2024 ICD-10-CM Diagnosis Code H35.54

Dystrophies primarily involving the retinal pigment epithelium

ICD-10-CM Code:
H35.54
ICD-10 Code for:
Dystrophies primarily w the retinal pigment epithelium
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the eye and adnexa
    (H00–H59)
    • Disorders of choroid and retina
      (H30-H36)
      • Other retinal disorders
        (H35)

H35.54 is a billable diagnosis code used to specify a medical diagnosis of dystrophies primarily involving the retinal pigment epithelium. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Adult vitelliform macular dystrophy
  • Amelogenesis imperfecta co-occurrent with cone rod dystrophy
  • Best vitelliform macular dystrophy
  • Biallelic RPE65 mutation associated retinal dystrophy
  • Fundus pulverulentus
  • Hereditary retinal dystrophy primarily involving retinal pigment epithelium
  • Hereditary retinal dystrophy primarily involving retinal pigment epithelium
  • Macular vitelliform deposits
  • Macular vitelliform deposits
  • Martinique crinkled retinal pigment epitheliopathy
  • Multifocal pattern dystrophy of retinal pigment epithelium simulating fundus flavimaculatus
  • Progressive cone-rod dystrophy
  • Reticular dystrophy of retinal pigment epithelium
  • Retinal pigment epithelial dystrophy
  • Retinal vitelliform deposits
  • Retinal vitelliform deposits
  • Spondylometaphyseal dysplasia with cone-rod dystrophy syndrome

Clinical Classification

Clinical Information

  • Hereditary Retinal Dystrophy

    an inherited form of retinal dystrophy.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Vitelliform retinal dystrophy

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert H35.54 to ICD-9-CM

  • ICD-9-CM Code: 362.76 - Vitelliform dystrophy

Patient Education


Retinal Disorders

The retina is a layer of tissue in the back of your eye that senses light and sends images to your brain. In the center of this nerve tissue is the macula. It provides the sharp, central vision needed for reading, driving and seeing fine detail.

Retinal disorders affect this vital tissue. They can affect your vision, and some can be serious enough to cause blindness. Examples are:

  • Macular degeneration - a disease that destroys your sharp, central vision
  • Diabetic eye disease
  • Retinal detachment - a medical emergency, when the retina is pulled away from the back of the eye
  • Retinoblastoma - cancer of the retina. It is most common in young children.
  • Macular pucker - scar tissue on the macula
  • Macular hole - a small break in the macula that usually happens to people over 60
  • Floaters - cobwebs or specks in your field of vision

NIH: National Eye Institute


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.