2024 ICD-10-CM Diagnosis Code Q24.8

Other specified congenital malformations of heart

ICD-10-CM Code:
Q24.8
ICD-10 Code for:
Other specified congenital malformations of heart
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Congenital malformations of the circulatory system
      (Q20-Q28)
      • Other congenital malformations of heart
        (Q24)

Q24.8 is a billable diagnosis code used to specify a medical diagnosis of other specified congenital malformations of heart. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • 3C syndrome
  • Abdominal heart
  • Abnormal communication between pericardial sac and peritoneal cavity
  • Abnormal left ventricular muscle band
  • Abnormal number of cusps
  • Abnormal position of cardiac valve
  • Abnormal ventriculoarterial connection with usual origin of left coronary artery from aortic sinus to right of nonfacing aortic sinus and usual origin of right coronary artery from aortic sinus to left of nonfacing aortic sinus
  • Abnormality of common atrioventricular valve chordae tendinae
  • Abnormality of common atrioventricular valve chordae tendinae
  • Abnormality of common atrioventricular valve papillary muscle
  • Abnormality of mitral chordae tendinae
  • Abnormality of mitral chordae tendinae
  • Abnormality of right atrioventricular valve chordae tendinae
  • Abnormality of right atrioventricular valve chordae tendinae
  • Abnormality of right atrioventricular valve chordae tendinae
  • Abnormality of right atrioventricular valve chordae tendinae
  • Abnormality of tricuspid chordae tendinae
  • Abnormality of truncal valve cusp
  • Absence of mitral chordae tendinae
  • Absence of primary mitral chordae tendinae
  • Absent common atrioventricular valve papillary muscle
  • Absent left atrioventricular valve leaflets
  • Absent mitral papillary muscle
  • Absent right atrioventricular valve leaflets
  • Absent right atrioventricular valve leaflets
  • Absent tricuspid papillary muscle
  • Acardia
  • Acardia
  • Acardia
  • Acardiacus anceps
  • Acardius
  • Accessory tissue on truncal valve cusp
  • Acquired abnormality of right cardiac ventricle
  • Acquired abnormality of right cardiac ventricle
  • Acquired stenosis of subpulmonary area
  • Acquired stenosis of subpulmonary area
  • Acquired subaortic stenosis
  • Acquired subaortic stenosis
  • Acquired subaortic stenosis
  • Acquired subaortic stenosis associated with functionally univentricular heart
  • Acquired subaortic stenosis associated with functionally univentricular heart
  • Acquired subaortic stenosis associated with functionally univentricular heart
  • Acquired subaortic stenosis due to restrictive ventricular septal defect associated with functionally univentricular heart
  • Acquired subpulmonary stenosis associated with functionally univentricular heart
  • Acquired subpulmonary stenosis associated with functionally univentricular heart
  • Acquired subpulmonary stenosis due to restrictive ventricular defect associated with functionally univentricular heart
  • Anomalous bands of heart
  • Anomalous cardiac muscle bands
  • Anomalous muscle bands of left ventricle
  • Anomalous muscle bands of right ventricle
  • Anomalous ventricular bands
  • Anterolateral muscle band
  • Aortic left ventricular tunnel
  • Aortic tunnel
  • Apex of heart anterior to cardiac base
  • Apex of heart posterior to cardiac base
  • Arcade abnormality of right atrioventricular valve chordae
  • Atresia of common atrioventricular valve
  • Atresia of common atrioventricular valve
  • Atresia of systemic vein
  • Atrioventricular septal defect - ventricular component under superior bridging leaflet
  • Atrioventricular septal defect with atrial and ventricular components and separate atrioventricular valves
  • Atrioventricular septal defect with atrioventricular valve regurgitation
  • Atrioventricular septal defect with atrioventricular valve regurgitation
  • Atrioventricular septal defect with atrioventricular valve regurgitation
  • Atrioventricular septal defect with atrioventricular valve regurgitation
  • Atrioventricular septal defect with atrioventricular valve regurgitation
