ICD-10 Diagnosis Code Q25.4

Other congenital malformations of aorta

Diagnosis Code Q25.4

ICD-10: Q25.4
Short Description: Other congenital malformations of aorta
Long Description: Other congenital malformations of aorta
This is the 2017 version of the ICD-10-CM diagnosis code Q25.4

Not Valid for Submission
The code Q25.4 is a "header" and not valid for submission for HIPAA-covered transactions.

Replaced Code Additional informationCallout TooltipReplaced Code
The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2016. This codes was replaced for the FY 2017 (October 1, 2016-September 30, 2017).

This code was replaced in the 2017 ICD-10 code set with the code(s) listed below.
  • Q25.40 - Congenital malformation of aorta unspecified
  • Q25.41 - Absence and aplasia of aorta
  • Q25.42 - Hypoplasia of aorta
  • Q25.43 - Congenital aneurysm of aorta
  • Q25.44 - Congenital dilation of aorta
  • Q25.45 - Double aortic arch
  • Q25.46 - Tortuous aortic arch
  • Q25.47 - Right aortic arch
  • Q25.48 - Anomalous origin of subclavian artery
  • Q25.49 - Other congenital malformations of aorta

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the circulatory system (Q20-Q28)
      • Congenital malformations of great arteries (Q25)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code Q25.4 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)

