ICD-10 Diagnosis Code M04.1

Periodic fever syndromes

Diagnosis Code M04.1

ICD-10: M04.1
Short Description: Periodic fever syndromes
Long Description: Periodic fever syndromes
This is the 2018 version of the ICD-10-CM diagnosis code M04.1

Valid for Submission
The code M04.1 is valid for submission for HIPAA-covered transactions.

Code Classification
  • Diseases of the musculoskeletal system and connective tissue (M00–M99)
    • Autoinflammatory syndromes (M04)
      • Autoinflammatory syndromes (M04)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code M04.1 is grouped in the following Diagnostic Related Group(s) (MS-DRG V34.0)

  • 545 - CONNECTIVE TISSUE DISORDERS WITH MCC
  • 546 - CONNECTIVE TISSUE DISORDERS WITH CC
  • 547 - CONNECTIVE TISSUE DISORDERS WITHOUT CC/MCC

Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

Synonyms
  • Amyloid of familial Mediterranean fever
  • Deficiency of mevalonate kinase
  • Familial Mediterranean fever
  • Hereditary inflammatory disorder involving skin
  • Hereditary periodic fever
  • Hyper-immunoglobulin D periodic fever syndrome
  • Inflammatory hereditary disorder
  • Pericarditis associated with familial Mediterranean fever
  • Tumor necrosis factor receptor-associated periodic fever syndrome

Index of Diseases and Injuries
References found for the code M04.1 in the Index of Diseases and Injuries:


Replacement Code Additional informationCallout TooltipReplacement Code
The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2017. This is a new and revised code for the FY 2018 (October 1, 2017-September 30, 2018).

This code replaces the following previously assigned ICD-10 code(s) listed below:
  • E85.0 - Non-neuropathic heredofamilial amyloidosis


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