  • Atrioventricular septal defect with atrioventricular valve regurgitation
  • Atrioventricular septal defect with atrioventricular valve regurgitation
  • Atrioventricular septal defect with atrioventricular valve regurgitation through left inferior bridging leaflet lateral mural commissure
  • Atrioventricular septal defect with atrioventricular valve regurgitation through left septal commissure
  • Atrioventricular septal defect with atrioventricular valve regurgitation through left superior bridging leaflet lateral mural commissure
  • Atrioventricular septal defect with atrioventricular valve regurgitation through right anterosuperior inferior mural commissure
  • Atrioventricular septal defect with atrioventricular valve regurgitation through right anterosuperior superior bridging leaflet commissure
  • Atrioventricular septal defect with atrioventricular valve regurgitation through right inferior bridging leaflet inferior mural commissure
  • Atrioventricular septal defect with atrioventricular valve regurgitation through right septal commissure
  • Atrioventricular septal defect with ventricular component and interchordal shunting under superior bridging leaflet
  • Atypical left ventricular component of common atrioventricular valve
  • Atypical right ventricular component of common atrioventricular valve
  • Bicuspid truncal valve
  • Bifid apex of heart
  • Bilateral deficient infundibula
  • Brachydactyly of hand
  • Bulbus cordis and cardiac septal closure anomalies
  • Cardiomegaly
  • Chiari's network
  • Coenzyme Q10 deficiency
  • Commissural fusion of truncal valve
  • Common atrioventricular valve chordae to outlet septum
  • Common atrioventricular valve chordae too short
  • Common atrioventricular valve prolapse
  • Common atrioventricular valve with unbalanced commitment of valve to ventricle
  • Congenital abnormality of anterior cardiac vein
  • Congenital abnormality of arterial valves
  • Congenital abnormality of atrioventricular valve leaflet in atrioventricular septal defect
  • Congenital abnormality of atrioventricular valve papillary muscle in atrioventricular septal defect
  • Congenital abnormality of atrioventricular valves in atrioventricular septal defect
  • Congenital abnormality of left atrioventricular valve in double inlet ventricle
  • Congenital abnormality of left atrioventricular valve in double inlet ventricle
  • Congenital abnormality of left atrioventricular valve papillary muscle
  • Congenital abnormality of left atrioventricular valve papillary muscle
  • Congenital abnormality of left atrioventricular valve papillary muscle
  • Congenital abnormality of left atrioventricular valve papillary muscle
  • Congenital abnormality of right atrioventricular valve chordae tendinae in double inlet ventricle
  • Congenital abnormality of right atrioventricular valve in double inlet ventricle
  • Congenital abnormality of right atrioventricular valve leaflet in double inlet ventricle
  • Congenital abnormality of right atrioventricular valve papillary muscle
  • Congenital abnormality of right atrioventricular valve papillary muscle
  • Congenital abnormality of right atrioventricular valve papillary muscle
  • Congenital abnormality of right atrioventricular valve papillary muscle
  • Congenital abnormality of right atrioventricular valve papillary muscle
  • Congenital abnormality of right atrioventricular valve papillary muscle in double inlet ventricle
  • Congenital abnormality of tricuspid chordae tendinae
  • Congenital abnormality of tricuspid papillary muscle
  • Congenital abnormality of truncal valve
  • Congenital abnormality of truncal valve
  • Congenital abnormality of truncal valve
  • Congenital abnormality of truncal valve
  • Congenital abnormality of truncal valve
  • Congenital absence of chordae tendineae
  • Congenital absence of heart structure
  • Congenital absence of left atrioventricular valve papillary muscle
  • Congenital absence of mitral valve
  • Congenital absence of mitral valve
  • Congenital absence of mitral valve
  • Congenital absence of papillary muscle
  • Congenital absence of papillary muscle
