ICD-10 Diagnosis Code J84.81


Diagnosis Code J84.81

ICD-10: J84.81
Short Description: Lymphangioleiomyomatosis
Long Description: Lymphangioleiomyomatosis
This is the 2017 version of the ICD-10-CM diagnosis code J84.81

Code Classification
  • Diseases of the respiratory system
    • Other respiratory diseases principally affecting the interstitium (J80-J84)
      • Other interstitial pulmonary diseases (J84)

Information for Medical Professionals

Code Edits
The following edits are applicable to this code:
Diagnoses for females only Additional informationCallout TooltipDiagnoses for females only
Diagnoses for females only.

Diagnostic Related Groups
The diagnosis code J84.81 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.
  • 516.4 - Lymphangioleiomyomatosis

  • Lymphangioleiomyomatosis due to tuberous sclerosis syndrome
  • Pulmonary hypertension in lymphangioleiomyomatosis
  • Pulmonary hypertension in systemic disorder
  • Pulmonary lymphangioleiomyomatosis
  • Pulmonary lymphangioleiomyomatosis
  • Pulmonary lymphangioleiomyomatosis

Index of Diseases and Injuries
References found for the code J84.81 in the Index of Diseases and Injuries:

Information for Patients

Interstitial Lung Diseases

Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. The inflammation and scarring make it hard to get enough oxygen. The scarring is called pulmonary fibrosis.

Breathing in dust or other particles in the air is responsible for some types of interstitial lung diseases. Specific types include

  • Black lung disease among coal miners, from inhaling coal dust
  • Farmer's lung, from inhaling farm dust
  • Asbestosis, from inhaling asbestos fibers
  • Siderosis, from inhaling iron from mines or welding fumes
  • Silicosis, from inhaling silica dust

Other causes include autoimmune diseases or occupational exposures to molds, gases, or fumes. Some types of interstitial lung disease have no known cause.

Treatment depends on the type of exposure and the stage of the disease. It may involve medicines, oxygen therapy, or a lung transplant in severe cases.

  • Hypersensitivity pneumonitis
  • Interstitial lung disease
  • Interstitial lung disease - adults - discharge
  • Pulmonary function tests

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Lymphangioleiomyomatosis Lymphangioleiomyomatosis (LAM) is a condition that affects the lungs, the kidneys, and the lymphatic system. The lymphatic system consists of a network of vessels that transport lymph fluid and immune cells throughout the body.LAM is found almost exclusively in women. It usually occurs as a feature of an inherited syndrome called tuberous sclerosis complex. When LAM occurs alone it is called isolated or sporadic LAM.Signs and symptoms of LAM most often appear during a woman's thirties. Affected women have an overgrowth of abnormal smooth muscle-like cells (LAM cells) in the lungs, resulting in the formation of lung cysts and the destruction of normal lung tissue. They may also have an accumulation of fluid in the cavity around the lungs (chylothorax).The lung abnormalities resulting from LAM may cause difficulty breathing (dyspnea), chest pain, and coughing, which may bring up blood (hemoptysis). Many women with this disorder have recurrent episodes of collapsed lung (spontaneous pneumothorax). The lung problems may be progressive and, without lung transplantation, may eventually lead to limitations in activities of daily living, the need for oxygen therapy, and respiratory failure. Although LAM cells are not considered cancerous, they may spread between tissues (metastasize). As a result, the condition may recur even after lung transplantation.Women with LAM may develop cysts in the lymphatic vessels of the chest and abdomen. These cysts are called lymphangioleiomyomas. Affected women may also develop tumors called angiomyolipomas made up of LAM cells, fat cells, and blood vessels. Angiomyolipomas usually develop in the kidneys. Internal bleeding is a common complication of angiomyolipomas.
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