ICD-10 Diagnosis Code Q61.5

Medullary cystic kidney

Diagnosis Code Q61.5

ICD-10: Q61.5
Short Description: Medullary cystic kidney
Long Description: Medullary cystic kidney
This is the 2017 version of the ICD-10-CM diagnosis code Q61.5

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities
    • Congenital malformations of the urinary system (Q60-Q64)
      • Cystic kidney disease (Q61)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code Q61.5 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Present on Admission (POA) Additional informationCallout TooltipPresent on Admission
The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement.

The code Q61.5 is exempt from POA reporting.

  • Adolescent nephronophthisis
  • Congenital cystic kidney disease
  • Infantile nephronophthisis
  • Juvenile nephronophthisis
  • Medullary cystic disease
  • Medullary cystic disease, adult type
  • Medullary cystic kidney disease type 1
  • Medullary cystic kidney disease type 2
  • Medullary sponge kidney
  • Medullary sponge kidney with nephrocalcinosis
  • Medullary sponge kidney without nephrocalcinosis
  • Nephronophthisis
  • Nephronophthisis - medullary cystic disease
  • Nephronophthisis type 4
  • Nephronophthisis type 5
  • Nephronophthisis type 6

Index of Diseases and Injuries
References found for the code Q61.5 in the Index of Diseases and Injuries:

Information for Patients

Kidney Cysts

A cyst is a fluid-filled sac. There are two types of kidney cysts.

Polycystic kidney disease (PKD) runs in families. In PKD, the cysts take the place of the normal tissue. They enlarge the kidneys and make them work poorly, leading to kidney failure. When PKD causes kidneys to fail - which usually happens after many years - people need dialysis or kidney transplantation. About half of people with the most common type of PKD end up with kidney failure. PKD also causes cysts in other parts of the body, such as the liver.

Symptoms of PKD include

  • Pain in the back and lower sides
  • Headaches
  • Urinary tract infections
  • Blood in the urine

Doctors diagnose PKD with imaging tests and family history. Treatments include medications, and, when people with PKD develop kidney failure, dialysis or kidney transplants.

Acquired cystic kidney disease (ACKD) usually happens in people who are on dialysis. Unlike PKD, the kidneys are normal sized, and cysts do not form in other parts of the body. People with ACKD already have chronic kidney disease when they develop cysts. ACKD often has no symptoms. In most cases, the cysts are harmless and do not need treatment.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases

  • Acquired Cystic Kidney Disease - NIH (National Institute of Diabetes and Digestive and Kidney Diseases)
  • Medullary cystic kidney disease
  • Polycystic kidney disease

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Medullary cystic kidney disease type 1 Medullary cystic kidney disease type 1 (MCKD1) is an inherited condition that affects the kidneys. It leads to scarring (fibrosis) and impaired function of the kidneys, usually beginning in adulthood. The kidneys filter fluid and waste products from the body. They also reabsorb needed nutrients and release them back into the blood. As MCKD1 progresses, the kidneys are less able to function, resulting in kidney failure.Declining kidney function in people with MCKD1 leads to the signs and symptoms of the condition. The features are variable, even among members of the same family. Many individuals with MCKD1 develop high blood pressure (hypertension), especially as kidney function worsens. Some develop high levels of a waste product called uric acid in the blood (hyperuricemia) because the damaged kidneys are unable to remove uric acid effectively. In a small number of affected individuals, the buildup of this waste product can cause gout, which is a form of arthritis resulting from uric acid crystals in the joints.Although the condition is named medullary cystic kidney disease, only about 40 percent of affected individuals have medullary cysts, which are fluid filled pockets found in a particular region of the kidney. When present, the cysts are usually found in the inner part of the kidney (the medullary region) or the border between the inner and outer parts (corticomedullary region). These cysts are visible by tests such as ultrasound or CT scan.
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