2024 ICD-10-CM Diagnosis Code N07.9

Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions

ICD-10-CM Code:
N07.9
ICD-10 Code for:
Hereditary nephropathy, NEC w unsp morphologic lesions
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the genitourinary system
    (N00–N99)
    • Glomerular diseases
      (N00-N08)
      • Hereditary nephropathy, not elsewhere classified
        (N07)

N07.9 is a billable diagnosis code used to specify a medical diagnosis of hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Unspecified diagnosis codes like N07.9 are acceptable when clinical information is unknown or not available about a particular condition. Although a more specific code is preferable, unspecified codes should be used when such codes most accurately reflect what is known about a patient's condition. Specific diagnosis codes should not be used if not supported by the patient's medical record.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • 10p partial monosomy syndrome
  • Autosomal dominant complex hereditary spastic paraplegia
  • Autosomal dominant progressive nephropathy with hypertension
  • Carpal-tarsal osteolysis with nephropathy
  • Choreoathetosis
  • Chronic deafness
  • Congenital nephritis
  • Crome syndrome
  • Deafness, small bowel diverticulosis, neuropathy syndrome
  • Deletion of part of chromosome 10
  • Dent disease type 1
  • Dent disease type 2
  • Dent's disease
  • Diplegia
  • Disorder of zinc metabolism
  • Familial aplasia of the vermis
  • Hereditary angiopathy with nephropathy, aneurysms, and muscle cramps syndrome
  • Hereditary nephritis
  • Hereditary nephropathy
  • Hereditary sensory neuropathy
  • Hypoparathyroidism, deafness, renal disease syndrome
  • Idiopathic osteolyses
  • Inherited magnesium-losing nephropathy
  • Joubert syndrome
  • Joubert syndrome with renal defect
  • Magnesium-losing nephropathy
  • Marfanoid physique
  • Microcephalus, glomerulonephritis, marfanoid habitus syndrome
  • Nephrogenic syndrome of inappropriate antidiuresis
  • Nephropathy, deafness, hyperparathyroidism syndrome
  • Non-progressive hereditary glomerulonephritis
  • Parathyroid hyperplasia
  • Peripheral sensory neuropathy
  • Primary hyperparathyroidism
  • Progressive hereditary glomerulonephritis without deafness
  • Psychomotor regression, oculomotor apraxia, movement disorder, nephropathy syndrome
  • Sensory neuropathy
  • Severe oculo-renal-cerebellar syndrome
  • Spastic diplegia
  • Spastic paralysis
  • Spastic paraplegia, nephritis, deafness syndrome

Clinical Classification

Clinical Information

  • Neonatal Severe Primary Hyperparathyroidism

    an autosomal recessive form of kenny-caffey syndrome that is secondary to mutation(s) in the tcbe gene that encodes tubulin-specific chaperone e; it is characterized by the following: hypoparathyroidism with hypocalcemia, marked growth retardation, craniofacial anomalies, absent diploic space, cortical thickening and medullary stenosis of long bones, and small hands and feet.
  • Primary Hyperparathyroidism

    hyperfunction of the parathyroid glands resulting in the overproduction of parathyroid hormone. it is caused by parathyroid adenoma, parathyroid hyperplasia, parathyroid carcinoma, and multiple endocrine neoplasia. it is associated with hypercalcemia and hypophosphatemia. signs and symptoms include weakness, fatigue, nausea, vomiting, constipation, depression, bone pain, osteoporosis, cystic bone lesions, and kidney stones.
  • Brachial Amyotrophic Diplegia|BAD|FAS|Flail Arm Syndrome|MIBS|Man-in-barrel Syndrome

    a neurodegenerative condition characterized by asymmetric weakness in the upper extremities resulting from segmental lower motor neuron dysfunction.
  • Diplegia

    paralysis affecting corresponding parts on both sides of the body.
  • Diplegia of Upper Limbs|Diplegia of upper limbs

    evidence of diplegia of the upper limbs.
  • Neurodevelopmental Disorder with Spastic Diplegia and Visual Defects|MRD19|Mental Retardation, Autosomal Dominant 19|NEDSDV

