Version 2024

2024 ICD-10-CM Diagnosis Code M35.0

Sjogren syndrome

ICD-10-CM Code:
M35.0
ICD-10 Code for:
Sjogren syndrome
Is Billable?
Not Valid for Submission
Code Navigator:

Code Classification

  • Diseases of the musculoskeletal system and connective tissue
    (M00–M99)
    • Systemic connective tissue disorders
      (M30-M36)
      • Other systemic involvement of connective tissue
        (M35)

M35.0 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of sjogren syndrome. The code is not specific and is NOT valid for the year 2024 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding Applicable to Sjogren syndrome

Non-specific codes like M35.0 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10-CM codes with a higher level of specificity when coding for sjogren syndrome:

  • Use M35.00 for Sjogren syndrome, unspecified - BILLABLE CODE

  • Use M35.01 for Sjogren syndrome with keratoconjunctivitis - BILLABLE CODE

  • Use M35.02 for Sjogren syndrome with lung involvement - BILLABLE CODE

  • Use M35.03 for Sjogren syndrome with myopathy - BILLABLE CODE

  • Use M35.04 for Sjogren syndrome with tubulo-interstitial nephropathy - BILLABLE CODE

  • Use M35.05 for Sjogren syndrome with inflammatory arthritis - BILLABLE CODE

  • Use M35.06 for Sjogren syndrome with peripheral nervous system involvement - BILLABLE CODE

  • Use M35.07 for Sjogren syndrome with central nervous system involvement - BILLABLE CODE

  • Use M35.08 for Sjogren syndrome with gastrointestinal involvement - BILLABLE CODE

  • Use M35.09 for Sjogren syndrome with other organ involvement - BILLABLE CODE

  • Use M35.0A for Sjogren syndrome with glomerular disease - BILLABLE CODE

  • Use M35.0B for Sjogren syndrome with vasculitis - BILLABLE CODE

  • Use M35.0C for Sjogren syndrome with dental involvement - BILLABLE CODE

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Patient Education


Sjögren syndrome

Sjögren syndrome is a disorder whose main features are dry eyes and a dry mouth. The condition typically develops gradually beginning in middle adulthood but can occur at any age.

Sjögren syndrome is classified as an autoimmune disorder, one of a large group of conditions that occur when the immune system attacks the body's own tissues and organs. In Sjögren syndrome, the immune system primarily attacks the glands that produce tears (the lacrimal glands) and saliva (the salivary glands), impairing the glands' ability to secrete these fluids.

Dry eyes may lead to itching, burning, a feeling of sand in the eyes, blurry vision, or intolerance of bright or fluorescent lighting. A dry mouth can feel chalky or full of cotton, and affected individuals may have difficulty speaking, tasting food, or swallowing. Because saliva helps protect the teeth and the tissues of the oral cavity, people with Sjögren syndrome are at increased risk of tooth decay and infections in the mouth.

In most people with Sjögren syndrome, dry eyes and dry mouth are the primary features of the disorder, and general health and life expectancy are largely unaffected. However, in some cases the immune system also attacks and damages other organs and tissues. This complication is known as extraglandular involvement. Affected individuals may develop inflammation in connective tissues, which provide strength and flexibility to structures throughout the body. Disorders involving connective tissue inflammation are sometimes called rheumatic conditions. In Sjögren syndrome, extraglandular involvement may result in painful inflammation of the joints and muscles; dry, itchy skin and skin rashes; chronic cough; a hoarse voice; kidney and liver problems; numbness or tingling in the hands and feet; and, in women, vaginal dryness. Prolonged and extreme tiredness (fatigue) severe enough to affect activities of daily living may also occur in this disorder. A small number of people with Sjögren syndrome develop lymphoma, a blood-related cancer that causes tumor formation in the lymph nodes but can spread to other organs.

Some individuals who are first diagnosed with another rheumatic disorder, such as rheumatoid arthritis or systemic lupus erythematosus, later develop the dry eyes and dry mouth characteristic of Sjögren syndrome. Other autoimmune disorders can also develop after the onset of Sjögren syndrome. In all, about half of all individuals with Sjögren syndrome also have another autoimmune disorder.


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - Code Updated, effective from 10/1/2021 through 9/30/2022
    • New Description: Sjogren syndrome
    • Previous Description: Sjogren syndrome
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.