2024 ICD-10-CM Diagnosis Code H90.5

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• 10p partial monosomy syndrome
• 3-Methylglutaconic aciduria type 4
• 3-methylglutaconic aciduria type IV with sensorineural deafness, encephalopathy and Leigh-like syndrome
• Achalasia of esophagus
• Acquired sensorineural hearing loss
• Acquired sensorineural hearing loss
• Acquired sensorineural hearing loss
• Acquired sensorineural hearing loss
• Acquired sensorineural hearing loss
• Albinism with deafness syndrome
• Anal atresia
• Aphonia, deafness, retinal dystrophy, bifid halluces, intellectual disability syndrome
• Arts syndrome
• Asymmetrical hearing loss
• Asymmetrical sensorineural hearing loss
• Auditory synaptopathy
• Autoimmune sensorineural hearing loss
• Autosomal dominant cerebellar ataxia, deafness and narcolepsy syndrome
• Autosomal dominant deafness with onychodystrophy syndrome
• Autosomal dominant ichthyosis
• Autosomal dominant myopia, midfacial retrusion, sensorineural hearing loss, rhizomelic dysplasia syndrome
• Autosomal dominant retinitis pigmentosa
• Autosomal recessive keratitis-ichthyosis-deafness syndrome
• Benign neoplasm of sacrococcygeal region
• Black locks, oculocutaneous albinism, AND deafness of the sensorineural type
• Cataract, growth hormone deficiency, sensory neuropathy, sensorineural hearing loss, skeletal dysplasia syndrome
• Central hearing loss
• Cerebellar ataxia, areflexia, pes cavus, optic atrophy, sensorineural hearing loss syndrome
• Charcot-Marie-Tooth disease, deafness, intellectual disability syndrome
• Chitty Hall Baraitser syndrome
• Chronic deafness
• Chronic deafness
• Combined perceptive hearing loss
• Complete deafness
• Complete deafness
• Complete deafness
• Complete deafness
• Complete deafness
• Congenital achalasia of esophagus
• Congenital atrophy of optic nerve
• Congenital calyceal diverticulum
• Congenital cataract with ataxia and deafness syndrome
• Congenital cataract with deafness and hypogonadism syndrome
• Congenital cataract, hearing loss, severe developmental delay syndrome
• Congenital cataract, progressive muscular hypotonia, hearing loss, developmental delay syndrome
• Congenital conductive hearing loss
• Congenital corneal dystrophy
• Congenital deafness
• Congenital deafness
• Congenital deafness
• Congenital deafness
• Congenital dilatation of colon
• Congenital hearing disorder
• Congenital hereditary endothelial dystrophy
• Congenital hereditary endothelial dystrophy and perceptive deafness syndrome
• Congenital kyphoscoliosis
• Congenital kyphosis
• Congenital nephritis
• Congenital osteodystrophy
• Congenital prelingual deafness
• Congenital sensorineural hearing loss
• Craniofacial deafness hand syndrome
• Cutaneous syndrome with ichthyosis
• Cutaneous syndrome with ichthyosis
• Cutaneous syndrome with ichthyosis
• Deafness and hypogonadism syndrome
• Deafness and oligodontia syndrome
• Deafness craniofacial syndrome
• Deafness with onychodystrophy syndrome
• Deafness with onychodystrophy syndrome
• Deafness, encephaloneuropathy, obesity, valvulopathy syndrome
• Deafness, genital anomaly, metacarpal and metatarsal synostosis syndrome
• Deafness, vitiligo, achalasia syndrome
• Deafness-dystonia-optic neuronopathy syndrome
• Deletion of part of chromosome 10
• Deletion of part of chromosome 11
• Dentinogenesis imperfecta
• Dentinogenesis imperfecta, short stature, hearing loss, intellectual disability syndrome
• Developmental malformation, deafness, dystonia syndrome
• Diabetes-deafness syndrome maternally transmitted
• DIAPH1-related sensorineural hearing loss-thrombocytopenia syndrome
• Distal renal tubular acidosis
• Distal renal tubular acidosis co-occurrent with sensorineural deafness
• Diverticulum of renal calyx
• Dominant sensorineural hearing loss
• DOORS syndrome
• Duane retraction syndrome with congenital deafness
• Duane's syndrome, type 3
• Ectodermal dysplasia and sensorineural deafness syndrome
• Ehlers-Danlos syndrome kyphoscoliotic and deafness type
• Ehlers-Danlos syndrome kyphoscoliotic type
• End organ deafness
• Epiphyseal dysplasia, hearing loss, dysmorphism syndrome
• Essential tremor
• Familial steroid-resistant nephrotic syndrome with sensorineural deafness
• Gemignani syndrome
• Generalized dystonia
• Gingival fibromatosis
• Gingival fibromatosis with progressive deafness syndrome
• Globodontia
• Gonadal dysgenesis with auditory dysfunction, autosomal recessive inheritance
• Hereditary essential tremor
• Hereditary gingival fibromatosis
• Hereditary growth hormone deficiency