  • Congenital absence of right atrioventricular valve papillary muscle
  • Congenital absence of tricuspid valve
  • Congenital aneurysm of heart
  • Congenital anomaly of atrioventricular valve
  • Congenital anomaly of body cavity
  • Congenital anomaly of heart valve
  • Congenital anomaly of left-sided atrioventricular valve in double inlet ventricle
  • Congenital anomaly of myocardium
  • Congenital anomaly of pericardium
  • Congenital anomaly of pericardium
  • Congenital anomaly of right-sided atrioventricular valve in double inlet ventricle
  • Congenital atresia of cardiac valve
  • Congenital atresia of cardiac vein
  • Congenital cardiac diverticulum
  • Congenital cardiomegaly
  • Congenital cataract, hypertrophic cardiomyopathy, mitochondrial myopathy syndrome
  • Congenital cleft of cardiac valve
  • Congenital cleft of cardiac valve
  • Congenital cleft of cardiac valve
  • Congenital cyst of mediastinum
  • Congenital cyst of mediastinum
  • Congenital cyst of mediastinum
  • Congenital cyst of mediastinum
  • Congenital diaphragmatic hernia
  • Congenital diverticulum of left ventricle
  • Congenital dysplasia of cardiac valve
  • Congenital dysplasia of truncal valve
  • Congenital enlargement of coronary sinus
  • Congenital epicardial cyst
  • Congenital extrapericardial cyst
  • Congenital fusion of kidneys
  • Congenital fusion of left atrioventricular valve papillary muscles
  • Congenital fusion of right atrioventricular valve papillary muscles
  • Congenital heart disease, septal and bulbar anomalies
  • Congenital hypertrophy of cardiac ventricle
  • Congenital hypoplasia of heart
  • Congenital hypoplasia of tricuspid valve
  • Congenital hypoplastic left atrioventricular valve papillary muscle
  • Congenital hypoplastic right atrioventricular valve papillary muscle
  • Congenital intrapericardial cyst
  • Congenital levorotation of heart
  • Congenital malposition of cardiac apex
  • Congenital malposition of heart
  • Congenital malrotation of heart
  • Congenital parachute malformation of left atrioventricular valve
  • Congenital parachute malformation of right atrioventricular valve
  • Congenital pericardial cyst
  • Congenital pericardial defect
  • Congenital regurgitation of truncal valve
  • Congenital sacral meningocele
  • Congenital stenosis of cardiac valve
  • Congenital stenosis of truncal valve
  • Congenital subaortic diverticulum
  • Congenital subaortic stenosis
  • Congenital subaortic stenosis due to restrictive ventricular septal defect associated with functionally univentricular heart
  • Congenital subpulmonary stenosis due to restrictive ventricular defect associated with functionally univentricular heart
  • Congenital valvular insufficiency
  • Criss-cross heart
  • Criss-cross heart with leftward rotation
  • Criss-cross heart with rightward rotation
  • Cyst of mediastinum
  • Cyst of mediastinum
  • Cyst of mediastinum
  • Cyst of mediastinum
  • Cyst of mediastinum
  • Deafness, encephaloneuropathy, obesity, valvulopathy syndrome
  • Deficiency of atrioventricular valve leaflet in atrioventricular septal defect
  • Deficient mural leaflet of left ventricular component of common atrioventricular valve
  • Diffuse hypoplasia of right ventricle
  • Disorder of ascending aorta due to conotruncal malformation
  • Double cardiac valve orifice
  • Double inlet right ventricle
  • Double orifice of common atrioventricular valve
  • Double orifice of right atrioventricular valve
  • Double orifice of right atrioventricular valve in double inlet ventricle
  • Doubly committed juxta-arterial outlet ventricular septal defect with anteriorly malaligned outlet septum
  • Doubly committed juxta-arterial outlet ventricular septal defect with perimembranous extension and anteriorly malaligned outlet septum
  • Doubly committed juxta-arterial outlet ventricular septal defect with perimembranous extension and posteriorly malaligned outlet septum
  • Doubly committed juxta-arterial outlet ventricular septal defect with posteriorly malaligned outlet septum
  • Doubly committed juxta-arterial ventricular septal defect with anteriorly malaligned fibrous outlet septum and muscular postero-inferior rim
