2024 ICD-10-CM Diagnosis Code Q24.9

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Abnormality of left atrioventricular valve chordae tendinae
• Acquired abnormality of aorta due to congenital heart anomaly
• Acrocardiofacial syndrome
• Acyanotic congenital heart disease
• Anophthalmia and megalocornea with cardiopathy and skeletal anomalies syndrome
• Aortic aneurysm due to congenital heart disease
• Associated pulmonary arterial hypertension
• Autosomal dominant intellectual disability, craniofacial anomalies, cardiac defects syndrome
• Beemer Ertbruggen syndrome
• Blepharophimosis, intellectual disability syndrome
• Blue skin
• Brachydactyly, mesomelia, intellectual disability, heart defect syndrome
• Brain malformation, congenital heart disease, postaxial polydactyly syndrome
• Cardiac anomaly and heterotaxy syndrome
• Cardio-acral-facial syndrome
• Cardiocranial syndrome Pfeiffer type
• Cardio-facio-cutaneous syndrome
• Cardiospondylocarpofacial syndrome
• Cataract, congenital heart disease, neural tube defect syndrome
• Central cyanosis
• Choanal atresia
• Choanal atresia, hearing loss, cardiac defect, craniofacial dysmorphism syndrome
• Cleft lip and cleft palate with intestinal malrotation and cardiopathy syndrome
• Cleft lip and palate, craniofacial dysmorphism, congenital heart defect, hearing loss syndrome
• Cognitive impairment, coarse facies, heart defects, obesity, pulmonary involvement, short stature, skeletal dysplasia syndrome
• Coloboma, congenital heart disease, ichthyosiform dermatosis, intellectual disability ear anomaly syndrome
• Complex congenital heart defect
• Congenital abnormality of left atrioventricular valve chordae tendinae in double inlet ventricle
• Congenital abnormality of relationship of cardiac component
• Congenital aplasia of lung
• Congenital atresia of nares
• Congenital atresia of nasopharynx
• Congenital atresia of pharynx
• Congenital blepharophimosis
• Congenital cardiovascular disorders during pregnancy, childbirth and the puerperium
• Congenital cleft hand
• Congenital conductive hearing loss
• Congenital heart disease
• Congenital heart disease in pregnancy
• Congenital hypoplasia of pancreas
• Congenital insufficiency of mitral valve
• Congenital vertebral, cardiac, renal anomalies syndrome
• Cyanosis of skin
• Cyanosis of skin and/or skin-associated mucous membrane
• Cyanotic attack
• Cyanotic congenital heart disease
• Defect of vertebral segmentation
• Erythrocytosis due to cardiovascular disease
• Erythrocytosis due to cyanotic congenital heart disease
• Erythrocytosis due to tissue hypoxemia
• Eye defects, arachnodactyly, cardiopathy syndrome
• Facial dysmorphism, conductive hearing loss, heart defect syndrome
• Genitopalatocardiac syndrome
• Grange syndrome
• Hadziselimovic syndrome
• Hamartoma of tongue
• Heart defect and limb shortening syndrome
• Heart defect, tongue hamartoma, polysyndactyly syndrome
• Heart disease in mother complicating pregnancy, childbirth AND/OR puerperium
• Heart failure due to end stage congenital heart disease
• Heart-hand syndrome Slovenian type
• Hereditary dysplasia of blood vessel
• Hypercyanotic spell due to congenital heart disease
• Intellectual disability, cardiac anomalies, short stature, joint laxity syndrome
• Intellectual disability, congenital heart disease, blepharophimosis, blepharoptosis and hypoplastic teeth
• ITPA-related lethal infantile neurological disorder with cataract and cardiac involvement
• Lethal brain and heart developmental defects syndrome
• Lung agenesis with heart defect and thumb anomaly syndrome
• McKusick Kaufman syndrome
• Mesomelic dysplasia of upper limb
• Microcephaly, seizure, intellectual disability, heart disease syndrome
• Multiple congenital cardiac defects
• Neck webbing
• Neurodevelopmental disorder, craniofacial dysmorphism, cardiac defect, skeletal anomalies syndrome
• Pancreatic hypoplasia, diabetes mellitus, congenital heart disease syndrome
• Pentose disorder
• PHAVER syndrome
• Polysyndactyly and cardiac malformation syndrome
• Pulmonary arterial hypertension associated with congenital heart disease
• Pure gonadal dysgenesis
• Pure gonadal dysgenesis 46,XY
• Secondary hypertension due to congenital heart disorder
• Short stature with webbed neck and congenital heart disease syndrome
• Short stature, developmental delay, congenital heart defect syndrome
• Situs ambiguus
• Sonoda syndrome
• Thomas syndrome
• TMEM94-associated congenital heart defect, facial dysmorphism, developmental delay syndrome
• TRAF7-associated heart defect, digital anomalies, facial dysmorphism, motor and speech delay syndrome
• VACTEL syndrome
• VACTERL syndrome with hydrocephalus
• Verloove Vanhorick Brubakk syndrome
• Vertebral abnormalities, anal atresia, cardiac abnormalities, tracheo-esophageal fistula, renal anomalies, limb defects syndrome