• Hereditary sensory neuropathy
• Heritable disorder of neutrophil function
• High frequency sensorineural hearing loss in right ear
• Hirschsprung disease with deafness and polydactyly syndrome
• Hypertelorism
• Hypertelorism, preauricular sinus, punctual pits, deafness syndrome
• Hypogonadotropic hypogonadism, severe microcephaly, sensorineural hearing loss, dysmorphism syndrome
• Hypoparathyroidism, deafness, renal disease syndrome
• Hypotrichosis and deafness syndrome
• Kawashima Tsuji syndrome
• Keipert syndrome
• KID syndrome
• KID syndrome
• Lipoma of lower back
• Lowe Kohn Cohen syndrome
• Lowry Yong syndrome
• Macrodontia
• Male infertility of chromosomal origin
• Mandibular hypoplasia, deafness, progeroid syndrome
• Maternal perinatal sensorineural hearing loss
• Maternally inherited cardiomyopathy and hearing loss syndrome
• Megaloblastic anemia due to inborn errors of metabolism
• Megaloblastic anemia, thiamine-responsive, with diabetes mellitus and sensorineural deafness
• Microcephaly, intellectual disability, sensorineural hearing loss, epilepsy, abnormal muscle tone syndrome
• Micromelia
• Multiple malformation syndrome, moderate short stature, facial
• Narcolepsy
• Nathalie syndrome
• Neonatal sensorineural hearing loss
• Nephrosis, deafness, urinary tract, digital malformation syndrome
• Nephrotic syndrome, deafness, pretibial epidermolysis bullosa syndrome
• Neural hearing loss
• Neural hearing loss
• Neural hearing loss of left ear
• Neural hearing loss of right ear
• Neutropenia, monocytopenia, deafness syndrome
• Non-acquired combined pituitary hormone deficiency, sensorineural hearing loss, spine abnormalities syndrome
• Non-syndromic mitochondrial sensorineural deafness
• Ocular albinism
• Ocular albinism with late-onset sensorineural deafness
• Oculootodental syndrome
• Oligodontia
• Olivopontocerebellar atrophy and deafness
• Olivopontocerebellar degeneration
• Osteochondrodysplatic nanism, deafness, retinitis pigmentosa syndrome
• Panhypopituitarism
• PCNA-related progressive neurodegenerative photosensitivity syndrome
• Peripheral neuropathy with sensorineural hearing impairment syndrome
• Phocomelia
• Phocomelia, ectrodactyly, deafness and sinus arrhythmia syndrome
• Pili torti
• Pili torti-deafness syndrome
• Postnatal acquired sensorineural hearing loss
• Postoperative profound sensorineural hearing loss
• Preauricular fistula
• Premature canities
• Primary hypersomnia
• Profound acquired hearing loss
• Profound hearing loss
• Profound hearing loss
• Profound sensorineural hearing loss
• Profound sensorineural hearing loss
• Progressive autosomal recessive cerebellar ataxia, sensorineural hearing loss syndrome
• Progressive sensorineural hearing loss and hypertrophic cardiomyopathy syndrome
• Recessive sensorineural hearing loss
• Recessive sensorineural hearing loss
• Renal caliceal diverticuli and deafness syndrome
• Renal tubular acidosis with progressive nerve deafness
• Retinitis pigmentosa, hearing loss, premature aging, short stature, facial dysmorphism syndrome
• Retinitis pigmentosa, intellectual disability, deafness, hypogenitalism syndrome
• Retinitis pigmentosa-deafness syndrome
• Retinitis pigmentosa-deafness syndrome type 3
• Seizure, sensorineural deafness, ataxia, intellectual disability, electrolyte imbalance syndrome
• Sellars Beighton syndrome
• Sensorineural deafness and male infertility
• Sensorineural deafness due to late congenital syphilis
• Sensorineural deafness with dilated cardiomyopathy syndrome
• Sensorineural hearing loss
• Sensorineural hearing loss in left ear
• Sensorineural hearing loss in right ear
• Sensorineural hearing loss in right ear
• Sensorineural hearing loss of combined sites
• Sensorineural hearing loss of left ear
• Sensorineural hearing loss of right ear
• Sensorineural hearing loss, early graying, essential tremor syndrome
• Sensory hearing loss
• Sensory hearing loss
• Sensory neuropathy
• Senter syndrome
• Severe motor and intellectual disabilities, sensorineural deafness, dystonia syndrome
• Severe X-linked intellectual disability Gustavson type
• Sinoatrial node dysfunction and deafness
• Spondyloepiphyseal dysplasia MacDermot type
• Steroid-resistant nephrotic syndrome
• Sudden hearing loss
• Sudden sensorineural hearing loss
• Syndromic sensorineural deafness due to combined oxidative phosphorylation defect
• Thiamine-responsive megaloblastic anemia
• Thong Douglas Ferrante syndrome
• Tungland Bellman syndrome
• Woodhouse Sakati syndrome
• X-linked sensorineural hearing loss
• X-linked sensorineural hearing loss