  • CARDIAC CONGENITAL AND VALVULAR DISORDERS WITH MCC 306
  • CARDIAC CONGENITAL AND VALVULAR DISORDERS WITHOUT MCC 307

Synonyms
  • Abnormal course of aortic arch
  • Abnormal course of aortic arch and descending aorta
  • Abnormality of aortic arch
  • Abnormality within thorax due to interruption of aortic arch
  • Aneurysm of aortic sinus of Valsalva with protrusion into left atrium
  • Aneurysm of aortic sinus of Valsalva with protrusion into left ventricle
  • Aneurysm of aortic sinus of Valsalva with protrusion into pericardial cavity
  • Aneurysm of aortic sinus of Valsalva with protrusion into pulmonary artery
  • Aneurysm of aortic sinus of Valsalva with protrusion into right atrium
  • Aneurysm of aortic sinus of Valsalva with protrusion into right ventricle
  • Aneurysm of aortic sinus of Valsalva without rupture
  • Anomalies of the aorta excluding coarction
  • Anomalous origin of ductus arteriosus from aortic diverticulum
  • Anomalous origin of ligamentum arteriosum from aortic diverticulum
  • Anomalous origin of ligamentum arteriosum from retroesophageal aortic diverticulum
  • Anomalous origin of the aortic arch
  • Aorta to right ventricle tunnel
  • Aortic arch centrally descending
  • Aortic arch hypoplasia between carotid arteries
  • Aortic arch hypoplasia between subclavian and common carotid arteries
  • Aortic arch hypoplasia distal to subclavian artery
  • Aortic left ventricular tunnel
  • Aortic left ventricular tunnel
  • Aortic left ventricular tunnel with right coronary artery from tunnel
  • Aortic root congenital abnormality
  • Aortic sinus of Valsalva aneurysm from left coronary sinus
  • Aortic sinus of Valsalva aneurysm from noncoronary sinus
  • Aortic sinus of Valsalva aneurysm from right coronary sinus
  • Aortic tunnel
  • Aortic tunnel
  • Aortico-left ventricular tunnel of simple type
  • Aortico-left ventricular tunnel with aneurysm of intracardiac septal wall and aneurysm of extracardiac aortic wall
  • Aortico-left ventricular tunnel with intracardiac aneurysm of septal portion
  • Aplasia of aorta
  • Ascending aorta absent
  • Atresia of aortic arch with fibrous cord
  • Atresia of aortic arch with fibrous cord between left common carotid artery and right common carotid artery
  • Atresia of aortic arch with fibrous cord between subclavian artery and common carotid artery
  • Atresia of aortic arch with fibrous cord distal to subclavian artery
  • Cervical aortic arch
  • Congenital abnormalities of thoracic aortic branches
  • Congenital abnormality of ascending aorta
  • Congenital abnormality of supraaortic branch of thoracic aorta
  • Congenital abnormality of thoracic aorta and pulmonary arteries
  • Congenital abnormality of thoracic aorta and pulmonary arteries
  • Congenital absence of aorta
  • Congenital aneurysm of aorta
  • Congenital aneurysm of aorta
  • Congenital aneurysm of ascending aorta
  • Congenital aneurysm of heart
  • Congenital aneurysm of sinus of Valsalva
  • Congenital aneurysm of systemic artery
  • Congenital aneurysm of systemic artery
  • Congenital anomaly of aorta
  • Congenital anomaly of aortic arch
  • Congenital anomaly of aortic arch AND/OR descending aorta
  • Congenital atresia of aortic arch
  • Congenital duplication of aorta
  • Congenital hypoplasia of abdominal aorta
  • Congenital hypoplasia of aorta
  • Congenital hypoplasia of aortic arch
  • Congenital hypoplasia of ascending aorta
  • Congenital hypoplasia of descending aorta
  • Congenital hypoplasia of thoracoabdominal aorta
  • Congenital malposition of aorta
  • Congenital malposition of subclavian artery
  • Congenital malposition of subclavian artery
  • Congenital peripheral aneurysm
  • Congenital peripheral aneurysm
  • Congenital tortuosity of branch of aortic arch
  • Descending aorta anterior and same side as azygos vein with absent inferior vena cava
  • Descending aorta anterior and same side as azygos vein with azygos continuity of inferior vena cava
  • Developmental malformation of branchial arch
  • Dextraposition of aorta
  • Dextraposition of aorta
  • Dextraposition of aorta
  • Dextroposition of aorta
  • Dextroposition of aorta
  • Dextroposition of aorta
  • Double aortic arch
  • Double aortic arch with balanced arches
  • Double aortic arch with both patent
  • Double aortic arch with left arch dominant
  • Double aortic arch with left arch dominant and atresia of right arch
  • Double aortic arch with left arch dominant and right arch patent
  • Double aortic arch with right arch dominant
  • Double aortic arch with right arch dominant and atresia of left arch
  • Double aortic arch with right arch dominant and atresia of left arch and left ligament to diverticulum
  • Double aortic arch with right arch dominant and left arch patent
  • Double aortic arch with unilateral atresia
  • Double aortic arch with unilateral hypoplasia
  • Ductus arteriosus from retroesophageal aortic diverticulum
  • Hypoplasia of aorta
  • Interrupted aortic arch
  • Interrupted aortic arch between left common carotid and brachiocephalic artery
  • Interrupted aortic arch between left subclavian and left common carotid artery
  • Interrupted aortic arch distal to left subclavian artery
  • Interruption of aortic arch between left common carotid artery and right common carotid artery
  • Interruption of aortic arch between subclavian artery and common carotid artery
  • Interruption of aortic arch distal to subclavian artery
  • Isolation of branch of aortic arch
  • Isolation of branch of aortic arch
  • Isolation of branch of aortic arch
  • Isolation of left subclavian artery
  • Isolation of right subclavian artery
  • Isolation of subclavian artery
  • Isolation of subclavian artery
  • Kommerell's diverticulum
  • Left aortic arch and right descending aorta
  • Major aortopulmonary collateral artery
  • Major systemic to pulmonary collateral artery
  • Malalignment of aortic sinus in relation to pulmonary sinus
  • Overriding aorta
  • Persistent aortic arch convolutions
  • Persisting fifth aortic arch
  • Persisting fifth aortic arch with atresia of fourth arch
  • Persisting fifth aortic arch with double barrell arch
  • Postductal coarctation of aorta
  • Postductal hypoplasia of aorta
  • Postductal interruption of aorta
  • Preductal coarctation of aorta
  • Preductal coarctation of aorta
  • Preductal hypoplasia of aorta
  • Preductal interruption of aorta
  • Pseudocoarctation of aorta
  • Retroesophageal aortic arch
  • Right aortic arch branching pattern
  • Ruptured sinus of Valsalva
  • Ruptured sinus of Valsalva into left ventricle
  • Ruptured sinus of Valsalva into right atrium
  • Ruptured sinus of Valsalva into right ventricle
  • Sinus of Valsalva abnormality
  • Sinus of Valsalva aneurysm with rupture
  • Solitary aortic trunk with pulmonary atresia
  • Systemic to pulmonary collateral artery from abdominal aorta
  • Systemic to pulmonary collateral artery from descending thoracic aorta
  • Thoracic aortic coarctation
  • Thoracic aortic coarctation
  • Thoracic aortic coarctation
  • Tortuosity of branch of aortic arch
  • Tortuosity of systemic artery
  • Tubular hypoplasia of aorta
  • Vascular ring of aorta
  • Vascular ring with left aortic arch
  • Vascular ring with left aortic arch and retroesophageal right descending aorta and right arterial duct arising from aortic diverticulum and aberrant right subclavian artery
  • Vascular ring with left aortic arch and retrotracheal right patent arterial duct
  • Vascular ring with left aortic arch and right arterial duct arising from aberrant retroesophageal right subclavian artery
  • Vascular ring with left aortic arch and right arterial duct arising from retroesophageal aortic diverticulum
  • Vascular ring with left aortic arch and right arterial duct arising from retroesophageal aortic diverticulum and aberrant right subclavian artery
  • Vascular ring with left aortic arch and right arterial duct ligament arising from retroesophageal aortic diverticulum with aberrant right subclavian artery
  • Vascular ring with left aortic arch and right arterial ligament
  • Vascular ring with left aortic arch and right patent arterial duct
  • Vascular ring with left aortic arch to right descending aorta and right arterial ligament
  • Vascular ring with left aortic arch to right descending aorta and right patent arterial duct
  • Vascular ring with mirror image branching of right aortic arch and left ligamentum arteriosum
  • Vascular ring with right aortic arch
  • Vascular ring with right aortic arch and left ductus arteriosus from anomalous retroesophageal brachiocephalic artery
  • Vascular ring with right aortic arch and left ductus arteriosus from anomalous retroesophageal left subclavian artery
  • Vascular ring with right aortic arch and left ductus arteriosus from retroesophageal diverticulum of aorta
  • Vascular ring with right aortic arch and left ductus arteriosus from retroesophageal diverticulum of aorta and anomalous left subclavian artery
  • Vascular ring with right aortic arch and left ligamentum arteriosum
  • Vascular ring with right aortic arch and left ligamentum arteriosum between left subclavian artery and left common carotid artery
  • Vascular ring with right aortic arch and left ligamentum arteriosum with anomalous retroesophageal left subclavian artery
  • Vascular ring with right aortic arch and left patent ductus arteriosus
  • Vascular ring with right aortic arch and right arterial ligament with absent left pulmonary artery
  • Vascular ring with right aortic arch and right patent arterial duct with absent left pulmonary artery

