2024 ICD-10-CM Diagnosis Code G71.3

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

• Adult-onset chronic progressive external ophthalmoplegia with mitochondrial myopathy
• Adult-onset multiple mitochondrial deoxyribonucleic acid deletion syndrome due to deoxyguanosine kinase deficiency
• Autosomal dominant mitochondrial myopathy with exercise intolerance
• Childhood myocerebrohepatopathy spectrum
• Congenital cataract, hypertrophic cardiomyopathy, mitochondrial myopathy syndrome
• Cytochrome-c oxidase deficiency
• DNA2-related mitochondrial DNA deletion syndrome
• FASTKD2-related infantile mitochondrial encephalomyopathy
• FBXL4-related encephalomyopathic mitochondrial DNA depletion syndrome
• Hereditary cerebellar atrophy
• Hypertrophic mitochondrial cardiomyopathy
• Lethal infantile mitochondrial myopathy
• Maternally inherited mitochondrial cardiomyopathy
• Maternally inherited mitochondrial cardiomyopathy and myopathy
• Maternally inherited mitochondrial deoxyribonucleic acid disease
• Maternally inherited mitochondrial deoxyribonucleic acid disease
• Maternally inherited mitochondrial deoxyribonucleic acid disease
• Maternally inherited mitochondrial myopathy
• Mitochondrial deoxyribonucleic acid depletion syndrome myopathic form
• Mitochondrial DNA depletion syndrome encephalomyopathic form
• Mitochondrial DNA depletion syndrome encephalomyopathic form
• Mitochondrial DNA depletion syndrome encephalomyopathic form
• Mitochondrial DNA depletion syndrome encephalomyopathic form
• Mitochondrial DNA depletion syndrome encephalomyopathic form with methylmalonic aciduria
• Mitochondrial DNA depletion syndrome, encephalomyopathic form with variable craniofacial anomalies
• Mitochondrial encephalomyopathy
• Mitochondrial myopathy
• Mitochondrial myopathy with reversible cytochrome C oxidase deficiency
• Mitochondrial myopathy with sideroblastic anemia syndrome
• Mitochondrial myopathy, cerebellar ataxia, pigmentary retinopathy syndrome
• Mitochondrial myopathy, lactic acidosis, deafness syndrome
• Mitochondrial neurogastrointestinal encephalomyopathy syndrome
• Myopathy and diabetes mellitus
• Progressive external ophthalmoplegia, myopathy, emaciation syndrome
• Pure mitochondrial myopathy
• RRM2B-related mitochondrial DNA depletion syndrome, encephalomyopathic form with renal tubulopathy
• Severe X-linked mitochondrial encephalomyopathy
• TK2-related mitochondrial deoxyribonucleic acid depletion syndrome myopathic form
• TMEM70 related mitochondrial encephalo-cardio-myopathy

Clinical Information

• Mitochondrial Myopathy

  myopathy caused by mitochondrial abnormalities.

Convert G71.3 to ICD-9-CM

• ICD-9-CM Code: 359.89 - Myopathies NEC
  Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education

Mitochondrial Diseases

Metabolism is the process your body uses to make energy from the food you eat. Food is made up of proteins, carbohydrates, and fats. Chemicals in your digestive system (enzymes) break the food parts down into sugars and acids, your body's fuel. Your body can use this fuel right away, or it can store the energy in your body tissues. If you have a metabolic disorder, something goes wrong with this process.

Mitochondrial diseases are a group of metabolic disorders. Mitochondria are small structures that produce energy in almost all of your cells. They make it by combining oxygen with the fuel molecules (sugars and fats) that come from your food. When the mitochondria are defective, the cells do not have enough energy. The unused oxygen and fuel molecules build up in the cells and cause damage.

The symptoms of mitochondrial disease can vary. It depends on how many mitochondria are defective, and where they are in the body. Sometimes only one organ, tissue, or cell type is affected. But often the problem affects many of them. Muscle and nerve cells have especially high energy needs, so muscular and neurological problems are common. The diseases range from mild to severe. Some types can be fatal.

Genetic mutations cause these diseases. They usually happen before age 20, and some are more common in infants. There are no cures for these diseases, but treatments may help with symptoms and slow down the disease. They may include physical therapy, vitamins and supplements, special diets, and medicines.

[Learn More in MedlinePlus]

Code History

• FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
• FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
• FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
• FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
• FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
• FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
• FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
• FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
• FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.