also affect your appearance.

NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases

  • Acrodermatitis
  • Cradle cap
  • Cryotherapy
  • Cutaneous skin tags
  • Dry skin -- self-care
  • Erythema multiforme
  • Granuloma annulare
  • Keratosis pilaris
  • Lichen planus
  • Milia
  • Sebaceous cyst
  • Seborrheic dermatitis
  • Seborrheic keratosis
  • Skin lesion removal
  • Skin lesion removal-aftercare
  • Stasis dermatitis and ulcers

[Read More]

Epidermolytic hyperkeratosis Epidermolytic hyperkeratosis is a skin disorder that is present at birth. Affected babies may have very red skin (erythroderma) and severe blisters. Because newborns with this disorder are missing the protection provided by normal skin, they are at risk of becoming dehydrated and developing infections in the skin or throughout the body (sepsis).As affected individuals get older, blistering is less frequent, erythroderma becomes less evident, and the skin becomes thick (hyperkeratotic), especially over joints, on areas of skin that come into contact with each other, or on the scalp or neck. This thickened skin is usually darker than normal. Bacteria can grow in the thick skin, often causing a distinct odor.Epidermolytic hyperkeratosis can be categorized into two types. People with PS-type epidermolytic hyperkeratosis have thick skin on the palms of their hands and soles of their feet (palmoplantar or palm/sole hyperkeratosis) in addition to other areas of the body. People with the other type, NPS-type, do not have extensive palmoplantar hyperkeratosis but do have hyperkeratosis on other areas of the body.Epidermolytic hyperkeratosis is part of a group of conditions called ichthyoses, which refers to the scaly skin seen in individuals with related disorders. However, in epidermolytic hyperkeratosis, the skin is thick but not scaly as in some of the other conditions in the group.
[Read More]
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