2024 ICD-10-CM Diagnosis Code I42.2

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Apical hypertrophic cardiomyopathy
• Apical hypertrophic cardiomyopathy with aneurysm
• Cardiomyopathy in Friedreich's ataxia
• Familial cardiomyopathy
• Fatal congenital hypertrophic cardiomyopathy due to glycogen storage disease
• Hypertrophic cardiomyopathy
• Hypertrophic cardiomyopathy and renal tubular disease due to mitochondrial DNA mutation
• Hypertrophic cardiomyopathy due to disorder
• Hypertrophic cardiomyopathy due to Friedreich ataxia
• Hypertrophic cardiomyopathy due to glycogen storage disease
• Hypertrophic cardiomyopathy due to hyperthyroidism
• Hypertrophic cardiomyopathy due to lysosomal disease
• Hypertrophic cardiomyopathy due to neuromuscular disorder
• Hypertrophic cardiomyopathy with genetic marker
• Hypertrophic cardiomyopathy with hypotonia and lactic acidosis syndrome
• Hypertrophic cardiomyopathy without obstruction
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy
• Hypertrophic mitochondrial cardiomyopathy associated with cataracts and lactic acidosis
• Infantile hypertrophic cardiomyopathy due to MRPL44 deficiency
• Left ventricular aneurysm
• Mitochondrial hypertrophic cardiomyopathy with lactic acidosis due to MTO1 deficiency
• Primary familial hypertrophic cardiomyopathy
• Primary hypertrophic cardiomyopathy
• Primary idiopathic hypertrophic cardiomyopathy
• Progressive sensorineural hearing loss and hypertrophic cardiomyopathy syndrome

Clinical Information

• Apical Hypertrophic Cardiomyopathy

  a hypertrophic cardiomyopathy characterized by apical hypertrophy, typically left ventricular hypertrophy (described as "ace of spades" sign), and deep t-wave inversions in ekg. clinical symptoms include minor symptoms such as chest pain; dyspnea; and syncope to more complex symptoms such as atrial fibrillation; ventricular fibrillation; myocardial infarction and congestive heart failure. a transient left ventricular apical hypertrophy is sometimes associated with takotsubo cardiomyopathy.

• Familial Hypertrophic Cardiomyopathy Type 1|Asymmetric Septal Hypertrophy|CMH1|Hereditary Ventricular Hypertrophy|IHSS|Idiopathic Hypertrophic Subaortic Stenosis

  an autosomal dominant subtype of familial hypertrophic cardiomyopathy caused by mutation(s) in the cav3 gene, myh7 gene, or mylk2 gene encoding caveolin-3, myosin heavy chain 7, and myosin light chain kinase 2, skeletal/cardiac muscle respectively.

• Familial Hypertrophic Cardiomyopathy Type 11|CMH11

  an autosomal dominant subtype of familial hypertrophic cardiomyopathy caused by mutation(s) in the actc1 gene, encoding actin, alpha cardiac muscle 1.

• Familial Hypertrophic Cardiomyopathy Type 14|CMH14

  an autosomal dominant subtype of familial hypertrophic cardiomyopathy caused by mutation(s) in the myh6 gene, encoding myosin-6.

• Familial Hypertrophic Cardiomyopathy Type 17|CMH17

  an autosomal dominant subtype of familial hypertrophic cardiomyopathy caused by mutation(s) in the jph2 gene, encoding junctophilin-2.

• Familial Hypertrophic Cardiomyopathy Type 2|CMH2

  an autosomal dominant subtype of familial hypertrophic cardiomyopathy caused by mutation(s) in the tnnt2 gene, encoding troponin t, cardiac muscle.

• Familial Hypertrophic Cardiomyopathy Type 26|CMH26

  an autosomal dominant subtype of familial hypertrophic cardiomyopathy caused by mutation(s) in the flnc gene, encoding filamin-c.

• Familial Hypertrophic Cardiomyopathy Type 27|CMH27

  an autosomal recessive subtype of familial hypertrophic cardiomyopathy caused by mutation(s) in the alpk3 gene, encoding alpha-protein kinase 3.

