2024 ICD-10-CM Diagnosis Code K00.5
Hereditary disturbances in tooth structure, not elsewhere classified
- ICD-10-CM Code:
- K00.5
- ICD-10 Code for:
- Hereditary disturbances in tooth structure, NEC
- Is Billable?
- Yes - Valid for Submission
- Chronic Condition Indicator: [1]
- Not chronic
- Code Navigator:
K00.5 is a billable diagnosis code used to specify a medical diagnosis of hereditary disturbances in tooth structure, not elsewhere classified. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.
Approximate Synonyms
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- Amelogenesis imperfecta
- Amelogenesis imperfecta - hypomaturation - recessive pigmented
- Amelogenesis imperfecta - hypomaturation - snow capped teeth
- Amelogenesis imperfecta - hypoplastic autosomal dominant - local
- Amelogenesis imperfecta - hypoplastic autosomal dominant - rough
- Amelogenesis imperfecta - hypoplastic autosomal dominant - smooth
- Amelogenesis imperfecta - recessive - rough
- Amelogenesis imperfecta and gingival hyperplasia syndrome
- Amelogenesis imperfecta co-occurrent with cone rod dystrophy
- Amelogenesis imperfecta, hypocalcification type
- Amelogenesis imperfecta, hypomaturation hypoplasia type with taurodontism
- Amelogenesis imperfecta, hypomaturation type
- Amelogenesis imperfecta, hypomaturation type
- Amelogenesis imperfecta, hypoplastic type
- Amelogenesis imperfecta, hypoplastic type
- Amelogenesis imperfecta, hypoplastic type
- Amelogenesis imperfecta, hypoplastic type with microdontia
- Amelogenesis imperfecta, pigmented hypomaturation type
- Atypical dentin dysplasia due to SMOC2 deficiency
- Brachyolmia
- Congenital anomaly of sclera
- Deep occlusal groove
- Dentin dysplasia
- Dentin dysplasia
- Dentin dysplasia with sclerotic bone syndrome
- Dentin dysplasia, type I
- Dentin dysplasia, type II
- Dentinogenesis imperfecta
- Dentinogenesis imperfecta
- Dentinogenesis imperfecta
- Dentinogenesis imperfecta
- Dentinogenesis imperfecta
- Dentinogenesis imperfecta - Shield's type I
- Dentinogenesis imperfecta - Shield's type II
- Dentinogenesis imperfecta - Shield's type III
- Dentinogenesis imperfecta, short stature, hearing loss, intellectual disability syndrome
- Dermo-odonto dysplasia
- Enamel-renal syndrome
- Goldblatt syndrome
- Horner's teeth
- Hyperplasia of gingiva
- Hypocalcification of teeth
- Hypomineralization of enamel of teeth
- Hypomineralization of enamel of tooth
- Hypomineralization of tooth
- Microdontia
- Nephrocalcinosis
- Odontogenesis imperfecta
- Osteogenesis imperfecta type I
- Osteogenesis imperfecta with blue sclerae AND dentinogenesis imperfecta
- Osteosclerosis
- Shell teeth
- Skeletal dysplasia with wormian bone, multiple fractures, dentinogenesis imperfecta syndrome
- Taurodontism
- Trichodysplasia with amelogenesis imperfecta syndrome
- Verloes Bourguignon syndrome
Clinical Classification
| Clinical Category | CCSR Category Code | Inpatient Default CCSR | Outpatient Default CCSR |
|---|---|---|---|
| Any dental condition including traumatic injury | DEN001 | N - Not default inpatient assignment for principal diagnosis or first-listed diagnosis. | N - Not default outpatient assignment for principal diagnosis or first-listed diagnosis. |
| Disorders of teeth and gingiva | DIG002 | Y - Yes, default inpatient assignment for principal diagnosis or first-listed diagnosis. | Y - Yes, default outpatient assignment for principal diagnosis or first-listed diagnosis. |
| Nontraumatic dental conditions | DEN002 | N - Not default inpatient assignment for principal diagnosis or first-listed diagnosis. | N - Not default outpatient assignment for principal diagnosis or first-listed diagnosis. |
Clinical Information
Dental Pulp Calcification
calcinosis of the dental pulp or root canal.Dentin Dysplasia
an apparently hereditary disorder of dentin formation, marked by a normal appearance of coronal dentin associated with pulpal obliteration, faulty root formation, and a tendency for peripheral lesions without obvious cause. (from dorland, 27th ed)Dentinogenesis Imperfecta
an autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. the dentin develops poorly with low mineral content while the pulp canal is obliterated.Nephrocalcinosis
a condition characterized by calcification of the renal tissue itself. it is usually seen in distal renal tubular acidosis with calcium deposition in the distal kidney tubules and the surrounding interstitium. nephrocalcinosis causes renal insufficiency.Osteopetrosis
excessive formation of dense trabecular bone leading to pathological fractures; osteitis; splenomegaly with infarct; anemia; and extramedullary hemopoiesis (hematopoiesis, extramedullary).Osteosclerosis
an abnormal hardening or increased density of bone tissue.Amelogenesis Imperfecta
a clinically and genetically heterogeneous group of hereditary conditions characterized by malformed dental enamel, usually involving dental enamel hypoplasia and/or tooth hypomineralization.Dentinogenesis Imperfecta
a congenital tooth development disorder caused by mutations in the dspp gene. the teeth are weak, discolored, and translucent.COL1A2 wt Allele|COL1A2|Collagen Type I Alpha 2 Chain wt Allele|Collagen, Type I, Alpha 2 Gene|OI4|Osteogenesis Imperfecta Type IV Gene