Clinical Information

• Dentinogenesis Imperfecta

  an autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth. the dentin develops poorly with low mineral content while the pulp canal is obliterated.

• Hypertelorism

  abnormal increase in the interorbital distance due to overdevelopment of the lesser wings of the sphenoid.

• Narcolepsy

  a condition characterized by recurrent episodes of daytime somnolence and lapses in consciousness (microsomnias) that may be associated with automatic behaviors and amnesia. cataplexy; sleep paralysis, and hypnagogic hallucinations frequently accompany narcolepsy. the pathophysiology of this disorder includes sleep-onset rapid eye movement (rem) sleep, which normally follows stage iii or iv sleep. (from neurology 1998 feb;50(2 suppl 1):s2-s7)

• Essential Tremor

  a relatively common disorder characterized by a fairly specific pattern of tremors which are most prominent in the upper extremities and neck, inducing titubations of the head. the tremor is usually mild, but when severe may be disabling. an autosomal dominant pattern of inheritance may occur in some families (i.e., familial tremor). (mov disord 1988;13(1):5-10)

• Dentinogenesis Imperfecta

  a congenital tooth development disorder caused by mutations in the dspp gene. the teeth are weak, discolored, and translucent.

• Autosomal Recessive Distal Renal Tubular Acidosis-4 with Hemolytic Anemia|DRTA4

  an autosomal recessive type of distal renal tubular acidosis caused by mutation(s) in the slc4a1 gene, encoding band 3 anion transport protein. additionally, it may be characterized by hemolytic anemia.

• Distal Renal Tubular Acidosis

  failure of the renal tubules of the kidney to excrete urine of sufficient acidity, resulting in metabolic acidosis.

• Narcolepsy

  a sleep disorder characterized by a tendency for excessive sleepiness during the day which occurs even after adequate sleep in the nighttime. the persons who suffer from this condition experience fatigue and may fall asleep at inappropriate times during the day.

• Narcolepsy in Conditions Classified Elsewhere with Cataplexy|Narcolepsy in conditions classified elsewhere with cataplexy

  evidence of narcolepsy in conditions classified elsewhere with cataplexy.

• Narcolepsy in Conditions Classified Elsewhere without Cataplexy|Narcolepsy in conditions classified elsewhere without cataplexy

  evidence of narcolepsy in conditions classified elsewhere without cataplexy.

• Narcolepsy with Cataplexy|Narcolepsy with cataplexy

  evidence of narcolepsy with cataplexy.

• Narcolepsy without Cataplexy|Narcolepsy without cataplexy

  evidence of narcolepsy without cataplexy.

• Essential Tremor

  a movement disorder characterized by involuntary and rhythmic shaking of parts of the body, most often the hands or arms, that can be triggered or worsened by physical or environmental stressors. essential tremor may be progressive and can be inherited in an autosomal dominant manner.

• Central Hearing Loss

  hearing loss resulting from disorders of the central nervous system auditory pathways.

• Congenital Kyphosis

  an abnormally increased curvature of the thoracic portion of the spine that is present at the time of birth.

• Sensory Hearing Loss

  hearing loss caused by damage to the cochlea in the inner ear.

