Version 2024
Replaced Code

2024 ICD-10-CM Diagnosis Code G11.8

Other hereditary ataxias

ICD-10-CM Code:
G11.8
ICD-10 Code for:
Other hereditary ataxias
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the nervous system
    (G00–G99)
    • Systemic atrophies primarily affecting the central nervous system
      (G10-G14)
      • Hereditary ataxia
        (G11)

G11.8 is a billable diagnosis code used to specify a medical diagnosis of other hereditary ataxias. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • 4H leukodystrophy
  • Abnormal saccadic eye movement
  • Acute hepatic failure
  • Acute infantile liver failure, cerebellar ataxia, peripheral sensory motor neuropathy syndrome
  • Arts syndrome
  • Ataxia pancytopenia syndrome
  • Ataxia, photosensitivity, short stature syndrome
  • Autosomal dominant cerebellar ataxia type 2
  • Autosomal recessive cerebellar ataxia Beauce type
  • Autosomal recessive cerebellar ataxia due to CWF19L1 deficiency
  • Autosomal recessive cerebellar ataxia with saccadic intrusion syndrome
  • Autosomal recessive cerebellar ataxia, epilepsy, intellectual disability syndrome due to WWOX deficiency
  • Autosomal recessive cerebellar ataxia, pyramidal signs, nystagmus, oculomotor apraxia syndrome
  • Autosomal recessive cerebelloparenchymal disorder type 3
  • Autosomal recessive spinocerebellar ataxia, blindness, deafness syndrome
  • Bailey-Cushing syndrome
  • CAMOS syndrome
  • Cerebellar ataxia Cayman type
  • Cerebellar ataxia, intellectual disability, oculomotor apraxia, cerebellar cysts syndrome
  • CLCN2-related leukoencephalopathy
  • Congenital atrophy of optic nerve
  • Congenital cerebellar ataxia due to RNU12 mutation
  • Congenital non-progressive ataxia
  • Episodic ataxia
  • Episodic ataxia
  • Episodic ataxia type 1
  • Episodic ataxia type 2
  • Episodic ataxia type 3
  • Episodic ataxia type 4
  • Episodic ataxia type 5
  • Episodic ataxia type 6
  • Episodic ataxia with slurred speech
  • Finding of intelligibility of articulation
  • Hereditary cerebellar atrophy
  • Hereditary cerebellar atrophy
  • Intellectual disability, hyperkinetic movement, truncal ataxia syndrome
  • Jervis' syndrome
  • Late tooth eruption
  • Leukoencephalopathy, ataxia, hypodontia, hypomyelination syndrome
  • Mitochondrial myopathy, cerebellar ataxia, pigmentary retinopathy syndrome
  • Neuhauser Eichner Opitz syndrome
  • Progressive autosomal recessive cerebellar ataxia, sensorineural hearing loss syndrome
  • Progressive sensory ataxia of Charolais
  • Recessive mitochondrial ataxia syndrome
  • Richards-Rundle syndrome
  • Sanger-Brown cerebellar ataxia
  • Severe intellectual disability, agenesis of corpus callosum, facial dysmorphism, cerebellar ataxia syndrome
  • Slurred speech
  • Spinocerebellar ataxia dysmorphism syndrome
  • Spinocerebellar ataxia type 1
  • Spinocerebellar ataxia type 10
  • Spinocerebellar ataxia type 11
  • Spinocerebellar ataxia type 12
  • Spinocerebellar ataxia type 13
  • Spinocerebellar ataxia type 14
  • Spinocerebellar ataxia type 15/16
  • Spinocerebellar ataxia type 17
  • Spinocerebellar ataxia type 18
  • Spinocerebellar ataxia type 19
  • Spinocerebellar ataxia type 2
  • Spinocerebellar ataxia type 20
  • Spinocerebellar ataxia type 21
  • Spinocerebellar ataxia type 23
  • Spinocerebellar ataxia type 25
  • Spinocerebellar ataxia type 26
  • Spinocerebellar ataxia type 27
  • Spinocerebellar ataxia type 28
  • Spinocerebellar ataxia type 29
  • Spinocerebellar ataxia type 30
  • Spinocerebellar ataxia type 31
  • Spinocerebellar ataxia type 32
  • Spinocerebellar ataxia type 34
  • Spinocerebellar ataxia type 35
  • Spinocerebellar ataxia type 36
  • Spinocerebellar ataxia type 37
  • Spinocerebellar ataxia type 38
  • Spinocerebellar ataxia type 4
  • Spinocerebellar ataxia type 40
  • Spinocerebellar ataxia type 41
  • Spinocerebellar ataxia type 42
  • Spinocerebellar ataxia type 43
  • Spinocerebellar ataxia type 5
  • Spinocerebellar ataxia type 6
  • Spinocerebellar ataxia type 7
  • Spinocerebellar ataxia type 8
  • Spinocerebellar ataxia with axonal neuropathy type 1
  • Third cranial nerve finding
  • Truncal ataxia
  • Truncal ataxia
  • Unintelligible articulation

