2024 ICD-10-CM Diagnosis Code E78.89

Other lipoprotein metabolism disorders

ICD-10-CM Code:
E78.89
ICD-10 Code for:
Other lipoprotein metabolism disorders
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Endocrine, nutritional and metabolic diseases
    (E00–E89)
    • Metabolic disorders
      (E70-E88)
      • Disorders of lipoprotein metabolism and other lipidemias
        (E78)

E78.89 is a billable diagnosis code used to specify a medical diagnosis of other lipoprotein metabolism disorders. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Combined heterozygous low density lipoprotein receptor co-occurrent with low density lipoprotein receptor adaptor protein 1 mutations
  • Combined pancreatic lipase and colipase deficiency
  • Deficiency of glycerophosphocholine phosphodiesterase
  • Dyslipidemia
  • Dyslipidemia
  • Dyslipidemia due to type 2 diabetes mellitus
  • Dyslipidemia with high density lipoprotein below reference range and triglyceride above reference range due to type 2 diabetes mellitus
  • Familial disease with storage of sterols
  • Farber's lipogranulomatosis
  • Fat overload syndrome
  • GM3 synthase deficiency
  • Hepatic lipase deficiency
  • Heterozygous sitosterolemia
  • High density lipoprotein below reference range
  • Homozygous sitosterolemia
  • Hypolipidemia
  • Intestinal lipofuscinosis
  • Lipid proteinosis
  • Lipofuscinosis
  • Lipogranulomatosis subcutanea of Rothmann and Makai
  • Lipoprotein above reference range
  • Lipoprotein below reference range
  • Low density lipoprotein cholesterol above reference range
  • Low density lipoprotein receptor adaptor protein 1 mutation
  • Low density lipoprotein receptor adaptor protein 1 mutation
  • Low density lipoprotein receptor mutation
  • Low density lipoprotein receptor mutation
  • Lysosomal acid lipase deficiency
  • Male emopamil-binding protein disorder with neurological defect
  • Proteinosis
  • Sitosterolemia
  • Triglyceride level - finding

Clinical Classification

Clinical Information

  • Sitosterolemia

    an extremely rare autosomal recessive inherited disorder caused by mutations in the abcg5 or abcg8 genes. it is characterized by a defective sterolin transporter that impairs the elimination of plant sterols and, to a lesser degree, cholesterol from the body. these fatty substances build up in the tissues including arteries and skin, resulting in atherosclerosis and xanthomas.
  • CDISC Dyslipidemia Therapeutic Area User Guide Version 1.0|Dyslipidemia Therapeutic Area User Guide v1.0

    the 1.0 version of the cdisc dyslipidemia therapeutic area user guide.
  • Dyslipidemia

    a lipoprotein metabolism disorder characterized by decreased levels of high-density lipoproteins, or elevated levels of plasma cholesterol, low-density lipoproteins and/or triglycerides.

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert E78.89 to ICD-9-CM

  • ICD-9-CM Code: 272.8 - Lipoid metabol dis NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Lipid Metabolism Disorders

Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder, something goes wrong with this process.

Lipid metabolism disorders, such as Gaucher disease and Tay-Sachs disease, involve lipids. Lipids are fats or fat-like substances. They include oils, fatty acids, waxes, and cholesterol. If you have one of these disorders, you may not have enough enzymes to break down lipids. Or the enzymes may not work properly and your body can't convert the fats into energy. They cause a harmful amount of lipids to build up in your body. Over time, that can damage your cells and tissues, especially in the brain, peripheral nervous system, liver, spleen, and bone marrow. Many of these disorders can be very serious, or sometimes even fatal.

These disorders are inherited. Newborn babies get screened for some of them, using blood tests. If there is a family history of one of these disorders, parents can get genetic testing to see whether they carry the gene. Other genetic tests can tell whether the fetus has the disorder or carries the gene for the disorder.

Enzyme replacement therapies can help with a few of these disorders. For others, there is no treatment. Medicines, blood transfusions, and other procedures may help with complications.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.