Systemic connective tissue disorders (M30-M36)
Browse all the diagnosis codes used for systemic connective tissue disorders (m30-m36). For easy navigation, the diagnosis codes are sorted in alphabetical order and grouped by sections. Each section is clearly marked with its description, and the corresponding three-digit code range. This format makes it simple to browse diagnosis codes in this chapter or section and find what you're looking for. We've also added green checkmark icons to label billable codes, and red warning icons for non-billable ones. This makes it easy to identify which codes can be billed.
Instructional Notations
Includes
This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
- autoimmune disease NOS
- collagen (vascular) disease NOS
- systemic autoimmune disease
- systemic collagen (vascular) disease
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- autoimmune disease, single organ or single cell-type -code to relevant condition category
Diseases of the musculoskeletal system and connective tissue (M00–M99)
Systemic connective tissue disorders (M30-M36)
M30 Polyarteritis nodosa and related conditions
- M30.0 Polyarteritis nodosa
- M30.1 Polyarteritis with lung involvement [Churg-Strauss]
- M30.2 Juvenile polyarteritis
- M30.3 Mucocutaneous lymph node syndrome [Kawasaki]
- M30.8 Other conditions related to polyarteritis nodosa
Polyarteritis nodosa and related conditions (M30)
M31 Other necrotizing vasculopathies
- M31.0 Hypersensitivity angiitis
M31.1 Thrombotic microangiopathy
- M31.10 Thrombotic microangiopathy, unspecified
- M31.11 Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]
- M31.19 Other thrombotic microangiopathy
- M31.2 Lethal midline granuloma
M31.3 Wegener's granulomatosis
- M31.30 Wegener's granulomatosis without renal involvement
- M31.31 Wegener's granulomatosis with renal involvement
- M31.4 Aortic arch syndrome [Takayasu]
- M31.5 Giant cell arteritis with polymyalgia rheumatica
- M31.6 Other giant cell arteritis
- M31.7 Microscopic polyangiitis
- M31.8 Other specified necrotizing vasculopathies
- M31.9 Necrotizing vasculopathy, unspecified
Other necrotizing vasculopathies (M31)
M32 Systemic lupus erythematosus (SLE)
- M32.0 Drug-induced systemic lupus erythematosus
M32.1 Systemic lupus erythematosus with organ or system involvement
- M32.10 Systemic lupus erythematosus, organ or system involvement unspecified
- M32.11 Endocarditis in systemic lupus erythematosus
- M32.12 Pericarditis in systemic lupus erythematosus
- M32.13 Lung involvement in systemic lupus erythematosus
- M32.14 Glomerular disease in systemic lupus erythematosus
- M32.15 Tubulo-interstitial nephropathy in systemic lupus erythematosus UPDATED CODE
- M32.19 Other organ or system involvement in systemic lupus erythematosus
- M32.8 Other forms of systemic lupus erythematosus
- M32.9 Systemic lupus erythematosus, unspecified
Systemic lupus erythematosus (SLE) (M32)
M33 Dermatopolymyositis
M33.0 Juvenile dermatomyositis
- M33.00 Juvenile dermatomyositis, organ involvement unspecified
- M33.01 Juvenile dermatomyositis with respiratory involvement
- M33.02 Juvenile dermatomyositis with myopathy
- M33.03 Juvenile dermatomyositis without myopathy
- M33.09 Juvenile dermatomyositis with other organ involvement
M33.1 Other dermatomyositis
- M33.10 Other dermatomyositis, organ involvement unspecified
- M33.11 Other dermatomyositis with respiratory involvement
- M33.12 Other dermatomyositis with myopathy
- M33.13 Other dermatomyositis without myopathy
- M33.19 Other dermatomyositis with other organ involvement
M33.2 Polymyositis
- M33.20 Polymyositis, organ involvement unspecified
- M33.21 Polymyositis with respiratory involvement
- M33.22 Polymyositis with myopathy
- M33.29 Polymyositis with other organ involvement
M33.9 Dermatopolymyositis, unspecified
- M33.90 Dermatopolymyositis, unspecified, organ involvement unspecified
- M33.91 Dermatopolymyositis, unspecified with respiratory involvement
- M33.92 Dermatopolymyositis, unspecified with myopathy
- M33.93 Dermatopolymyositis, unspecified without myopathy
- M33.99 Dermatopolymyositis, unspecified with other organ involvement
Dermatopolymyositis (M33)
M34 Systemic sclerosis [scleroderma]
- M34.0 Progressive systemic sclerosis
- M34.1 CR(E)ST syndrome
- M34.2 Systemic sclerosis induced by drug and chemical
M34.8 Other forms of systemic sclerosis
- M34.81 Systemic sclerosis with lung involvement
- M34.82 Systemic sclerosis with myopathy
- M34.83 Systemic sclerosis with polyneuropathy
- M34.89 Other systemic sclerosis
- M34.9 Systemic sclerosis, unspecified
Systemic sclerosis [scleroderma] (M34)
M35 Other systemic involvement of connective tissue
M35.0 Sjogren syndrome
- M35.00 Sjogren syndrome, unspecified
- M35.01 Sjogren syndrome with keratoconjunctivitis
- M35.02 Sjogren syndrome with lung involvement
- M35.03 Sjogren syndrome with myopathy
- M35.04 Sjogren syndrome with tubulo-interstitial nephropathy
- M35.05 Sjogren syndrome with inflammatory arthritis
- M35.06 Sjogren syndrome with peripheral nervous system involvement
- M35.07 Sjogren syndrome with central nervous system involvement
- M35.08 Sjogren syndrome with gastrointestinal involvement
- M35.09 Sjogren syndrome with other organ involvement
- M35.0A Sjogren syndrome with glomerular disease
- M35.0B Sjogren syndrome with vasculitis
- M35.0C Sjogren syndrome with dental involvement
- M35.1 Other overlap syndromes
- M35.2 Behcet's disease
- M35.3 Polymyalgia rheumatica
- M35.4 Diffuse (eosinophilic) fasciitis
- M35.5 Multifocal fibrosclerosis
- M35.6 Relapsing panniculitis [Weber-Christian]
- M35.7 Hypermobility syndrome
M35.8 Other specified systemic involvement of connective tissue
- M35.81 Multisystem inflammatory syndrome
- M35.89 Other specified systemic involvement of connective tissue
- M35.9 Systemic involvement of connective tissue, unspecified
Other systemic involvement of connective tissue (M35)
M36 Systemic disorders of connective tissue in diseases classified elsewhere
- M36.0 Dermato(poly)myositis in neoplastic disease
- M36.1 Arthropathy in neoplastic disease
- M36.2 Hemophilic arthropathy
- M36.3 Arthropathy in other blood disorders
- M36.4 Arthropathy in hypersensitivity reactions classified elsewhere
- M36.8 Systemic disorders of connective tissue in other diseases classified elsewhere
Systemic disorders of connective tissue in diseases classified elsewhere (M36)