human col1a2 wild-type allele is located in the vicinity of 7q22.1 and is approximately 37 kb in length. this allele, which encodes collagen alpha-2 (i) chain protein, plays a role in the structural integrity of tendons, ligaments and bones. mutations in the gene are associated with atypical marfan syndrome, ehlers-danlos syndrome types and osteogenesis imperfecta types.Osteogenesis Imperfecta Type I
the mildest and most common type of osteogenesis imperfecta. it is characterized by bone fractures, muscle weakness, and loose joints. bone deformities are either absent or minimal.Osteogenesis Imperfecta Type II
a severe form of osteogenesis imperfecta. it is characterized by bone deformities, multiple fractures, underdeveloped lungs, and often death during or after birth due to respiratory abnormalities.Osteogenesis Imperfecta Type III
a type of osteogenesis imperfecta characterized by bone fractures, bone deformities, short stature, poor muscle development, barrel-shaped chest, and triangular face.Osteogenesis Imperfecta Type IV
a type of osteogenesis imperfecta that is characterized by fractures and hearing loss. it is more severe than type i and less severe than types ii and iii.Nephrocalcinosis
deposition of calcium in the renal parenchyma, resulting from high levels of calcium in the blood and/or urine.Osteosclerosis
abnormally high bone density.
Tabular List of Diseases and Injuries
The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.
Inclusion Terms
Inclusion TermsThese terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
- Amelogenesis imperfecta
- Dentinogenesis imperfecta
- Odontogenesis imperfecta
- Dentinal dysplasia
- Shell teeth
Index to Diseases and Injuries References
The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).
- - Amelogenesis imperfecta - K00.5
- - Brown enamel of teeth (hereditary) - K00.5
- - Defect, defective - Q89.9
- - dentin (hereditary) - K00.5
- - Dentin
- - opalescent - K00.5
- - Dentinogenesis imperfecta - K00.5
- - Disturbance (s) - See Also: Disease;
- - tooth
- - structure, hereditary NEC - K00.5
- - tooth
- - Odontogenesis imperfecta - K00.5
- - Opalescent dentin (hereditary) - K00.5
- - Shell teeth - K00.5
Convert K00.5 to ICD-9-CM
- ICD-9-CM Code: 520.5 - Heredit tooth struct NEC
Patient Education
Tooth Disorders
What are teeth?
Your teeth are made of a hard, bonelike material. There are four parts:
- Enamel, your tooth's hard surface
- Dentin, the hard yellow part under the enamel
- Cementum, the hard tissue that covers the root and keeps your teeth in place
- Pulp, the soft connective tissue in the center of your tooth. It contains nerves and blood vessels.
You need your teeth for many activities that you may take for granted. These include eating, speaking and even smiling.
What are tooth disorders?
There are many different problems that can affect your teeth, including:
- Tooth decay - damage to a tooth's surface, which can lead to cavities
- Abscess - a pocket of pus, caused by a tooth infection
- Impacted tooth - a tooth did not erupt (break through the gum) when it should have. It is usually wisdom teeth that are impacted, but it can sometimes happen to other teeth.
- Misaligned teeth (malocclusion)
- Tooth injuries such as broken or chipped teeth
What causes tooth disorders?
The causes of tooth disorders varies, depending on the problem. Sometimes the cause is not taking good care of your teeth. In other cases, you may have been born with the problem or the cause is an accident.
What are the symptoms of tooth disorders?
The symptoms can vary, depending on the problem. Some of the more common symptoms include:
- Abnormal color or shape of the tooth
- Tooth pain
- Worn-down teeth
How are tooth disorders diagnosed?
Your dentist will ask about your symptoms, look at your teeth, and probe them with dental instruments. In some cases, you may need dental x-rays.
What are the treatments for tooth disorders?
The treatment will depend on the problem. Some common treatments are:
- Fillings for cavities
- Root canals for cavities or infections that affect the pulp (inside of the tooth)
- Extractions (pulling teeth) for teeth that are impacted and causing problems or are too damaged to be fixed. You may also have a tooth or teeth pulled because of overcrowding in your mouth.
Can tooth disorders be prevented?
The main thing that you can do to prevent tooth disorders is to take good care of your teeth:
- Brush your teeth twice a day with a fluoride toothpaste
- Clean between your teeth every day with floss or another type of between-the-teeth cleaner
- Limit sugary snacks and drinks
- Don't smoke or chew tobacco
- See your dentist or oral health professional regularly
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Code History
- FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
- FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
- FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
- FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
- FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
- FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
- FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
- FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
- FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.
Footnotes
[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.