ICD-10 Diagnosis Code E74.31

Sucrase-isomaltase deficiency

Diagnosis Code E74.31

ICD-10: E74.31
Short Description: Sucrase-isomaltase deficiency
Long Description: Sucrase-isomaltase deficiency
This is the 2017 version of the ICD-10-CM diagnosis code E74.31

Code Classification
  • Endocrine, nutritional and metabolic diseases
    • Metabolic disorders (E70-E88)
      • Other disorders of carbohydrate metabolism (E74)

Information for Medical Professionals

Diagnostic Related Groups
The diagnosis code E74.31 is grouped in the following Diagnostic Related Group(s) (MS-DRG v33.0)


Convert to ICD-9 Additional informationCallout TooltipGeneral Equivalence Map
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • Deficiency of isomaltase
  • Disaccharidase deficiency
  • Disaccharidase deficiency
  • Intestinal disaccharidase deficiency
  • Intestinal disaccharidase deficiency
  • Sucrase-isomaltase deficiency
  • Sucrose intolerance

Information for Patients

Carbohydrate Metabolism Disorders

Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder, something goes wrong with this process.

Carbohydrate metabolism disorders are a group of metabolic disorders. Normally your enzymes break carbohydrates down into glucose (a type of sugar). If you have one of these disorders, you may not have enough enzymes to break down the carbohydrates. Or the enzymes may not work properly. This causes a harmful amount of sugar to build up in your body. That can lead to health problems, some of which can be serious. Some of the disorders are fatal.

These disorders are inherited. Newborn babies get screened for many of them, using blood tests. If there is a family history of one of these disorders, parents can get genetic testing to see whether they carry the gene. Other genetic tests can tell whether the fetus has the disorder or carries the gene for the disorder.

Treatments may include special diets, supplements, and medicines. Some babies may also need additional treatments, if there are complications. For some disorders, there is no cure, but treatments may help with symptoms.

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Malabsorption Syndromes

Your small intestine does most of the digesting of the foods you eat. If you have a malabsorption syndrome, your small intestine cannot absorb nutrients from foods.

Causes of malabsorption syndromes include

  • Celiac disease
  • Lactose intolerance
  • Short bowel syndrome. This happens after surgery to remove half or more of the small intestine. You might need the surgery if you have a problem with the small intestine from a disease, injury, or birth defect.
  • Whipple disease, a rare bacterial infection
  • Genetic diseases
  • Certain medicines

Symptoms of different malabsorption syndromes can vary. They often include chronic diarrhea, abnormal stools, weight loss, and gas. Your doctor may use lab, imaging, or other tests to make a diagnosis.

Treatment of malabsorption syndromes depends on the cause.

  • Blind loop syndrome
  • D-xylose absorption
  • Fecal fat
  • Lower GI Series - NIH (National Institute of Diabetes and Digestive and Kidney Diseases)
  • Malabsorption
  • Short bowel syndrome
  • Small bowel bacterial overgrowth
  • Stools - floating
  • Whipple's Disease - NIH (National Institute of Diabetes and Digestive and Kidney Diseases)
  • Whipple's disease

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Congenital sucrase-isomaltase deficiency Congenital sucrase-isomaltase deficiency is a disorder that affects a person's ability to digest certain sugars. People with this condition cannot break down the sugars sucrose and maltose. Sucrose (a sugar found in fruits, and also known as table sugar) and maltose (the sugar found in grains) are called disaccharides because they are made of two simple sugars. Disaccharides are broken down into simple sugars during digestion. Sucrose is broken down into glucose and another simple sugar called fructose, and maltose is broken down into two glucose molecules. People with congenital sucrase-isomaltase deficiency cannot break down the sugars sucrose and maltose, and other compounds made from these sugar molecules (carbohydrates).Congenital sucrase-isomaltase deficiency usually becomes apparent after an infant is weaned and starts to consume fruits, juices, and grains. After ingestion of sucrose or maltose, an affected child will typically experience stomach cramps, bloating, excess gas production, and diarrhea. These digestive problems can lead to failure to gain weight and grow at the expected rate (failure to thrive) and malnutrition. Most affected children are better able to tolerate sucrose and maltose as they get older.
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