2024 ICD-10-CM Diagnosis Code C47.9

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Epithelioid malignant nerve sheath tumor
• Ganglioneuroblastoma
• Glandular malignant peripheral nerve sheath tumor
• Hirschsprung disease, ganglioneuroblastoma syndrome
• Malignant infiltration of peripheral nerve plexus
• Malignant neoplasm of peripheral nerves and autonomic nervous system
• Malignant peripheral nerve sheath tumor
• Malignant peripheral nerve sheath tumor with perineurial differentiation
• Malignant Triton tumor
• Malignant tumor of nerve sheath origin
• Malignant tumor of peripheral nerve
• Malignant tumor of spinal nerve and sheath
• Medulloepithelioma
• Melanotic malignant nerve sheath tumor
• Neoplasm of autonomic nerve
• Primary epithelioid malignant nerve sheath tumor
• Primary glandular malignant peripheral nerve sheath tumor
• Primary malignant neoplasm of peripheral nerve
• Primary malignant neoplasm of peripheral nerves and peripheral autonomic nervous system
• Primary malignant nerve sheath neoplasm of autonomic nerve
• Primary malignant nerve sheath neoplasm of peripheral nervous system structure
• Primary malignant neuroepitheliomatous neoplasm of autonomic nervous system
• Primary malignant neuroepitheliomatous neoplasm of peripheral nerve
• Primary medulloepithelioma
• Primary melanotic malignant nerve sheath tumor
• Primary primitive neuroectodermal tumor
• Tumor of spinal nerve and sheath

Clinical Information

• Ganglioneuroblastoma

  a moderately malignant neoplasm composed of primitive neuroectodermal cells dispersed in myxomatous or fibrous stroma intermixed with mature ganglion cells. it may undergo transformation into a neuroblastoma. it arises from the sympathetic trunk or less frequently from the adrenal medulla, cerebral cortex, and other locations. cervical ganglioneuroblastomas may be associated with horner syndrome and the tumor may occasionally secrete vasoactive intestinal peptide, resulting in chronic diarrhea.

• Horner Syndrome

  a syndrome associated with defective sympathetic innervation to one side of the face, including the eye. clinical features include miosis; mild blepharoptosis; and hemifacial anhidrosis (decreased sweating)(see hypohidrosis). lesions of the brain stem; cervical spinal cord; first thoracic nerve root; apex of the lung; carotid artery; cavernous sinus; and apex of the orbit may cause this condition. (from miller et al., clinical neuro-ophthalmology, 4th ed, pp500-11)

C47.9 is grouped with Diagnostic Related Groups - MS-DRG Mapping

Diagnostic Related Groups (DRGs) are a classification system used to group together diagnosis codes for the purpose of reimbursement and healthcare management. DRGs are used to standardize the way hospitals and other providers are paid for inpatient services. In this system patients are grouped together based on their principal diagnosis in areas referred to as Major Diagnostic Categories (MDC). Once a patient is assigned a particular diagnostic category, providers receive a predetermined payment rate for the services rendered. This reimbursement rate is often fixed and is meant to cover the cost of care for that patient. Reimbursement is also affected by the relative weight of a diagnostic related group based on the severity of a patient's illness and the associated cost of care during hospitalization.

Diagnostic related groups encourage healthcare providers to focus on quality and efficiency in patient care while managing costs effectively. The diagnosis code is present in the following groups for version MS-DRG V41.0 applicable from 10/01/2023 through 09/30/2024.

MS-DRG	MS-DRG Title	MCD	Relative Weight
542	PATHOLOGICAL FRACTURES AND MUSCULOSKELETAL AND CONNECTIVE TISSUE MALIGNANCY WITH MCC	08	1.8237
543	PATHOLOGICAL FRACTURES AND MUSCULOSKELETAL AND CONNECTIVE TISSUE MALIGNANCY WITH CC	08	1.0907
544	PATHOLOGICAL FRACTURES AND MUSCULOSKELETAL AND CONNECTIVE TISSUE MALIGNANCY WITHOUT CC/MCC	08	0.7675

The relative weight of a diagnostic related group determines the reimbursement rate based on the severity of a patient's illness and the associated cost of care during hospitalization.