Clinical Classification

Clinical Information

  • Ataxin-7|ATXN7|Ataxin 7|Spinocerebellar Ataxia Type 7 Protein

    ataxin-7 (892 aa, ~95 kda) is encoded by the human atxn7 gene. this protein is involved in the regulation of histone acetylation and chromatin remodeling.
  • Spinocerebellar Ataxia Type 7

    an autosomal dominant inherited neurodegenerative disorder caused by mutations in the atxn7 gene. it is characterized by progressive cerebellar ataxia, including dysarthria and dysphagia, cone-rod and retinal dystrophy, and progressive central visual loss resulting in blindness.

Replaced Code

This code was replaced in the 2024 ICD-10-CM code set with the code(s) listed below. The National Center for Health Statistics (NCHS) has published an update to the ICD-10-CM diagnosis codes which became effective October 1, 2023. This code was replaced for the FY 2024 (October 1, 2023 - September 30, 2024).


  • G11.5 - Hypomyelination - hypogonadotropic hypogonadism - hypodontia
  • G11.6 - Leukodystrophy with vanishing white matter disease

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert G11.8 to ICD-9-CM

  • ICD-9-CM Code: 334.8 - Spinocerebellar dis NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Cerebellar Disorders

When you play the piano or hit a tennis ball you are activating the cerebellum. The cerebellum is the area of the brain that controls coordination and balance. Problems with the cerebellum include:

  • Cancer
  • Genetic disorders
  • Ataxias - failure of muscle control in the arms and legs that result in movement disorders
  • Degeneration - disorders caused by brain cells decreasing in size or wasting away

Treatment of cerebellar disorders depends on the cause. In some cases, there is no cure but treatment may help with symptoms.

NIH: National Institute of Neurological Disorders and Stroke


[Learn More in MedlinePlus]

Movement Disorders

Movement disorders are neurologic conditions that cause problems with movement, such as:

  • Increased movement that can be voluntary (intentional) or involuntary (unintended)
  • Decreased or slow voluntary movement

There are many different movement disorders. Some of the more common types include:

  • Ataxia, the loss of muscle coordination
  • Dystonia, in which involuntary contractions of your muscles cause twisting and repetitive movements. The movements can be painful.
  • Huntington's disease, an inherited disease that causes nerve cells in certain parts of the brain to waste away. This includes the nerve cells that help to control voluntary movement.
  • Parkinson's disease, which is disorder that slowly gets worse over time. It causes tremors, slowness of movement, and trouble walking.
  • Tourette syndrome, a condition which causes people to make sudden twitches, movements, or sounds (tics)
  • Tremor and essential tremor, which cause involuntary trembling or shaking movements. The movements may be in one or more parts of your body.

Causes of movement disorders include:

  • Genetics
  • Infections
  • Medicines
  • Damage to the brain, spinal cord, or peripheral nerves
  • Metabolic disorders
  • Stroke and vascular diseases
  • Toxins

Treatment varies by disorder. Medicines can cure some disorders. Others get better when an underlying disease is treated. Often, however, there is no cure. In that case, the goal of treatment is to improve symptoms and relieve pain.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.