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  6. 2024 ICD-10-CM Code D76.3

2024 ICD-10-CM Diagnosis Code D76.3

Other histiocytosis syndromes

ICD-10-CM Code:
D76.3
ICD-10 Code for:
Other histiocytosis syndromes
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Chronic
Code Navigator:

Code Classification

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
    (D50–D89)
    • Other disorders of blood and blood-forming organs
      (D70-D77)
      • Other specified diseases with participation of lymphoreticular and reticulohistiocytic tissue
        (D76)

D76.3 is a billable diagnosis code used to specify a medical diagnosis of other histiocytosis syndromes. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Benign cephalic histiocytosis
  • Chronic histiocytosis
  • Cutaneous reticulohistiocytosis
  • Dermal dendritic cell histiocytosis
  • Erdheim-Chester disease
  • Hemolytic erythrophagocytic syndrome
  • Hereditary progressive mucinous histiocytosis
  • Histiocytic syndrome
  • Histiocytosis-lymphadenopathy plus syndrome
  • Juvenile xanthogranuloma
  • Juvenile xanthogranuloma of iris
  • Juvenile xanthogranuloma of skin
  • Malakoplakia
  • Malakoplakia
  • Mucinous histiocytosis of the colon
  • Multiple eruptive juvenile xanthogranuloma
  • Necrobiotic xanthogranuloma
  • Necrobiotic xanthogranuloma with paraproteinemia
  • Non-Langerhans cell histiocytic dermatosis
  • Panniculitis secondary to histiocytic disorder
  • Periodontitis due to histiocytosis syndrome
  • Progressive nodular histiocytosis
  • Retroperitoneal xanthogranuloma
  • Sea-blue histiocyte syndrome
  • Sinus histiocytosis with massive lymphadenopathy
  • Solitary eruptive xanthogranuloma
  • Solitary reticulohistiocytoma
  • Subcutaneous xanthogranulomatosis
  • Undetermined cell histiocytosis
  • Xanthogranuloma
  • Xanthogranuloma
  • Xanthogranuloma
  • Xanthogranuloma of choroid plexus

Clinical Classification

Clinical Information

  • Necrobiotic Xanthogranuloma

    a cutaneous necrobiotic disorder characterized by firm, yellow plaques or nodules, often in a periorbital distribution. it is often accompanied by an elevated erythrocyte sedimentation rate; leukopenia; and monoclonal gammopathy (igg-kappa type) and systemic involvement.

  • Malakoplakia

    an inflammatory reaction characterized by the presence of papules or nodules usually in the genitourinary tract. it is usually a reaction to an infection. morphologically, it consists of foamy histiocytes and characteristic basophilic inclusion bodies called michaelis-gutmann bodies.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Reticulohistiocytoma (giant-cell)
  • Sinus histiocytosis with massive lymphadenopathy
  • Xanthogranuloma

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert D76.3 to ICD-9-CM

  • ICD-9-CM Code: 288.4 - Hemophagocytic syndromes
    Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.