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  6. 2024 ICD-10-CM Code Q01
Version 2024
Non-Billable Code

2024 ICD-10-CM Diagnosis Code Q01

Encephalocele

ICD-10-CM Code:
Q01
ICD-10 Code for:
Encephalocele
Is Billable?
Not Valid for Submission
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Congenital malformations of the nervous system
      (Q00-Q07)
      • Encephalocele
        (Q01)

Q01 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of encephalocele. The code is not specific and is NOT valid for the year 2024 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding Applicable to Encephalocele

Non-specific codes like Q01 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10-CM codes with a higher level of specificity when coding for encephalocele:

  • Use Q01.0 for Frontal encephalocele - BILLABLE CODE

  • Use Q01.1 for Nasofrontal encephalocele - BILLABLE CODE

  • Use Q01.2 for Occipital encephalocele - BILLABLE CODE

  • Use Q01.8 for Encephalocele of other sites - BILLABLE CODE

  • Use Q01.9 for Encephalocele, unspecified - BILLABLE CODE

Clinical Information

  • Encephalocele

    brain tissue herniation through a congenital or acquired defect in the skull. the majority of congenital encephaloceles occur in the occipital or frontal regions. clinical features include a protuberant mass that may be pulsatile. the quantity and location of protruding neural tissue determines the type and degree of neurologic deficit. visual defects, psychomotor developmental delay, and persistent motor deficits frequently occur.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Includes

Includes
This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
  • Arnold-Chiari syndrome, type III
  • encephalocystocele
  • encephalomyelocele
  • hydroencephalocele
  • hydromeningocele, cranial
  • meningocele, cerebral
  • meningoencephalocele

Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • Meckel-Gruber syndrome Q61.9

Patient Education


Neural Tube Defects

Neural tube defects are birth defects of the brain, spine, or spinal cord. They happen in the first month of pregnancy, often before a woman even knows that she is pregnant. The two most common neural tube defects are spina bifida and anencephaly. In spina bifida, the fetal spinal column doesn't close completely. There is usually nerve damage that causes at least some paralysis of the legs. In anencephaly, most of the brain and skull do not develop. Babies with anencephaly are usually either stillborn or die shortly after birth. Another type of defect, Chiari malformation, causes the brain tissue to extend into the spinal canal.

The exact causes of neural tube defects aren't known. You're at greater risk of having an infant with a neural tube defect if you:

  • Have obesity
  • Have poorly controlled diabetes
  • Take certain antiseizure medicines

Getting enough folic acid, a type of B vitamin, before and during pregnancy prevents most neural tube defects.

Neural tube defects are usually diagnosed before the infant is born, through lab or imaging tests. There is no cure for neural tube defects. The nerve damage and loss of function that are present at birth are usually permanent. However, a variety of treatments can sometimes prevent further damage and help with complications.

NIH: National Institute of Child Health and Human Development


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.