2024 ICD-10-CM Diagnosis Code D58.0

Hereditary spherocytosis

ICD-10-CM Code:
D58.0
ICD-10 Code for:
Hereditary spherocytosis
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
    (D50–D89)
    • Hemolytic anemias
      (D55-D59)
      • Other hereditary hemolytic anemias
        (D58)

D58.0 is a billable diagnosis code used to specify a medical diagnosis of hereditary spherocytosis. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Anemia due to membrane defect
  • Anemia due to membrane defect
  • Anemia due to membrane defect
  • Anemia due to membrane defect
  • Anemia due to membrane defect
  • Anemia due to membrane defect
  • Anemia due to membrane defect
  • Anemia due to membrane defect
  • Anemia due to membrane defect
  • Hereditary spherocytosis
  • Hereditary spherocytosis
  • Hereditary spherocytosis
  • Hereditary spherocytosis
  • Hereditary spherocytosis
  • Hereditary spherocytosis
  • Hereditary spherocytosis
  • Hereditary spherocytosis
  • Hereditary spherocytosis
  • Hereditary spherocytosis due to beta spectrin defect
  • Hereditary spherocytosis due to combined deficiency of spectrin AND ankyrin
  • Hereditary spherocytosis due to deficiency of protein 4.2
  • Hereditary spherocytosis due to spectrin deficiency
  • Mild hereditary spherocytosis due to combined deficiency of spectrin AND ankyrin
  • Mild hereditary spherocytosis due to spectrin deficiency
  • Severe hereditary spherocytosis due to combined deficiency of spectrin AND ankyrin
  • Severe hereditary spherocytosis due to spectrin deficiency
  • Spherocytosis

Clinical Classification

Clinical Information

  • Hereditary Spherocytosis

    an autosomal dominant inherited disorder characterized by the presence of smaller than normal, sphere-shaped erythrocytes. it results in hemolytic anemia and splenomegaly.
  • Spherocytosis

    a hereditary or acquired blood disorder characterized by the presence of smaller than normal, sphere-shaped erythrocytes. it results in hemolytic anemia and splenomegaly.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Acholuric (familial) jaundice
  • Congenital (spherocytic) hemolytic icterus
  • Minkowski-Chauffard syndrome

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert D58.0 to ICD-9-CM

  • ICD-9-CM Code: 282.0 - Hereditary spherocytosis

Patient Education


Anemia

If you have anemia, your blood does not carry enough oxygen to the rest of your body. The most common cause of anemia is not having enough iron. Your body needs iron to make hemoglobin. Hemoglobin is an iron-rich protein that gives the red color to blood. It carries oxygen from the lungs to the rest of the body.

Anemia has three main causes: blood loss, lack of red blood cell production, and high rates of red blood cell destruction.

Conditions that may lead to anemia include:

  • Heavy periods
  • Pregnancy
  • Ulcers
  • Colon polyps or colon cancer
  • Inherited disorders
  • A diet that does not have enough iron, folic acid or vitamin B12
  • Blood disorders such as sickle cell anemia and thalassemia, or cancer
  • Aplastic anemia, a condition that can be inherited or acquired
  • G6PD deficiency, a metabolic disorder

Anemia can make you feel tired, cold, dizzy, and irritable. You may be short of breath or have a headache.

Your doctor will diagnose anemia with a physical exam and blood tests. Treatment depends on the kind of anemia you have.

NIH: National Heart, Lung, and Blood Institute


[Learn More in MedlinePlus]

Hereditary spherocytosis

Hereditary spherocytosis is a condition that affects red blood cells. People with this condition typically experience a shortage of red blood cells (anemia), yellowing of the eyes and skin (jaundice), and an enlarged spleen (splenomegaly). Most newborns with hereditary spherocytosis have severe anemia, although it improves after the first year of life. Splenomegaly can occur anytime from early childhood to adulthood. About half of affected individuals develop hard deposits in the gallbladder called gallstones, which typically occur from late childhood to mid-adulthood.

There are four forms of hereditary spherocytosis, which are distinguished by the severity of signs and symptoms. They are known as the mild form, the moderate form, the moderate/severe form, and the severe form. It is estimated that 20 to 30 percent of people with hereditary spherocytosis have the mild form, 60 to 70 percent have the moderate form, 10 percent have the moderate/severe form, and 3 to 5 percent have the severe form.

People with the mild form may have very mild anemia or sometimes have no symptoms. People with the moderate form typically have anemia, jaundice, and splenomegaly. Many also develop gallstones. The signs and symptoms of moderate hereditary spherocytosis usually appear in childhood. Individuals with the moderate/severe form have all the features of the moderate form but also have severe anemia. Those with the severe form have life-threatening anemia that requires frequent blood transfusions to replenish their red blood cell supply. They also have severe splenomegaly, jaundice, and a high risk for developing gallstones. Some individuals with the severe form have short stature, delayed sexual development, and skeletal abnormalities.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.