2024 ICD-10-CM Diagnosis Code Q61.9

Cystic kidney disease, unspecified

ICD-10-CM Code:
Q61.9
ICD-10 Code for:
Cystic kidney disease, unspecified
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Congenital malformations of the urinary system
      (Q60-Q64)
      • Cystic kidney disease
        (Q61)

Q61.9 is a billable diagnosis code used to specify a medical diagnosis of cystic kidney disease, unspecified. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Unspecified diagnosis codes like Q61.9 are acceptable when clinical information is unknown or not available about a particular condition. Although a more specific code is preferable, unspecified codes should be used when such codes most accurately reflect what is known about a patient's condition. Specific diagnosis codes should not be used if not supported by the patient's medical record.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Autosomal dominant polycystic kidney disease
  • Cerebral ventriculomegaly
  • Cerebral ventriculomegaly, cystic kidney disease
  • Congenital cerebral ventriculomegaly
  • Meckel-Gruber syndrome
  • Multinodular goiter
  • Multinodular goiter, cystic kidney, polydactyly syndrome
  • Multiple congenital cysts of kidney

Clinical Classification

Clinical Information

  • Autosomal Dominant Polycystic Kidney Disease

    polycystic kidney disease inherited in an autosomal dominant pattern. symptoms usually appear at middle age and include abdominal pain, hematuria and high blood pressure. patients may develop brain aneurysms and liver cysts.
  • Autosomal Dominant Polycystic Kidney Disease Type 2

    autosomal dominant polycystic kidney disease caused by a mutation in pkd2.
  • Autosomal Dominant Polycystic Kidney Disease Type I

    autosomal dominant polycystic kidney disease caused by a mutation in pkd1.
  • Autosomal Recessive Polycystic Kidney Disease|Autosomal Recessive Polycystic Kidney|Polycystic Kidney Disease, Infantile Type

    polycystic kidney disease inherited in an autosomal recessive pattern. patients present with progressive renal failure early in life. the autosomal recessive trait is associated with abnormalities of chromosome 6.
  • CDISC Polycystic Kidney Disease (PKD) Therapeutic Area User Guide Version 1.0|Polycystic Kidney Disease (PKD) Therapeutic Area User Guide v1.0

    the 1.0 version of the polycystic kidney disease cdisc therapeutic area user guide.
  • Cystic Kidney Disease

    a congenital or acquired kidney disorder characterized by the presence of renal cysts.
  • Glomerulocystic Disease|Glomerulocystic Kidney Disease

    a condition characterized by dilatation of the bowman space and affecting more than 5% of the glomeruli.
  • IFT88 wt Allele|D13S1056E|DAF19|DAF19, C. elegans, Homolog of Gene|Intraflagellar Transport 88 Homolog (Chlamydomonas) Gene|Intraflagellar Transport 88 Homolog Gene|Intraflagellar Transport 88 wt Allele|MGC26259|Polaris Homolog Gene|Polaris, Mouse, Homolog of Gene|Probe HTg737 (Polycystic Kidney Disease, Autosomal Recessive) Gene|TG737|TG737, Mouse, Homolog of Gene|TTC10|hTg737

    human ift88 wild-type allele is located in the vicinity of 13q12.1 and is approximately 125 kb in length. this allele, which encodes intraflagellar transport protein 88 homolog, plays a role in the assembly of both cilia and autophagosomes.
  • Intraflagellar Transport Protein 88 Homolog|IFT88|Recessive Polycystic Kidney Disease Protein Tg737 Homolog|TPR Repeat Protein 10|Testicular Tissue Protein Li 93|Tetratricopeptide Repeat Domain 10|Tetratricopeptide Repeat Protein 10

    intraflagellar transport protein 88 homolog (833 aa, ~94 kda) is encoded by the human ift88 gene. this protein is involved in cilium and autophagosome assembly.
  • Medullary Cystic Kidney Disease Type I|Autosomal Dominant Interstitial Kidney Disease

    an inherited form of cystic kidney disease that leads to fibrosis and impaired renal function as a result of defects in the muc1 gene, which encodes mucin 1.
  • Medullary Cystic Kidney Disease Type II

    an inherited form of cystic kidney disease leading to fibrosis and impaired renal function that is caused by mutations in the umod gene, which encodes uromodulin/tamm-horsfall mucoprotein.
  • MUC1 wt Allele|ADMCKD|ADMCKD1|CA 15-3|CD227|EMA|H23AG|KL-6|MAM6|MCD|MCKD|MCKD1|MUC-1|MUC-1/SEC|MUC-1/X|MUC1|MUC1/ZD|Medullary Cystic Kidney Disease 1 (Autosomal Dominant) Gene|Mucin 1, Cell Surface Associated wt Allele|Mucin 1, Transmembrane Gene|Mucin 1, Tumor-Associated Epithelial Gene|Mucin 1, Urinary Gene|Mucin Like 1 Gene|Mucin-Like 1 Gene|PEM|PUM

    human muc1 wild-type allele is located within 1q21 and is approximately 121 kb in length. this allele, which encodes mucin-like protein 1, plays a role in both cellular defense by binding pathogens and in cell signaling.
  • PKD1 Gene|PKD1|PKD1|Polycystic Kidney Disease 1 (Autosomal Dominant) Gene