  • Doubly committed subarterial ventricular septal defect
  • Doubly committed subarterial ventricular septal defect
  • Doubly committed subarterial ventricular septal defect
  • Doubly committed subarterial ventricular septal defect
  • Doubly committed subarterial ventricular septal defect
  • Ectopia cordis
  • Encephalopathy, hypertrophic cardiomyopathy, renal tubular disease syndrome
  • Faciocardiorenal syndrome
  • False tendon - heart
  • Flail atrioventricular valve leaflet in atrioventricular septal defect
  • FLNA-related X-linked myxomatous valvular dysplasia
  • Functionally univentricular heart
  • Functionally univentricular heart
  • Functionally univentricular heart
  • Functionally univentricular heart
  • Functionally univentricular heart
  • Functionally univentricular heart
  • Fused common atrioventricular valve papillary muscle
  • Fused mitral papillary muscles
  • Fused tricuspid papillary muscle
  • Gelatinous atrioventricular valve leaflet in atrioventricular septal defect
  • Heart valve stenosis
  • Heart-hand syndrome type 2
  • Heart-hand syndrome type 3
  • Hemicardia
  • Holoacardius acormus
  • Holzgreve syndrome
  • Horseshoe kidney
  • Hypertrophic mitochondrial cardiomyopathy
  • Hypertrophic mitochondrial cardiomyopathy
  • Hypoplasia of left atrioventricular valve annulus in double inlet ventricle
  • Hypoplasia of left heart without intrinsic valve stenosis and without atresia
  • Hypoplasia of left ventricular outflow tract
  • Hypoplasia of left ventricular outflow tract and trabecular area
  • Hypoplasia of right atrioventricular valve annulus in double inlet ventricle
  • Hypoplasia of right ventricular inflow tract
  • Hypoplasia of right ventricular outflow tract
  • Hypoplasia of right ventricular outflow tract and trabecular area
  • Hypoplasia of trabecular portion of left ventricle
  • Hypoplasia of trabecular portion of right ventricle
  • Hypoplastic tricuspid papillary muscle
  • Imperforate common atrioventricular valve
  • Imperforate left atrioventricular valve
  • Juxtaposed atrial appendage
  • Kousseff syndrome
  • Larsen-like syndrome B3GAT3 type
  • Left atrial hypoplasia
  • Left atrioventricular valve atresia
  • Left atrioventricular valve bifoliate with fused left sided superior and inferior bridging leaflet
  • Left atrioventricular valve hypoplasia
  • Left atrioventricular valve leaflet abnormality
  • Left atrioventricular valve leaflet abnormality
  • Left atrioventricular valve stenosis
  • Left atrioventricular valve stenosis
  • Left atrioventricular valve stenosis in double inlet ventricle
  • Left ventricular diverticulum
  • Left ventricular hypoplasia
  • Left ventricular hypoplasia
  • Left ventricular hypoplasia
  • Left ventricular outflow tract obstruction due to aneurysm of membranous septum
  • Left ventricular outflow tract obstruction due to atrioventricular valve
  • Left ventricular outflow tract obstruction due to diaphragm
  • Left ventricular outflow tract obstruction due to fibromuscular tunnel
  • Left ventricular outflow tract obstruction due to neoplasm
  • Left ventricular outflow tract obstruction due to prolapsed arterial valve
  • Malaligned outlet septum
  • Mass associated with atrioventricular valve leaflet in atrioventricular septal defect
  • Membranous ventricular septum defect
  • Membranous ventricular septum defect
  • Membranous ventricular septum defect
  • Mesocardia
  • Microcephalus with cardiac defect and lung malsegmentation syndrome
  • Midline anterior apex of heart
  • Midline apex of heart
  • Midline posterior apex of heart
  • Mitral papillary muscle abnormality
  • Mitral papillary muscle abnormality
  • Mitral papillary muscle abnormality
  • Monocuspid cardiac valve
  • Multiple congenital cardiac defects
  • Multiple intracardiac shunts
  • Multiple malformation syndrome, moderate short stature, facial
  • Multiple mitral papillary muscles with hammock valve
  • Myocardial bridge of coronary artery
  • Myxoid transformation of cardiac valve
  • Noncoapting atrioventricular valve leaflet in atrioventricular septal defect
  • Obesity, colitis, hypothyroidism, cardiac hypertrophy, developmental delay syndrome