Clinical Information

• Choanal Atresia

  a congenital abnormality that is characterized by a blocked choanae, the opening between the nose and the nasopharynx. blockage can be unilateral or bilateral; bony or membranous.

• Age at Diagnosis of Congenital Heart Disease|Age Diagnosed

  the age of the patient when congenital heart disease was diagnosed.

• Congenital Heart Disease

  a heart disease that is present at birth. representative examples include atrial septal defect, ventricular septal defect, tetralogy of fallot, and patent foramen ovale.

• Family History of Congenital Heart Disease|Family History of CHD|Family history of CHD

  a history of a first-degree relative with congenital heart disease.

• History of Congenital Heart Disease|History of CHD

  an abnormality of cardiac structure or function was present at birth.

• Intervention for Congenital Heart Disease|Intervention(s)

  the treatment the patient had for congenital heart disease.

• Known History of Congenital Heart Disease|Yes

  an indication that the patient has a history of congenital heart disease.

• No History of Congenital Heart Disease|No

  an indication that the patient does not have a history of congenital heart disease.

• Other Presenting Finding of Congenital Heart Disease|Other

  an indication that the patient had a presenting finding of congenital heart disease other than those listed.

• Presenting Finding of Congenital Heart Disease|Presenting Finding

  the presenting findings of congenital heart disease in the patient.

• Unknown History of Congenital Heart Disease|Unknown

  an indication that it is unknown whether the patient has a history of congenital heart disease.

Q24.9 is grouped with Diagnostic Related Groups - MS-DRG Mapping

Diagnostic Related Groups (DRGs) are a classification system used to group together diagnosis codes for the purpose of reimbursement and healthcare management. DRGs are used to standardize the way hospitals and other providers are paid for inpatient services. In this system patients are grouped together based on their principal diagnosis in areas referred to as Major Diagnostic Categories (MDC). Once a patient is assigned a particular diagnostic category, providers receive a predetermined payment rate for the services rendered. This reimbursement rate is often fixed and is meant to cover the cost of care for that patient. Reimbursement is also affected by the relative weight of a diagnostic related group based on the severity of a patient's illness and the associated cost of care during hospitalization.

Diagnostic related groups encourage healthcare providers to focus on quality and efficiency in patient care while managing costs effectively. The diagnosis code is present in the following groups for version MS-DRG V41.0 applicable from 10/01/2023 through 09/30/2024.

MS-DRG	MS-DRG Title	MCD	Relative Weight
306	CARDIAC CONGENITAL AND VALVULAR DISORDERS WITH MCC	05	1.5368
307	CARDIAC CONGENITAL AND VALVULAR DISORDERS WITHOUT MCC	05	0.9426

The relative weight of a diagnostic related group determines the reimbursement rate based on the severity of a patient's illness and the associated cost of care during hospitalization.

Present on Admission (POA)

Q24.9 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here.

CMS POA Indicator Options and Definitions

POA Indicator	Reason for Code	CMS will pay the CC/MCC DRG?
Y	Diagnosis was present at time of inpatient admission.	YES
N	Diagnosis was not present at time of inpatient admission.	NO
U	Documentation insufficient to determine if the condition was present at the time of inpatient admission.	NO
W	Clinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.	YES
1	Unreported/Not used - Exempt from POA reporting.	NO

Convert Q24.9 to ICD-9-CM

• ICD-9-CM Code: 746.9 - Cong heart anomaly NOS
  Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education

Congenital Heart Defects

What are congenital heart defects?

Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a baby's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect.

Congenital heart defects can change the way the heart pumps blood. They may make blood flow too slowly, go the wrong way, or block it completely.

There are many types of congenital heart defects. They can happen in one or more parts of the heart. The most common types are:

• Septal defects ("hole in the heart") - openings in the wall between the left and right sides of the heart
• Heart valve defects - problems with the valves that control the flow of blood through the heart
• Defects in the large blood vessels that carry blood in and out of the heart

Congenital heart defects can range from very mild problems that never need treatment to life-threatening problems at birth. The most serious congenital heart defects are called critical congenital heart disease. Babies with these defects usually need surgery in the first year of life. But the symptoms of milder heart defects may not show up until childhood or adulthood.

