ICD-10 Diagnosis Code N04

Nephrotic syndrome

Diagnosis Code N04

ICD-10: N04
Short Description: Nephrotic syndrome
Long Description: Nephrotic syndrome
This is the 2018 version of the ICD-10-CM diagnosis code N04

Not Valid for Submission
The code N04 is a "header" and not valid for submission for HIPAA-covered transactions.

Code Classification
  • Diseases of the genitourinary system (N00–N99)
    • Glomerular diseases (N00-N08)
      • Nephrotic syndrome (N04)

Information for Medical Professionals

Index of Diseases and Injuries
References found for the code N04 in the Index of Diseases and Injuries:


Information for Patients


Kidney Diseases

Also called: Renal disease

You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters. It goes to your bladder, which stores the urine until you go to the bathroom.

Most kidney diseases attack the nephrons. This damage may leave kidneys unable to remove wastes. Causes can include genetic problems, injuries, or medicines. You have a higher risk of kidney disease if you have diabetes, high blood pressure, or a close family member with kidney disease. Chronic kidney disease damages the nephrons slowly over several years. Other kidney problems include

  • Cancer
  • Cysts
  • Stones
  • Infections

Your doctor can do blood and urine tests to check if you have kidney disease. If your kidneys fail, you will need dialysis or a kidney transplant.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases

  • ACE inhibitors (Medical Encyclopedia)
  • Acute nephritic syndrome (Medical Encyclopedia)
  • Analgesic nephropathy (Medical Encyclopedia)
  • Atheroembolic renal disease (Medical Encyclopedia)
  • Bartter syndrome (Medical Encyclopedia)
  • Bilateral hydronephrosis (Medical Encyclopedia)
  • Congenital nephrotic syndrome (Medical Encyclopedia)
  • Distal renal tubular acidosis (Medical Encyclopedia)
  • Focal segmental glomerulosclerosis (Medical Encyclopedia)
  • Glomerulonephritis (Medical Encyclopedia)
  • Goodpasture syndrome (Medical Encyclopedia)
  • IgA nephropathy (Medical Encyclopedia)
  • Injury - kidney and ureter (Medical Encyclopedia)
  • Interstitial nephritis (Medical Encyclopedia)
  • Kidney removal (Medical Encyclopedia)
  • Kidney removal - discharge (Medical Encyclopedia)
  • Medicines and Kidney Disease - NIH (National Kidney Disease Education Program)
  • Membranoproliferative GN I (Medical Encyclopedia)
  • Membranous nephropathy (Medical Encyclopedia)
  • Minimal change disease (Medical Encyclopedia)
  • Nephrocalcinosis (Medical Encyclopedia)
  • Nephrotic syndrome (Medical Encyclopedia)
  • Obstructive uropathy (Medical Encyclopedia)
  • Perirenal abscess (Medical Encyclopedia)
  • Proximal renal tubular acidosis (Medical Encyclopedia)
  • Reflux nephropathy (Medical Encyclopedia)
  • Renal papillary necrosis (Medical Encyclopedia)
  • Renal perfusion scintiscan (Medical Encyclopedia)
  • Renal vein thrombosis (Medical Encyclopedia)
  • Unilateral hydronephrosis (Medical Encyclopedia)


[Read More]

Congenital nephrotic syndrome Congenital nephrotic syndrome is a kidney condition that begins in infancy and typically leads to irreversible kidney failure (end-stage renal disease) by early childhood. Children with congenital nephrotic syndrome begin to have symptoms of the condition between birth and 3 months.The features of congenital nephrotic syndrome are caused by failure of the kidneys to filter waste products from the blood and remove them in urine. Signs and symptoms of this condition are excessive protein in the urine (proteinuria), increased cholesterol in the blood (hypercholesterolemia), an abnormal buildup of fluid in the abdominal cavity (ascites), and swelling (edema). Affected individuals may also have blood in the urine (hematuria), which can lead to a reduced number of red blood cells (anemia) in the body, abnormal blood clotting, or reduced amounts of certain white blood cells. Low white blood cell counts can lead to a weakened immune system and frequent infections in people with congenital nephrotic syndrome.Children with congenital nephrotic syndrome typically develop end-stage renal disease between ages 2 and 8, although with treatment, some may not have kidney failure until adolescence or early adulthood.
[Read More]
Previous Code
Previous Code N03.9
Next Code
N04.0 Next Code