  • Outlet ventricular septal defect with anteriorly malaligned outlet septum
  • Outlet ventricular septal defect with posteriorly malaligned outlet septum
  • Overriding left atrioventricular valve
  • Overriding right atrioventricular valve
  • Parachute malformation of common atrioventricular valve
  • Parasitic twin of asymmetrical conjoined twins
  • Parasitic twin of asymmetrical conjoined twins
  • Partial agenesis of pericardium
  • Pericardial and diaphragmatic defect syndrome
  • Pericardial anomaly
  • Pericardial anomaly
  • Pericardial anomaly
  • Pericardial anomaly
  • Pericardial anomaly
  • Pericardial cyst
  • Pericardial cyst
  • Pericardial cyst
  • Pericardial cyst
  • Pericardial cyst
  • Pericardial cyst along right cardiophrenic angle
  • Pericardial defect
  • Pericardial defect
  • Pericardial defect
  • Pericardial defect
  • Pericardial defect
  • Pericardial defect
  • Pericardial diverticulum
  • Perimembranous inlet ventricular septal defect
  • Perimembranous inlet ventricular septal defect with atrioventricular septal malalignment
  • Perimembranous outlet ventricular septal defect with anteriorly malaligned outlet septum
  • Perimembranous outlet ventricular septal defect with posteriorly malaligned outlet septum
  • Perimembranous ventricular septal defect
  • Perimembranous ventricular septal defect
  • Perimembranous ventricular septal defect
  • Pleuropericardial cyst
  • Polyvalvular heart disease syndrome
  • Posteromedial muscle band
  • Potter's facies
  • Prolapse of Eustachian valve
  • Prolapse of Eustachian valve
  • Prolapse of Eustachian valve through atrial septum
  • Prolapse of Eustachian valve through tricuspid valve
  • Prominent valve of inferior vena cava
  • Pseudoacardia
  • Quadricuspid cardiac valve
  • Renal agenesis
  • Right atrial hypoplasia
  • Right atrioventricular valve chordae too long
  • Right atrioventricular valve chordae too short
  • Right atrioventricular valve hypoplasia
  • Right atrioventricular valve hypoplasia
  • Right atrioventricular valve leaflet dysplasia
  • Right atrioventricular valve leaflets absent in double inlet ventricle
  • Right atrioventricular valve prolapse
  • Right atrioventricular valve stenosis
  • Right ventricular outflow tract abnormality
  • Right ventricular outflow tract obstruction due to abnormal cardiac muscle bands
  • Right ventricular outflow tract obstruction due to common atrioventricular valve
  • Right ventricular outflow tract obstruction due to neoplasm
  • Septoparietal trabeculations
  • Short stature with valvular heart disease and characteristic facies syndrome
  • Subaortic stenosis as complication of procedure
  • Subaortic stenosis associated with functionally univentricular heart as complication of procedure
  • Subpulmonary stenosis
  • Subpulmonary stenosis
  • Subpulmonary stenosis
  • Thickened atrioventricular valve leaflet in atrioventricular septal defect
  • Thoracodidymus
  • Thoracopagus
  • Thoracopagus with separate hearts and common pericardial sac
  • Totally absent pericardium
  • Tricuspid papillary muscle abnormality
  • Tricuspid papillary muscle abnormality
  • Tricuspid papillary muscle abnormality
  • Tricuspid papillary muscle abnormality
  • Trifoliate left atrioventricular valve
  • True cleft of common atrioventricular valve leaflet
  • True cleft of left atrioventricular valve leaflet
  • True cleft of right atrioventricular valve leaflet
  • Truncal valve overriding ventricular septum
  • Truncal valve regurgitation
  • Truncal valve stenosis
  • Uhl's disease
  • Venous valvular anomaly
  • Venous valvular anomaly
  • Ventricular imbalance
  • Ventricular imbalance with dominant left ventricle and hypoplastic right ventricle
  • Ventricular septal defect with absent outlet septum and overriding truncal valve
  • Ventricular septal defect with absent outlet septum and overriding truncal valve with extension of membranous septum
  • Ventricular septal defect with absent outlet septum and overriding truncal valve with inferior muscular rim
  • X-linked intellectual disability, cardiomegaly, congestive heart failure syndrome