• Familial Hypertrophic Cardiomyopathy Type 3|CMH3

  an autosomal dominant subtype of familial hypertrophic cardiomyopathy caused by mutation(s) in the tpm1 gene, encoding tropomyosin alpha-1 chain.

• Familial Hypertrophic Cardiomyopathy Type 4|CMH4

  an autosomal dominant condition caused by mutation(s) in the mybpc3 gene, encoding mybpc3 protein. it is characterized by severe neonatal hypertrophic cardiomyopathy.

• Familial Hypertrophic Cardiomyopathy Type 6|CMH6

  an autosomal dominant subtype of familial hypertrophic cardiomyopathy caused by mutation(s) in the prkag2 gene, encoding 5'-amp-activated protein kinase subunit gamma-2.

• Familial Hypertrophic Cardiomyopathy Type 7|CMH7

  an autosomal dominant subtype of familial hypertrophic cardiomyopathy caused by mutation(s) in the tnni3 gene, encoding troponin i, cardiac muscle.

• Familial Hypertrophic Cardiomyopathy|Hypertrophic Familial Cardiomyopathy

  hypertrophic cardiomyopathy caused by mutations in the genes encoding components of the sarcomere, in the absence of predisposing conditions.

• Hypertrophic Cardiomyopathy

  a condition in which the myocardium is hypertrophied without an obvious cause. the hypertrophy is generally asymmetric and may be associated with obstruction of the ventricular outflow tract.

• Left Ventricular Aneurysm

  a bulge or ballooning in the wall of the left ventricle of the heart.

I42.2 is grouped with Diagnostic Related Groups - MS-DRG Mapping

Diagnostic Related Groups (DRGs) are a classification system used to group together diagnosis codes for the purpose of reimbursement and healthcare management. DRGs are used to standardize the way hospitals and other providers are paid for inpatient services. In this system patients are grouped together based on their principal diagnosis in areas referred to as Major Diagnostic Categories (MDC). Once a patient is assigned a particular diagnostic category, providers receive a predetermined payment rate for the services rendered. This reimbursement rate is often fixed and is meant to cover the cost of care for that patient. Reimbursement is also affected by the relative weight of a diagnostic related group based on the severity of a patient's illness and the associated cost of care during hospitalization.

Diagnostic related groups encourage healthcare providers to focus on quality and efficiency in patient care while managing costs effectively. The diagnosis code is present in the following groups for version MS-DRG V41.0 applicable from 10/01/2023 through 09/30/2024.

MS-DRG	MS-DRG Title	MCD	Relative Weight
314	OTHER CIRCULATORY SYSTEM DIAGNOSES WITH MCC	05	2.0935
315	OTHER CIRCULATORY SYSTEM DIAGNOSES WITH CC	05	0.9673
316	OTHER CIRCULATORY SYSTEM DIAGNOSES WITHOUT CC/MCC	05	0.6927

The relative weight of a diagnostic related group determines the reimbursement rate based on the severity of a patient's illness and the associated cost of care during hospitalization.

Convert I42.2 to ICD-9-CM

• ICD-9-CM Code: 425.18 - Oth hyprtrophic cardiomy

Patient Education

Cardiomyopathy

Cardiomyopathy is the name for diseases of the heart muscle. These diseases enlarge your heart muscle or make it thicker and more rigid than normal. In rare cases, scar tissue replaces the muscle tissue.

Some people live long, healthy lives with cardiomyopathy. Some people don't even realize they have it. In others, however, it can make the heart less able to pump blood through the body. This can cause serious complications, including:

• Heart failure
• Abnormal heart rhythms
• Heart valve problems
• Sudden cardiac arrest (SCA)

Heart attacks, high blood pressure, infections, and other diseases can all cause cardiomyopathy. Some types of cardiomyopathy run in families. In many people, however, the cause is unknown. Treatment might involve medicines, surgery, other medical procedures, and lifestyle changes.

NIH: National Heart, Lung, and Blood Institute

[Learn More in MedlinePlus]

Code History

• FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.