Convert C47.9 to ICD-9-CM

• ICD-9-CM Code: 171.9 - Mal neo soft tissue NOS
  Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Table of Neoplasms

This code is referenced in the table of neoplasms by anatomical site. For each site there are six possible code numbers according to whether the neoplasm in question is malignant, benign, in situ, of uncertain behavior, or of unspecified nature. The description of the neoplasm will often indicate which of the six columns is appropriate.

Where such descriptors are not present, the remainder of the Index should be consulted where guidance is given to the appropriate column for each morphological (histological) variety listed. However, the guidance in the Index can be overridden if one of the descriptors mentioned above is present.

Filter table of neoplasms:

Neoplasm, neoplastic	Malignant Primary	Malignant Secondary	CaInSitu	Benign	Uncertain Behavior	Unspecified Behavior
»Neoplasm, neoplastic   »ganglia [See Also: Neoplasm, nerve, peripheral]	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »nerve (ganglion)	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »nerve (ganglion)     »autonomic NEC [See Also: Neoplasm, nerve, peripheral]	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »nerve (ganglion)     »ganglion NEC [See Also: Neoplasm, nerve, peripheral]	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »nerve (ganglion)     »parasympathetic NEC	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »nerve (ganglion)     »peripheral NEC	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »nerve (ganglion)     »peripheral NEC       »extremity	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »nerve (ganglion)     »peripheral NEC       »limb NEC	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »nerve (ganglion)     »spinal NEC	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »nerve (ganglion)     »sympathetic NEC [See Also: Neoplasm, nerve, peripheral]	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »peripheral nerve NEC	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »spine, spinal (column)     »nerve (root)	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »spine, spinal (column)     »root	C47.9	C79.89		D36.10	D48.2	D49.2
»Neoplasm, neoplastic   »sympathetic nerve or nervous system NEC	C47.9	C79.89		D36.10	D48.2	D49.2

Patient Education

Autonomic Nervous System Disorders

Your autonomic nervous system is the part of your nervous system that controls involuntary actions, such as the beating of your heart and the widening or narrowing of your blood vessels. When something goes wrong in this system, it can cause serious problems, including:

• Blood pressure problems
• Heart problems
• Trouble with breathing and swallowing
• Erectile dysfunction in men

Autonomic nervous system disorders can occur alone or as the result of another disease, such as Parkinson's disease, alcoholism and diabetes. Problems can affect either part of the system, as in complex regional pain syndromes, or all of the system. Some types are temporary, but many worsen over time. When they affect your breathing or heart function, these disorders can be life-threatening.

Some autonomic nervous system disorders get better when an underlying disease is treated. Often, however, there is no cure. In that case, the goal of treatment is to improve symptoms.

NIH: National Institute of Neurological Disorders and Stroke

[Learn More in MedlinePlus]

Cancer

Cancer begins in your cells, which are the building blocks of your body. Normally, your body forms new cells as you need them, replacing old cells that die. Sometimes this process goes wrong. New cells grow even when you don't need them, and old cells don't die when they should. These extra cells can form a mass called a tumor. Tumors can be benign or malignant. Benign tumors aren't cancer while malignant ones are. Cells from malignant tumors can invade nearby tissues. They can also break away and spread to other parts of the body.

Cancer is not just one disease but many diseases. There are more than 100 different types of cancer. Most cancers are named for where they start. For example, lung cancer starts in the lung, and breast cancer starts in the breast. The spread of cancer from one part of the body to another is called metastasis. Symptoms and treatment depend on the cancer type and how advanced it is. Most treatment plans may include surgery, radiation and/or chemotherapy. Some may involve hormone therapy, immunotherapy or other types of biologic therapy, or stem cell transplantation.

NIH: National Cancer Institute

[Learn More in MedlinePlus]

Soft Tissue Sarcoma-Patient Version

Learn about soft tissue sarcoma risk factors, symptoms, tests to diagnose, factors affecting prognosis, staging, and treatment.
[Learn More in MedlinePlus]

Code History

• FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.