    an autosomal dominant condition caused by mutation(s) in the ctnnb1 gene, encoding catenin beta-1. it is characterized by severe intellectual disability, progressive spastic diplegia, visual impairment, and dysmorphic craniofacial features.
  • Quadriplegia|Bilateral Diplegia|Bilateral Diplegia|Quadriplegia, unspecified|Tetraplegia

    paralysis of all four limbs.
  • Spastic Diplegia|Little's Disease|Spastic diplegic cerebral palsy

    a type of cerebral palsy characterized by spasticity and hypertonia of the lower extremities bilaterally, particularly the legs, hips, and pelvis; this is the most common (70%) form of cerebral palsy.
  • Joubert Syndrome

    a rare genetic syndrome characterized by the hypoplasia or absence of the cerebellar vermis. signs and symptoms include rapid breathing (hyperpnea), sleep apnea, abnormal eye movements, mental retardation, and ataxia.
  • Joubert Syndrome 17|JBTS17

    an autosomal recessive subtype of joubert syndrome caused by mutation(s) in the cplane1 gene, encoding ciliogenesis and planar polarity effector 1.
  • Joubert Syndrome 3|JBTS3

    an autosomal recessive subtype of joubert syndrome caused by mutation(s) in the ahi1 gene, encoding jouberin.
  • Joubert Syndrome 4

    a rare genetic syndrome caused by mutations in the nphp1 gene. it is characterized by the hypoplasia or absence of the cerebellar vermis. signs and symptoms include rapid breathing (hyperpnea), sleep apnea, abnormal eye movements, mental retardation, and ataxia.
  • Joubert Syndrome 7|JBTS7

    an autosomal recessive sub-type of joubert syndrome caused by mutation(s) in the rpgrip1l gene, encoding a protein thought to function in programmed cell death. it is characterized by cerebellar and oculomotor apraxia, hypotonia and psychomotor delay, neonatal respiratory abnormalities, renal abnormalities, and retinal dystrophy.
  • Joubert Syndrome 9|JBTS9

    an autosomal recessive subtype of joubert syndrome caused by mutation(s) in the cc2d2a gene, encoding coiled-coil and c2 domain-containing protein 2a.

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert N07.9 to ICD-9-CM

  • ICD-9-CM Code: 583.9 - Nephritis NOS
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


Genetic Disorders

Genes are the building blocks of heredity. They are passed from parent to child. They hold DNA, the instructions for making proteins. Proteins do most of the work in cells. They move molecules from one place to another, build structures, break down toxins, and do many other maintenance jobs.

Sometimes there is a mutation, a change in a gene or genes. The mutation changes the gene's instructions for making a protein, so the protein does not work properly or is missing entirely. This can cause a medical condition called a genetic disorder.

You can inherit a gene mutation from one or both parents. A mutation can also happen during your lifetime.

There are three types of genetic disorders:

  • Single-gene disorders, where a mutation affects one gene. Sickle cell anemia is an example.
  • Chromosomal disorders, where chromosomes (or parts of chromosomes) are missing or changed. Chromosomes are the structures that hold our genes. Down syndrome is a chromosomal disorder.
  • Complex disorders, where there are mutations in two or more genes. Often your lifestyle and environment also play a role. Colon cancer is an example.

Genetic tests on blood and other tissue can identify genetic disorders.

NIH: National Library of Medicine


[Learn More in MedlinePlus]

Kidney Diseases

You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters. It goes to your bladder, which stores the urine until you go to the bathroom.

Most kidney diseases attack the nephrons. This damage may leave kidneys unable to remove wastes. Causes can include genetic problems, injuries, or medicines. You have a higher risk of kidney disease if you have diabetes, high blood pressure, or a close family member with kidney disease. Chronic kidney disease damages the nephrons slowly over several years. Other kidney problems include:

  • Cancer
  • Cysts
  • Stones
  • Infections

Your doctor can do blood and urine tests to check if you have kidney disease. If your kidneys fail, you will need dialysis or a kidney transplant.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.