H90.5 is grouped with Diagnostic Related Groups - MS-DRG Mapping

Diagnostic Related Groups (DRGs) are a classification system used to group together diagnosis codes for the purpose of reimbursement and healthcare management. DRGs are used to standardize the way hospitals and other providers are paid for inpatient services. In this system patients are grouped together based on their principal diagnosis in areas referred to as Major Diagnostic Categories (MDC). Once a patient is assigned a particular diagnostic category, providers receive a predetermined payment rate for the services rendered. This reimbursement rate is often fixed and is meant to cover the cost of care for that patient. Reimbursement is also affected by the relative weight of a diagnostic related group based on the severity of a patient's illness and the associated cost of care during hospitalization.

Diagnostic related groups encourage healthcare providers to focus on quality and efficiency in patient care while managing costs effectively. The diagnosis code is present in the following groups for version MS-DRG V41.0 applicable from 10/01/2023 through 09/30/2024.

MS-DRG	MS-DRG Title	MCD	Relative Weight
154	OTHER EAR, NOSE, MOUTH AND THROAT DIAGNOSES WITH MCC	03	1.5382
155	OTHER EAR, NOSE, MOUTH AND THROAT DIAGNOSES WITH CC	03	0.9466
156	OTHER EAR, NOSE, MOUTH AND THROAT DIAGNOSES WITHOUT CC/MCC	03	0.6555

The relative weight of a diagnostic related group determines the reimbursement rate based on the severity of a patient's illness and the associated cost of care during hospitalization.

Convert H90.5 to ICD-9-CM

• ICD-9-CM Code: 389.10 - Sensorneur hear loss NOS
  Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
• ICD-9-CM Code: 389.14 - Central hearing loss
  Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.
• ICD-9-CM Code: 389.16 - Sensoneur hear loss asym
  Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education

Hearing Disorders and Deafness

It's frustrating to be unable to hear well enough to enjoy talking with friends or family. Hearing disorders make it hard, but not impossible, to hear. They can often be helped. Deafness can keep you from hearing sound at all.

What causes hearing loss? Some possibilities are:

• Heredity
• Diseases such as ear infections and meningitis
• Trauma
• Certain medicines
• Long-term exposure to loud noise
• Aging

There are two main types of hearing loss. One happens when your inner ear or auditory nerve is damaged. This type is usually permanent. The other kind happens when sound waves cannot reach your inner ear. Earwax buildup, fluid, or a punctured eardrum can cause it. Treatment or surgery can often reverse this kind of hearing loss.

Untreated, hearing problems can get worse. If you have trouble hearing, you can get help. Possible treatments include hearing aids, cochlear implants, special training, certain medicines, and surgery.

NIH: National Institute on Deafness and Other Communication Disorders

[Learn More in MedlinePlus]

Nonsyndromic hearing loss

Nonsyndromic hearing loss is a partial or total loss of hearing that is not associated with other signs and symptoms. In contrast, syndromic hearing loss occurs with signs and symptoms affecting other parts of the body.

Nonsyndromic hearing loss can be classified in several different ways. One common way is by the condition's pattern of inheritance: autosomal dominant (DFNA), autosomal recessive (DFNB), X-linked (DFNX), or mitochondrial (which does not have a special designation). Each of these types of hearing loss includes multiple subtypes. DFNA, DFNB, and DFNX subtypes are numbered in the order in which they were first described. For example, DFNA1 was the first type of autosomal dominant nonsyndromic hearing loss to be identified.

The characteristics of nonsyndromic hearing loss vary among the different types. Hearing loss can affect one ear (unilateral) or both ears (bilateral). Degrees of hearing loss range from mild (difficulty understanding soft speech) to profound (inability to hear even very loud noises). The term "deafness" is often used to describe severe-to-profound hearing loss. Hearing loss can be stable, or it may be progressive, becoming more severe as a person gets older. Particular types of nonsyndromic hearing loss show distinctive patterns of hearing loss. For example, the loss may be more pronounced at high, middle, or low tones.

Most forms of nonsyndromic hearing loss are described as sensorineural, which means they are associated with a permanent loss of hearing caused by damage to structures in the inner ear. The inner ear processes sound and sends the information to the brain in the form of electrical nerve impulses. Less commonly, nonsyndromic hearing loss is described as conductive, meaning it results from changes in the middle ear. The middle ear contains three tiny bones that help transfer sound from the eardrum to the inner ear. Some forms of nonsyndromic hearing loss, particularly a type called DFNX2, involve changes in both the inner ear and the middle ear. This combination is called mixed hearing loss.

Depending on the type, nonsyndromic hearing loss can become apparent at any time from infancy to old age. Hearing loss that is present before a child learns to speak is classified as prelingual or congenital. Hearing loss that occurs after the development of speech is classified as postlingual.

[Learn More in MedlinePlus]

Code History

• FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.