    this gene plays a role in kidney development.
  • PKD1 wt Allele|PBP|Polycystic Kidney Disease 1 (Autosomal Dominant) wt Allele|Polycystin 1 Gene

    human pkd1 wild-type allele is located in the vicinity of 16p13.3 and is approximately 47 kb in length. this allele, which encodes polycystin-1 protein, is involved in the development of the kidney. mutations in the gene are associated with polycystic kidney disease autosomal dominant type 1.
  • PKD1L1 Gene|PKD1L1|PKD1L1|Polycystic Kidney Disease 1 Like 1 Gene

    this gene is involved in the modulation of calcium transport.
  • PKD1L1 wt Allele|PRO19563|Polycystic Kidney Disease 1 Like 1 wt Allele|Polycystin 1-Like 1 Gene|UNQ5785/PRO19563

    human pkd1l1 wild-type allele is located in the vicinity of 7p12.3 and is approximately 174 kb in length. this allele, which encodes polycystic kidney disease protein 1-like 1 protein, plays a role in the modulation of ciliary calcium concentration.
  • Polycystic Kidney Disease Protein 1-Like 1|PC1-Like 1 Protein|PKD1L1|Polycystin-1L1

    polycystic kidney disease protein 1-like 1 (2849 aa, ~315 kda) is encoded by the human pkd1l1 gene. this protein is involved in ciliary calcium concentration modulation.
  • Polycystic Kidney Disease Protein 1-Like 2|PC1-Like 2 Protein|PKD1L2|Polycystic Kidney Disease 1-Like 2|Polycystin-1L2

    polycystic kidney disease protein 1-like 2 (2459 aa, ~273 kda) is encoded by the human pkd1l2 gene. this protein may play a role in calcium transport and receptor signaling.
  • Polycystic Kidney Disease, Infantile Severe, with Tuberous Sclerosis|Autosomal Dominant Polycystic Kidney Disease Type 1 with Tuberous Sclerosis|PKDTS|TSC2-PKD1 Contiguous Gene Deletion Syndrome

    an autosomal dominant condition caused by a contiguous gene deletion involving the pkd1 and tsc2 genes, encoding polycystin-1 and tuberin respectively. it is characterized by polycystic kidneys and tuberous sclerosis.
  • Polycystic Kidney Disease|Fibrocystic Renal Disease|PKD - Polycystic Kidney Disease

    a usually autosomal dominant and less frequently autosomal recessive genetic disorder characterized by the presence of numerous cysts in the kidneys leading to end-stage renal failure. the autosomal dominant trait is associated with abnormalities on the short arm of chromosome 16. symptoms in patients with the autosomal dominant trait usually appear at middle age and include abdominal pain, hematuria, and high blood pressure. patients may develop brain aneurysms and liver cysts. patients with the autosomal recessive trait present with progressive renal failure early in life and symptoms resulting from hepatic fibrosis. the autosomal recessive trait is associated with abnormalities of chromosome 6. polycystic kidney disease may also result as a side effect in patients on renal dialysis.
  • Polycystin-1|Autosomal Dominant Polycystic Kidney Disease Protein 1

    polycystin-1 (4303 aa, ~463 kda) is encoded by the human pkd1 gene. this protein may play a role in protein-protein and protein-carbohydrate interactions during kidney development.
  • Multinodular Goiter

    nodular goiter characterized by more than one discrete tissue mass.
  • Non-Toxic Multinodular Goiter|Nontoxic multinodular goiter

    a multinodular goiter that is not associated with changes in thyroid function or malignancy.
  • Thyrotoxicosis with Toxic Multinodular Goiter with Thyrotoxic Crisis|Thyrotoxicosis with toxic multinodular goiter with thyrotoxic crisis

    evidence of thyrotoxicosis with toxic multinodular goiter with thyrotoxic crisis.
  • Thyrotoxicosis with Toxic Multinodular Goiter without Thyrotoxic Crisis|Thyrotoxicosis with toxic multinodular goiter without thyrotoxic crisis

    evidence of thyrotoxicosis with toxic multinodular goiter without thyrotoxic crisis.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Meckel-Gruber syndrome

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Present on Admission (POA)

Q61.9 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA IndicatorReason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q61.9 to ICD-9-CM

  • ICD-9-CM Code: 753.10 - Cystic kidney diseas NOS
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Kidney Cysts

A cyst is a fluid-filled sac. You may get simple kidney cysts as you age; they are usually harmless. There are also some diseases which cause kidney cysts. One type is polycystic kidney disease (PKD). It runs in families. In PKD, many cysts grow in the kidneys. This can enlarge the kidneys and make them work poorly. About half of people with the most common type of PKD end up with kidney failure. PKD also causes cysts in other parts of the body, such as the liver.

Often, there are no symptoms at first. Later, symptoms include:

  • Pain in the back and lower sides
  • Headaches
  • Blood in the urine

Doctors diagnose PKD with imaging tests and family history. There is no cure. Treatments can help with symptoms and complications. They include medicines and lifestyle changes, and if there is kidney failure, dialysis or kidney transplants.

Acquired cystic kidney disease (ACKD) happens in people who have chronic kidney disease, especially if they are on dialysis. Unlike PKD, the kidneys are normal sized, and cysts do not form in other parts of the body. ACKD often has no symptoms. Usually, the cysts are harmless and do not need treatment. If they do cause complications, treatments include medicines, draining the cysts, or surgery.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.