Other interstitial pulmonary diseases (J84)
Clinical Information
Asbestosis - A form of pneumoconiosis caused by inhalation of asbestos fibers which elicit potent inflammatory responses in the parenchyma of the lung. The disease is characterized by interstitial fibrosis of the lung, varying from scattered sites to extensive scarring of the alveolar interstitium.
Aspergillus - A genus of mitosporic fungi containing about 100 species and eleven different teleomorphs in the family Trichocomaceae.
Cryptogenic Organizing Pneumonia - An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a "pneumonia-like" illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts.
Dyspnea - Difficult or labored breathing.
Hemosiderosis - Conditions in which there is a generalized increase in the iron stores of body tissues, particularly of liver and the MONONUCLEAR PHAGOCYTE SYSTEM, without demonstrable tissue damage. The name refers to the presence of stainable iron in the tissue in the form of hemosiderin.
Idiopathic Pulmonary Fibrosis - A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.
Invasive Pulmonary Aspergillosis - Lung infections with the invasive forms of ASPERGILLUS, usually after surgery, transplantation, prolonged NEUTROPENIA or treatment with high-doses of CORTICOSTEROIDS. Invasive pulmonary aspergillosis can progress to CHRONIC NECROTIZING PULMONARY ASPERGILLOSIS or hematogenous spread to other organs.
Lymphangioleiomyomatosis - A disease characterized by the progressive invasion of SMOOTH MUSCLE CELLS into the LYMPHATIC VESSELS, and the BLOOD VESSELS. The majority of the cases occur in the LUNGS of women of child-bearing age, eventually blocking the flow of air, blood, and lymph. The common symptom is shortness of breath (DYSPNEA).
Mononuclear Phagocyte System - Mononuclear cells with pronounced phagocytic ability that are distributed extensively in lymphoid and other organs. It includes MACROPHAGES and their precursors; PHAGOCYTES; KUPFFER CELLS; HISTIOCYTES; DENDRITIC CELLS; LANGERHANS CELLS; and MICROGLIA. The term mononuclear phagocyte system has replaced the former reticuloendothelial system, which also included less active phagocytic cells such as fibroblasts and endothelial cells. (From Illustrated Dictionary of Immunology, 2d ed.)
Pulmonary Alveolar Proteinosis - A PULMONARY ALVEOLI-filling disease, characterized by dense phospholipoproteinaceous deposits in the alveoli, cough, and DYSPNEA. This disease is often related to, congenital or acquired, impaired processing of PULMONARY SURFACTANTS by alveolar macrophages, a process dependent on GRANULOCYTE-MACROPHAGE COLONY-STIMULATING FACTOR.
Pulmonary Aspergillosis - Infections of the respiratory tract with fungi of the genus ASPERGILLUS.
Pulmonary Fibrosis - A process in which normal lung tissues are progressively replaced by FIBROBLASTS and COLLAGEN causing an irreversible loss of the ability to transfer oxygen into the bloodstream via PULMONARY ALVEOLI. Patients show progressive DYSPNEA finally resulting in death.
Instructional Notations
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Diseases of the respiratory system (J00–J99)
Other respiratory diseases principally affecting the interstitium (J80-J84)
J84 Other interstitial pulmonary diseases
J84.0 Alveolar and parieto-alveolar conditions
- J84.01 Alveolar proteinosis
- J84.02 Pulmonary alveolar microlithiasis
- J84.03 Idiopathic pulmonary hemosiderosis
- J84.09 Other alveolar and parieto-alveolar conditions
J84.1 Other interstitial pulmonary diseases with fibrosis
- J84.10 Pulmonary fibrosis, unspecified
J84.11 Idiopathic interstitial pneumonia
- J84.111 Idiopathic interstitial pneumonia, not otherwise specified
- J84.112 Idiopathic pulmonary fibrosis
- J84.113 Idiopathic non-specific interstitial pneumonitis
- J84.114 Acute interstitial pneumonitis
- J84.115 Respiratory bronchiolitis interstitial lung disease
- J84.116 Cryptogenic organizing pneumonia
- J84.117 Desquamative interstitial pneumonia
J84.17 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
- J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
- J84.178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
- J84.2 Lymphoid interstitial pneumonia
J84.8 Other specified interstitial pulmonary diseases
- J84.81 Lymphangioleiomyomatosis
- J84.82 Adult pulmonary Langerhans cell histiocytosis
- J84.83 Surfactant mutations of the lung
J84.84 Other interstitial lung diseases of childhood
- J84.841 Neuroendocrine cell hyperplasia of infancy
- J84.842 Pulmonary interstitial glycogenosis
- J84.843 Alveolar capillary dysplasia with vein misalignment
- J84.848 Other interstitial lung diseases of childhood
- J84.89 Other specified interstitial pulmonary diseases
- J84.9 Interstitial pulmonary disease, unspecified
Other interstitial pulmonary diseases (J84)