Clinical Classification

Clinical Information

  • Ectopia Cordis

    a rare developmental defect in which the heart is abnormally located partially or totally outside the thorax. it is the result of defective fusion of the anterior chest wall. depending on the location of the heart, ectopia cordis can be thoracic, thoracoabdominal, abdominal, and cervical.
  • Cardiomegaly

    enlargement of the heart, usually indicated by a cardiothoracic ratio above 0.50. heart enlargement may involve the right, the left, or both heart ventricles or heart atria. cardiomegaly is a nonspecific symptom seen in patients with chronic systolic heart failure (heart failure) or several forms of cardiomyopathies.
  • Cardiomegaly, Exercise-Induced

    non-pathological heart enlargement and other remodeling in cardiac morphology and electrical circuitry found in individuals who participate in intense repeated exercises.
  • Thorax

    the upper part of the trunk between the neck and the abdomen. it contains the chief organs of the circulatory and respiratory systems. (from stedman, 25th ed)
  • Congenital Diaphragmatic Hernia

    diaphragmatic hernia that is present at birth.
  • Bilateral Renal Agenesis

    a congenital abnormality characterized by the absence of both kidneys.
  • Renal Agenesis

    a congenital abnormality characterized by the absence of one or both kidneys.
  • Unilateral Renal Agenesis|Congenital Single Kidney|Congenital Solitary Kidney|Congenital Solitary Kidney

    a congenital abnormality characterized by the presence of only one kidney.
  • Pericardial Anomaly

    any abnormality involving the pericardium.
  • Horseshoe Kidney

    a congenital abnormality in which the two kidneys fuse together during fetal development to create a horseshoe-shaped structure.
  • Coenzyme Q10 Deficiency

    a genetically heterogeneous condition, typically inherited in an autosomal recessive fashion, characterized by coenzyme q10 deficiency.
  • Ectopia Cordis

    a rare congenital anomaly where the heart is formed outside of the thoracic cavity. it is associated with intracardiac lesions and other structural malformations.
  • Externalized Heart|EXTERNALIZED HEART|Ectopia Cordis|Exocardia

    a type of exocardia in which the heart develops outside of the body.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Congenital diverticulum of left ventricle
  • Congenital malformation of myocardium
  • Congenital malformation of pericardium
  • Malposition of heart
  • Uhl's disease

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Present on Admission (POA)

Q24.8 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA IndicatorReason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q24.8 to ICD-9-CM

  • ICD-9-CM Code: 746.84 - Obstruct heart anom NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
  • ICD-9-CM Code: 746.87 - Malposition of heart
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
  • ICD-9-CM Code: 746.89 - Cong heart anomaly NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Congenital Heart Defects

What are congenital heart defects?

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a baby's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

Congenital heart defects can change the way the heart pumps blood. They may make blood flow too slowly, go the wrong way, or block it completely.

There are many types of congenital heart defects. They can happen in one or more parts of the heart. The most common types are:

  • Septal defects ("hole in the heart") - openings in the wall between the left and right sides of the heart
  • Heart valve defects - problems with the valves that control the flow of blood through the heart
  • Defects in the large blood vessels that carry blood in and out of the heart

Congenital heart defects can range from very mild problems that never need treatment to life-threatening problems at birth. The most serious congenital heart defects are called critical congenital heart disease. Babies with these defects usually need surgery in the first year of life. But the symptoms of milder heart defects may not show up until childhood or adulthood.

What causes congenital heart defects?

Researchers often don't know what causes congenital heart defects. They do know that changes in a baby's genes sometimes cause a heart defect. The changed genes may come from the parents, or the changes may happen during pregnancy.

