2024 ICD-10-CM Diagnosis Code Q44.5

Other congenital malformations of bile ducts

ICD-10-CM Code:
Q44.5
ICD-10 Code for:
Other congenital malformations of bile ducts
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Other congenital malformations of the digestive system
      (Q38-Q45)
      • Congenital malformations of gallbladder, bile ducts and liver
        (Q44)

Q44.5 is a billable diagnosis code used to specify a medical diagnosis of other congenital malformations of bile ducts. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Accessory hepatic duct
  • Agenesis of bile duct
  • Biliary anomalies
  • Bronchobiliary fistula
  • Caroli disease
  • Caroli syndrome
  • Choledochal cyst
  • Choledochal cyst
  • Congenital abnormal long growth of bile duct
  • Congenital abnormality of liver and/or biliary tract
  • Congenital absence of bile duct
  • Congenital absence of cystic duct
  • Congenital absence of hepatic ducts
  • Congenital anomalous arrangement of pancreatobiliary duct
  • Congenital anomaly of bile ducts
  • Congenital anomaly of biliary tract
  • Congenital bronchobiliary fistula
  • Congenital choledochal cyst
  • Congenital cystic dilatation of common bile duct
  • Congenital developmental anomaly of cystic duct
  • Congenital dilatation of common bile duct
  • Congenital dilatation of lobar intrahepatic bile duct
  • Congenital dilatation of lobar intrahepatic bile duct with obstruction
  • Congenital disorder of gallbladder and biliary tract
  • Congenital diverticulum of bile duct
  • Congenital duplication of biliary duct
  • Congenital duplication of cystic duct
  • Congenital hepatic fibrosis
  • Congenital hyperplasia of intrahepatic bile duct
  • Congenital hypoplasia of bile duct
  • Congenital paucity of intrahepatic bile ducts
  • Congenital respiratory biliary fistula
  • Congenital respiratory biliary fistula
  • Congenital respiratory biliary fistula
  • Congenital tracheal fistula
  • Congenital tracheobiliary fistula
  • Cystic dilatation of common bile duct
  • Cystic dilation of intrahepatic duct
  • Fistula of bile duct
  • Fistula of bile duct
  • Intrahepatic biliary hypoplasia
  • Liver and/or biliary duplication
  • Liver and/or biliary duplication
  • Liver and/or biliary duplication
  • Pancreatic duct anomaly
  • Tracheobiliary fistula

Clinical Classification

Clinical Information

  • Choledochal Cyst

    a congenital anatomic malformation of a bile duct, including cystic dilatation of the extrahepatic bile duct or the large intrahepatic bile duct. classification is based on the site and type of dilatation. type i is most common.
  • Caroli Disease

    congenital cystic dilatation of the intrahepatic bile ducts (bile ducts, intrahepatic). it consists of 2 types: simple caroli disease is characterized by bile duct dilatation (ectasia) alone; and complex caroli disease is characterized by bile duct dilatation with extensive hepatic fibrosis and portal hypertension (hypertension, portal). benign renal tubular ectasia is associated with both types of caroli disease.
  • Choledochal Cyst

    cystic dilatation of the hepatic duct or bile duct.
  • Caroli Disease

    a rare congenital disorder characterized by cystic dilatation of the intrahepatic bile ducts. it is associated with cholangitis and the formation of stones.
  • Congenital Hepatic Fibrosis

    a congenital disorder usually inherited in an autosomal recessive pattern. it affects the hepatobiliary system and the kidneys. it is characterized by liver fibrosis, portal hypertension, and renal cysts.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Accessory hepatic duct
  • Biliary duct duplication
  • Congenital malformation of bile duct NOS
  • Cystic duct duplication

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Present on Admission (POA)

Q44.5 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA IndicatorReason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q44.5 to ICD-9-CM

  • ICD-9-CM Code: 751.60 - Biliary & liver anom NOS
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
  • ICD-9-CM Code: 751.69 - Biliary & liver anom NEC
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Bile Duct Diseases

Your liver makes a digestive juice called bile. Your gallbladder stores it between meals. When you eat, your gallbladder pushes the bile into tubes called bile ducts. They carry the bile to your small intestine. The bile helps break down fat. It also helps the liver get rid of toxins and wastes.

Different diseases can block the bile ducts and cause a problem with the flow of bile:

  • Gallstones, which can increase pressure in the gallbladder and cause a gallbladder attack. The pain usually lasts from one to several hours.
  • Cancer
  • Infections
  • Birth defects, such as biliary atresia. It is the most common reason for liver transplants in children in the United States.
  • Inflammation, which can cause scarring. Over time, this can lead to liver failure.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.