ICD-10 Diagnosis Code Q79.6

Ehlers-Danlos syndrome

Diagnosis Code Q79.6

ICD-10: Q79.6
Short Description: Ehlers-Danlos syndrome
Long Description: Ehlers-Danlos syndrome
This is the 2017 version of the ICD-10-CM diagnosis code Q79.6

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities
    • Congenital malformations and deformations of the musculoskeletal system (Q65-Q79)
      • Congenital malformations of musculoskeletal system, NEC (Q79)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code Q79.6 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.
  • 756.83 - Ehlers-danlos syndrome

Present on Admission (POA) Additional informationCallout TooltipPresent on Admission
The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement.

The code Q79.6 is exempt from POA reporting.

  • Congenital anomaly of sclera
  • Corneal fragility keratoglobus, blue sclerae AND joint hypermobility
  • Cutis laxa, x-linked
  • Disorder of copper metabolism
  • Ehlers-Danlos syndrome
  • Ehlers-Danlos syndrome, dominant type 4
  • Ehlers-Danlos syndrome, dysfibronectinemic
  • Ehlers-Danlos syndrome, familial joint laxity type
  • Ehlers-Danlos syndrome, hydroxylysine-deficient
  • Ehlers-Danlos syndrome, non hydroxylysine deficient ocular type
  • Ehlers-Danlos syndrome, procollagen proteinase deficient
  • Ehlers-Danlos syndrome, procollagen proteinase resistant
  • Ehlers-Danlos syndrome, recessive type 4
  • Ehlers-Danlos syndrome, type 1
  • Ehlers-Danlos syndrome, type 2
  • Ehlers-Danlos syndrome, type 3
  • Ehlers-Danlos syndrome, type 4
  • Ehlers-Danlos syndrome, type 4
  • Ehlers-Danlos syndrome, type 5
  • Ehlers-Danlos syndrome, type 8
  • Hypermobility syndrome
  • Inherited cutis laxa
  • Laxity of ligament
  • Periodontitis co-occurrent with Ehlers-Danlos syndrome type 4
  • Periodontitis co-occurrent with genetic disorder
  • Periodontitis co-occurrent with genetic disorder
  • Scleral discoloration

Information for Patients

Ehlers-Danlos Syndrome

Also called: Cutis elastica, EDS

Ehlers-Danlos syndrome (EDS) is a group of inherited disorders that weaken connective tissues. Connective tissues are proteins that support skin, bones, blood vessels, and other organs.

EDS usually affects your skin, joints and blood vessel walls. Symptoms include

  • Loose joints
  • Fragile, small blood vessels
  • Abnormal scar formation and wound healing
  • Soft, velvety, stretchy skin that bruises easily

There are several types of EDS. They can range from mild to life-threatening. About 1 in 5,000 people has EDS. There is no cure. Treatment involves managing symptoms, often with medicines and physical therapy. It also includes learning how to protect your joints and prevent injuries.

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Ehlers-Danlos syndrome Ehlers-Danlos syndrome is a group of disorders that affect the connective tissues that support the skin, bones, blood vessels, and many other organs and tissues. Defects in connective tissues cause the signs and symptoms of Ehlers-Danlos syndrome, which vary from mildly loose joints to life-threatening complications.Previously, there were more than 10 recognized types of Ehlers-Danlos syndrome, differentiated by Roman numerals. In 1997, researchers proposed a simpler classification that reduced the number of major types to six and gave them descriptive names: the classical type (formerly types I and II), the hypermobility type (formerly type III), the vascular type (formerly type IV), the kyphoscoliosis type (formerly type VIA), the arthrochalasia type (formerly types VIIA and VIIB), and the dermatosparaxis type (formerly type VIIC). This six-type classification, known as the Villefranche nomenclature, is still commonly used. The types are distinguished by their signs and symptoms, their underlying genetic causes, and their patterns of inheritance. Since 1997, several additional forms of the condition have been described. These additional forms appear to be rare, affecting a small number of families, and most have not been well characterized.Although all types of Ehlers-Danlos syndrome affect the joints and skin, additional features vary by type. An unusually large range of joint movement (hypermobility) occurs with most forms of Ehlers-Danlos syndrome, particularly the hypermobility type. Infants with hypermobile joints often have weak muscle tone, which can delay the development of motor skills such as sitting, standing, and walking. The loose joints are unstable and prone to dislocation and chronic pain. Hypermobility and dislocations of both hips at birth are characteristic features in infants with the arthrochalasia type of Ehlers-Danlos syndrome.Many people with Ehlers-Danlos syndrome have soft, velvety skin that is highly stretchy (elastic) and fragile. Affected individuals tend to bruise easily, and some types of the condition also cause abnormal scarring. People with the classical form of Ehlers-Danlos syndrome experience wounds that split open with little bleeding and leave scars that widen over time to create characteristic "cigarette paper" scars. The dermatosparaxis type of the disorder is characterized by skin that sags and wrinkles. Extra (redundant) folds of skin may be present as affected children get older.Some forms of Ehlers-Danlos syndrome, notably the vascular type and to a lesser extent the kyphoscoliosis and classical types, can involve serious and potentially life-threatening complications due to unpredictable tearing (rupture) of blood vessels. This rupture can cause internal bleeding, stroke, and shock. The vascular type of Ehlers-Danlos syndrome is also associated with an increased risk of organ rupture, including tearing of the intestine and rupture of the uterus (womb) during pregnancy. People with the kyphoscoliosis form of Ehlers-Danlos syndrome experience severe, progressive curvature of the spine that can interfere with breathing.
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