ICD-10 Diagnosis Code Q25.3

Supravalvular aortic stenosis

Diagnosis Code Q25.3

ICD-10: Q25.3
Short Description: Supravalvular aortic stenosis
Long Description: Supravalvular aortic stenosis
This is the 2017 version of the ICD-10-CM diagnosis code Q25.3

Code Classification
  • Congenital malformations, deformations and chromosomal abnormalities
    • Congenital malformations of the circulatory system (Q20-Q28)
      • Congenital malformations of great arteries (Q25)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code Q25.3 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Present on Admission (POA) Additional informationCallout TooltipPresent on Admission
The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement.

The code Q25.3 is exempt from POA reporting.

  • Aortic root congenital abnormality
  • Atresia and stenosis of aorta
  • Congenital stenosis of aorta
  • Congenital stenosis of aorta
  • Congenital stenosis of aortic arch
  • Congenital stenosis of aortic valve
  • Congenital stenosis of cardiac valve
  • Congenital supravalvular aortic stenosis
  • Obstruction of aortic arch
  • Obstruction of ascending aorta
  • Postductal aortic stenosis
  • Postductal coarctation of aorta
  • Preductal aortic stenosis
  • Preductal coarctation of aorta
  • Stenosis of thoracic aorta
  • Stenosis of thoracic aorta
  • Supravalvar aortic stenosis
  • Thoracic aortic coarctation
  • Thoracic aortic coarctation

Index of Diseases and Injuries
References found for the code Q25.3 in the Index of Diseases and Injuries:

Information for Patients

Congenital Heart Defects

A congenital heart defect is a problem with the structure of the heart. It is present at birth. Congenital heart defects are the most common type of birth defect. The defects can involve the walls of the heart, the valves of the heart, and the arteries and veins near the heart. They can disrupt the normal flow of blood through the heart. The blood flow can slow down, go in the wrong direction or to the wrong place, or be blocked completely.

Doctors use a physical exam and special heart tests to diagnose congenital heart defects. They often find severe defects during pregnancy or soon after birth. Signs and symptoms of severe defects in newborns include

  • Rapid breathing
  • Cyanosis - a bluish tint to the skin, lips, and fingernails
  • Fatigue
  • Poor blood circulation

Many congenital heart defects cause few or no signs and symptoms. They are often not diagnosed until children are older.

Many children with congenital heart defects don't need treatment, but others do. Treatment can include medicines, catheter procedures, surgery, and heart transplants. The treatment depends on the type of the defect, how severe it is, and a child's age, size, and general health.

NIH: National Heart, Lung, and Blood Institute

  • Atrial septal defect
  • Bicuspid aortic valve
  • Congenital heart defect corrective surgeries
  • Congenital heart disease
  • Cyanotic heart disease
  • Dextrocardia
  • Echocardiogram -- children
  • Heart murmurs and other sounds
  • Patent ductus arteriosus
  • Ventricular septal defect

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Heart Valve Diseases

Also called: Valvular heart disease

Your heart has four valves. Normally, these valves open to let blood flow through or out of your heart, and then shut to keep it from flowing backward. But sometimes they don't work properly. If they don't, you could have

  • Regurgitation - when blood leaks back through the valve in the wrong direction
  • Mitral valve prolapse - when one of the valves, the mitral valve, has "floppy" flaps and doesn't close tightly. It's one of the most common heart valve conditions. Sometimes it causes regurgitation.
  • Stenosis - when the valve doesn't open enough and blocks blood flow

Valve problems can be present at birth or caused by infections, heart attacks, or heart disease or damage. The main sign of heart valve disease is an unusual heartbeat sound called a heart murmur. Your doctor can hear a heart murmur with a stethoscope. But many people have heart murmurs without having a problem. Heart tests can show if you have a heart valve disease. Some valve problems are minor and do not need treatment. Others might require medicine, medical procedures, or surgery to repair or replace the valve.

NIH: National Heart, Lung, and Blood Institute

  • Aortic insufficiency
  • Aortic stenosis
  • Aortic valve surgery - minimally invasive
  • Aortic valve surgery - open
  • Bicuspid aortic valve
  • Heart murmurs and other sounds
  • Heart valve surgery
  • Tricuspid regurgitation

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Supravalvular aortic stenosis Supravalvular aortic stenosis (SVAS) is a heart defect that develops before birth. This defect is a narrowing (stenosis) of the large blood vessel that carries blood from the heart to the rest of the body (the aorta). The condition is described as supravalvular because the section of the aorta that is narrowed is located just above the valve that connects the aorta with the heart (the aortic valve). Some people with SVAS also have defects in other blood vessels, most commonly stenosis of the artery from the heart to the lungs (the pulmonary artery). An abnormal heart sound during a heartbeat (heart murmur) can often be heard during a chest exam. If SVAS is not treated, the aortic narrowing can lead to shortness of breath, chest pain, and ultimately heart failure.The severity of SVAS varies considerably, even among family members. Some affected individuals die in infancy, while others never experience symptoms of the disorder.
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