ICD-10 Diagnosis Code Q40.0

Congenital hypertrophic pyloric stenosis

Diagnosis Code Q40.0

ICD-10: Q40.0
Short Description: Congenital hypertrophic pyloric stenosis
Long Description: Congenital hypertrophic pyloric stenosis
This is the 2017 version of the ICD-10-CM diagnosis code Q40.0

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities
    • Other congenital malformations of the digestive system (Q38-Q45)
      • Other congenital malformations of upper alimentary tract (Q40)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code Q40.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.
  • 750.5 - Cong pyloric stenosis

Present on Admission (POA) Additional informationCallout TooltipPresent on Admission
The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement.

The code Q40.0 is exempt from POA reporting.

  • Congenital constriction of pylorus
  • Congenital hypertrophic pyloric stenosis
  • Congenital hypertrophy of pylorus
  • Congenital junctional epidermolysis bullosa
  • Congenital junctional epidermolysis bullosa-pyloric atresia syndrome
  • Congenital pyloric spasm
  • Congenital pyloric stenosis
  • Congenital stenosis of stomach
  • Gastric atresia
  • Generalized junctional epidermolysis bullosa
  • Junctional epidermolysis bullosa
  • Pyloric antral stenosis
  • Pyloric atresia
  • Pyloric obstruction
  • Pyloric stenosis
  • Pyloric stenosis
  • Pylorospasm
  • Pylorospasm

Index of Diseases and Injuries
References found for the code Q40.0 in the Index of Diseases and Injuries:

Information for Patients

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

A birth defect may affect how the body looks, works or both. Some birth defects like cleft lip or neural tube defects are structural problems that can be easy to see. To find others, like heart defects, doctors use special tests. Birth defects can vary from mild to severe. Some result from exposures to medicines or chemicals. For example, alcohol abuse can cause fetal alcohol syndrome. Infections during pregnancy can also result in birth defects. For most birth defects, the cause is unknown.

Some birth defects can be prevented. Taking folic acid can help prevent some birth defects. Talk to your doctor about any medicines you take. Some medicines can cause serious birth defects.

Babies with birth defects may need surgery or other medical treatments. Today, doctors can diagnose many birth defects in the womb. This enables them to treat or even correct some problems before the baby is born.

Centers for Disease Control and Prevention

  • Intersex

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Stomach Disorders

Also called: Gastric disorders

Your stomach is an organ between your esophagus and small intestine. It is where digestion of protein begins. The stomach has three tasks. It stores swallowed food. It mixes the food with stomach acids. Then it sends the mixture on to the small intestine.

Most people have a problem with their stomach at one time or another. Indigestion and heartburn are common problems. You can relieve some stomach problems with over-the-counter medicines and lifestyle changes, such as avoiding fatty foods or eating more slowly. Other problems like peptic ulcers or GERD require medical attention.

You should see a doctor if you have any of the following:

  • Blood when you have a bowel movement
  • Severe abdominal pain
  • Heartburn not relieved by antacids
  • Unintended weight loss
  • Ongoing vomiting or diarrhea

NIH: National Institute of Diabetes and Digestive and Kidney Diseases

  • Bezoar
  • Dumping Syndrome - NIH (National Institute of Diabetes and Digestive and Kidney Diseases)
  • EGD discharge
  • Gastrectomy
  • Gastritis
  • Gastroparesis
  • Pyloric stenosis
  • Stomach acid test
  • Upper GI and small bowel series

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Uncommon Infant and Newborn Problems

It can be scary when your baby is sick, especially when it is not an everyday problem like a cold or a fever. You may not know whether the problem is serious or how to treat it. If you have concerns about your baby's health, call your health care provider right away.

Learning information about your baby's condition can help ease your worry. Do not be afraid to ask questions about your baby's care. By working together with your health care provider, you make sure that your baby gets the best care possible.

  • Crying - excessive (0-6 months)
  • Failure to thrive
  • Hemorrhagic disease of the newborn
  • Hyperglycemia - infants
  • Neonatal respiratory distress syndrome
  • Neonatal sepsis
  • Neutropenia - infants

[Read More]
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