Who is more likely to have a baby with a congenital heart defect?

Several things may increase the chance that your baby has a congenital heart defect, such as:

  • Your health before and during pregnancy, including
    • Having diabetes before pregnancy or developing it in the first 3 months of pregnancy (diabetes that develops later in pregnancy isn't a major risk for heart defects). Carefully controlling your blood sugar before and during pregnancy can lower your baby's risk of congenital heart defects.
    • Having phenylketonuria (PKU), a rare inherited disorder that affects how the body uses a protein in foods. If you have PKU, eating a low-protein diet before getting pregnant can lower your baby's risk of having a congenital heart defect.
    • Having rubella (German measles) during pregnancy.
  • Your contact with certain substances during pregnancy, including
    • Smoking or secondhand smoke (breathing smoke from another smoker).
    • Certain medicines, such as angiotensin-converting (ACE) inhibitors for high blood pressure and retinoic acids for acne. If you're pregnant or plan to get pregnant, talk with your health care provider about all the medicines you take.
  • Your family history and genetics. In most cases, congenital heart defects don't run in families. But your chance of having a baby with a congenital heart defect does go up if you or the other parent has a congenital heart defect, or if you already have a child with a congenital heart defect.

What are the symptoms of congenital heart defects?

Congenital heart defects don't cause pain. The signs and symptoms are different, depending on the type and number of defects and how serious they are.

Common signs and symptoms of congenital heart defects include:

  • Cyanosis - a bluish color to the skin, lips, and fingernails. It happens when there isn't enough oxygen in the blood
  • Fatigue - your baby may be unusually sleepy and may become very tired during feedings
  • Poor blood flow
  • Fast or difficult breathing
  • Heart murmur - an unusual sound between heartbeats

What other problems do congenital heart defects cause?

Congenital heart defects don't always cause other problems. If they do, which problems you have would depend on the type and number of defects and how serious the defects are.

Children with congenital heart defects are more likely to:

  • Be smaller than other children
  • Have problems or delays in mental, and emotional growth, and behavior, such as:
    • Speech and language problems
    • Attention deficit hyperactivity disorders (ADHD)

People with congenital heart defects may develop other health conditions, including:

  • Endocarditis - an infection of lining of the heart and valves
  • Arrhythmia - a problem with the rate or rhythm of your heartbeat
  • Heart failure - when your heart can't pump enough blood to the body
  • Pulmonary hypertension - high blood pressure in your lungs
  • Kidney and liver disease

How are congenital heart defects diagnosed?

  • Before a baby is born, your provider may use ultrasound pictures of the baby's heart to look for heart defects. This is called a fetal echocardiogram. It's done between weeks 18 and 22 of pregnancy.
  • During the first few days after birth, all newborns are checked for congenital heart defects. A pulse oximeter is clipped to your baby's hands or feet to measure blood oxygen. If it shows low levels of blood oxygen, more tests will be needed to find out if your baby has a heart defect.
  • To diagnose congenital heart defects in babies, children, and adults, a provider may use many tools, including:
    • A physical exam.
    • Certain heart tests to see how the heart is working.
    • Genetic testing to see if certain gene problems caused the defect.

What are the treatments for congenital heart defects?

Treatment depends on the type of congenital heart defect and how serious it is. Possible treatments include:

  • Cardiac catheterization to repair simple defects, such as a small hole in the inside wall of the heart. A catheterization uses a thin tube guided through a vein and into the heart.
  • Heart surgery may be needed to:
    • Repair defects in the heart and blood vessels.
    • Repair or replace a heart valve.
    • Place a device in the chest to help the heart pump blood.
    • Do a heart transplant.
  • Medicine is often used if your baby has a specific type of congenital heart defect called patent ductus arteriosus.

All children and adults who have congenital heart defects need regular follow-up care from a cardiologist (a doctor who specializes in heart diseases) throughout their life, even if their defect was repaired.

Some people may need several heart surgeries or catheterizations over the years. They may also need to take medicines to help their hearts work as well as possible.

NIH: National Heart, Lung, and Blood Institute


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.