What causes congenital heart defects?

Researchers often don't know what causes congenital heart defects. They do know that changes in a baby's genes sometimes cause a heart defect. The changed genes may come from the parents, or the changes may happen during pregnancy.

Who is more likely to have a baby with a congenital heart defect?

Several things may increase the chance that your baby has a congenital heart defect, such as:

• Your health before and during pregnancy, including
  • Having diabetes before pregnancy or developing it in the first 3 months of pregnancy (diabetes that develops later in pregnancy isn't a major risk for heart defects). Carefully controlling your blood sugar before and during pregnancy can lower your baby's risk of congenital heart defects.
  • Having phenylketonuria (PKU), a rare inherited disorder that affects how the body uses a protein in foods. If you have PKU, eating a low-protein diet before getting pregnant can lower your baby's risk of having a congenital heart defect.
  • Having rubella (German measles) during pregnancy.
• Your contact with certain substances during pregnancy, including
  • Smoking or secondhand smoke (breathing smoke from another smoker).
  • Certain medicines, such as angiotensin-converting (ACE) inhibitors for high blood pressure and retinoic acids for acne. If you're pregnant or plan to get pregnant, talk with your health care provider about all the medicines you take.
• Your family history and genetics. In most cases, congenital heart defects don't run in families. But your chance of having a baby with a congenital heart defect does go up if you or the other parent has a congenital heart defect, or if you already have a child with a congenital heart defect.

What are the symptoms of congenital heart defects?

Congenital heart defects don't cause pain. The signs and symptoms are different, depending on the type and number of defects and how serious they are.

Common signs and symptoms of congenital heart defects include:

• Cyanosis - a bluish color to the skin, lips, and fingernails. It happens when there isn't enough oxygen in the blood
• Fatigue - your baby may be unusually sleepy and may become very tired during feedings
• Poor blood flow
• Fast or difficult breathing
• Heart murmur - an unusual sound between heartbeats

What other problems do congenital heart defects cause?

Congenital heart defects don't always cause other problems. If they do, which problems you have would depend on the type and number of defects and how serious the defects are.

Children with congenital heart defects are more likely to:

• Be smaller than other children
• Have problems or delays in mental, and emotional growth, and behavior, such as:
  • Speech and language problems
  • Attention deficit hyperactivity disorders (ADHD)

People with congenital heart defects may develop other health conditions, including:

• Endocarditis - an infection of lining of the heart and valves
• Arrhythmia - a problem with the rate or rhythm of your heartbeat
• Heart failure - when your heart can't pump enough blood to the body
• Pulmonary hypertension - high blood pressure in your lungs
• Kidney and liver disease

How are congenital heart defects diagnosed?

• Before a baby is born, your provider may use ultrasound pictures of the baby's heart to look for heart defects. This is called a fetal echocardiogram. It's done between weeks 18 and 22 of pregnancy.
• During the first few days after birth, all newborns are checked for congenital heart defects. A pulse oximeter is clipped to your baby's hands or feet to measure blood oxygen. If it shows low levels of blood oxygen, more tests will be needed to find out if your baby has a heart defect.
• To diagnose congenital heart defects in babies, children, and adults, a provider may use many tools, including:
  • A physical exam.
  • Certain heart tests to see how the heart is working.
  • Genetic testing to see if certain gene problems caused the defect.

What are the treatments for congenital heart defects?

Treatment depends on the type of congenital heart defect and how serious it is. Possible treatments include:

• Cardiac catheterization to repair simple defects, such as a small hole in the inside wall of the heart. A catheterization uses a thin tube guided through a vein and into the heart.
• Heart surgery may be needed to:
  • Repair defects in the heart and blood vessels.
  • Repair or replace a heart valve.
  • Place a device in the chest to help the heart pump blood.
  • Do a heart transplant.
• Medicine is often used if your baby has a specific type of congenital heart defect called patent ductus arteriosus.

All children and adults who have congenital heart defects need regular follow-up care from a cardiologist (a doctor who specializes in heart diseases) throughout their life, even if their defect was repaired.

Some people may need several heart surgeries or catheterizations over the years. They may also need to take medicines to help their hearts work as well as possible.

NIH: National Heart, Lung, and Blood Institute

[Learn More in MedlinePlus]

Code History

• FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.