Index of Diseases and Injuries
References found for the code Q25.4 in the Index of Diseases and Injuries:


Information for Patients


Congenital Heart Defects

A congenital heart defect is a problem with the structure of the heart. It is present at birth. Congenital heart defects are the most common type of birth defect. The defects can involve the walls of the heart, the valves of the heart, and the arteries and veins near the heart. They can disrupt the normal flow of blood through the heart. The blood flow can slow down, go in the wrong direction or to the wrong place, or be blocked completely.

Doctors use a physical exam and special heart tests to diagnose congenital heart defects. They often find severe defects during pregnancy or soon after birth. Signs and symptoms of severe defects in newborns include

  • Rapid breathing
  • Cyanosis - a bluish tint to the skin, lips, and fingernails
  • Fatigue
  • Poor blood circulation

Many congenital heart defects cause few or no signs and symptoms. They are often not diagnosed until children are older.

Many children with congenital heart defects don't need treatment, but others do. Treatment can include medicines, catheter procedures, surgery, and heart transplants. The treatment depends on the type of the defect, how severe it is, and a child's age, size, and general health.

NIH: National Heart, Lung, and Blood Institute

  • Atrial septal defect
  • Bicuspid aortic valve
  • Congenital heart defect corrective surgeries
  • Congenital heart disease
  • Cyanotic heart disease
  • Dextrocardia
  • Echocardiogram -- children
  • Heart murmurs and other sounds
  • Patent ductus arteriosus
  • Ventricular septal defect


[Read More]
Previous Code
Previous Code Q25.3
Next Code
Q25.40 Next Code